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Hibch | 3-hydroxyisobutyryl-CoA hydrolase, mitochondrial; Hydrolyzes 3-hydroxyisobutyryl-CoA (HIBYL-CoA), a saline catabolite; Belongs to the enoyl-CoA hydratase/isomerase family. (358 aa) | ||||
Echdc1 | Enoyl-CoA hydratase domain-containing protein 1; Belongs to the enoyl-CoA hydratase/isomerase family. (299 aa) | ||||
I79_021396 | Isovaleryl-CoA dehydrogenase, mitochondrial. (422 aa) | ||||
Bckdha | 2-oxoisovalerate dehydrogenase subunit alpha; The branched-chain alpha-keto dehydrogenase complex catalyzes the overall conversion of alpha-keto acids to acyl-CoA and CO(2). It contains multiple copies of three enzymatic components: branched-chain alpha-keto acid decarboxylase (E1), lipoamide acyltransferase (E2) and lipoamide dehydrogenase (E3). (338 aa) | ||||
Mccc1 | Methylcrotonoyl-CoA carboxylase subunit alpha, mitochondrial. (683 aa) | ||||
Bckdk | Protein-serine/threonine kinase. (412 aa) | ||||
Acadsb | Short/branched chain specific acyl-CoA dehydrogenase, mitochondrial. (389 aa) | ||||
Dld | Dihydrolipoyl dehydrogenase. (509 aa) | ||||
Acat1 | Acetyl-CoA acetyltransferase, mitochondrial; Belongs to the thiolase-like superfamily. Thiolase family. (424 aa) | ||||
Bcat2 | Branched-chain-amino-acid aminotransferase, mitochondrial. (783 aa) | ||||
Auh | Methylglutaconyl-CoA hydratase, mitochondrial; Belongs to the enoyl-CoA hydratase/isomerase family. (230 aa) | ||||
Aldh6a1 | Methylmalonate-semialdehyde dehydrogenase [acylating], mitochondrial. (243 aa) | ||||
Ppm1k | Protein phosphatase 1K, mitochondrial. (149 aa) | ||||
Mccc2 | Methylcrotonoyl-CoA carboxylase beta chain, mitochondrial. (563 aa) | ||||
Slc25a44 | Solute carrier family 25 member 44; Belongs to the mitochondrial carrier (TC 2.A.29) family. (337 aa) | ||||
Hibadh | 3-hydroxyisobutyrate dehydrogenase; Belongs to the HIBADH-related family. (301 aa) | ||||
H671_1g1921 | Dihydrolipoyl dehydrogenase, mitochondrial. (180 aa) | ||||
Hsd17b10 | 3-hydroxyacyl-CoA dehydrogenase type-2-like protein; Belongs to the short-chain dehydrogenases/reductases (SDR) family. (261 aa) | ||||
I79_006148 | 2-oxoisovalerate dehydrogenase subunit beta, mitochondrial. (221 aa) | ||||
I79_004748 | Branched-chain-amino-acid aminotransferase; Belongs to the class-IV pyridoxal-phosphate-dependent aminotransferase family. (429 aa) | ||||
I79_004236 | Protein-serine/threonine kinase. (49 aa) | ||||
I79_001918 | Enoyl-CoA hydratase domain-containing protein 2, mitochondrial; Belongs to the enoyl-CoA hydratase/isomerase family. (259 aa) | ||||
Acad8 | Isobutyryl-CoA dehydrogenase, mitochondrial. (411 aa) | ||||
I79_024352 | Enoyl-CoA hydratase, mitochondrial; Belongs to the enoyl-CoA hydratase/isomerase family. (271 aa) | ||||
I79_024231 | 2-oxoisovalerate dehydrogenase E2 component (dihydrolipoyl transacylase). (220 aa) |