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MAIP1 | Matrix AAA peptidase interacting protein 1. (273 aa) | ||||
DNAJC15 | DnaJ heat shock protein family (Hsp40) member C15. (149 aa) | ||||
ACSS3 | Acyl-CoA synthetase short chain family member 3. (682 aa) | ||||
SSBP1 | Single stranded DNA binding protein 1. (137 aa) | ||||
MRPS31 | Mitochondrial ribosomal protein S31. (383 aa) | ||||
POLDIP2 | DNA polymerase delta interacting protein 2. (368 aa) | ||||
PDHX | Dihydrolipoamide acetyltransferase component of pyruvate dehydrogenase complex. (442 aa) | ||||
SUCLG1 | Succinate--CoA ligase [ADP/GDP-forming] subunit alpha, mitochondrial; Succinyl-CoA synthetase functions in the citric acid cycle (TCA), coupling the hydrolysis of succinyl-CoA to the synthesis of either ATP or GTP and thus represents the only step of substrate-level phosphorylation in the TCA. The alpha subunit of the enzyme binds the substrates coenzyme A and phosphate, while succinate binding and specificity for either ATP or GTP is provided by different beta subunits. (346 aa) | ||||
PRIMPOL | Primase and DNA directed polymerase. (547 aa) | ||||
LOC100723477 | Uncharacterized protein. (456 aa) | ||||
HSPA9 | Heat shock protein family A (Hsp70) member 9; Belongs to the heat shock protein 70 family. (678 aa) | ||||
Mrpl47 | Uncharacterized protein. (251 aa) | ||||
MRPS30 | Mitochondrial ribosomal protein S30. (421 aa) | ||||
TIMM44 | Mitochondrial import inner membrane translocase subunit TIM44; Essential component of the PAM complex, a complex required for the translocation of transit peptide-containing proteins from the inner membrane into the mitochondrial matrix in an ATP-dependent manner; Belongs to the Tim44 family. (452 aa) | ||||
LOC100713838 | Uncharacterized protein. (705 aa) | ||||
PDE12 | Phosphodiesterase 12. (608 aa) | ||||
MRPL45 | Mitochondrial ribosomal protein L45. (307 aa) | ||||
IDH3A | Isocitrate dehydrogenase [NAD] subunit, mitochondrial. (379 aa) | ||||
PITRM1 | Pitrilysin metallopeptidase 1. (1032 aa) | ||||
MRPS7 | Mitochondrial ribosomal protein S7. (242 aa) | ||||
MLYCD | Malonyl-CoA decarboxylase. (488 aa) | ||||
TWNK | Twinkle mtDNA helicase. (670 aa) | ||||
GLRX5 | Glutaredoxin 5. (156 aa) | ||||
MRPL11 | Mitochondrial ribosomal protein L11; Belongs to the universal ribosomal protein uL11 family. (192 aa) | ||||
Bckdha | 2-oxoisovalerate dehydrogenase subunit alpha; The branched-chain alpha-keto dehydrogenase complex catalyzes the overall conversion of alpha-keto acids to acyl-CoA and CO(2). It contains multiple copies of three enzymatic components: branched-chain alpha-keto acid decarboxylase (E1), lipoamide acyltransferase (E2) and lipoamide dehydrogenase (E3). (446 aa) | ||||
Lrpprc | PPR_long domain-containing protein. (1203 aa) | ||||
MRPL10 | Mitochondrial ribosomal protein L10. (262 aa) | ||||
MRPL46 | Mitochondrial ribosomal protein L46. (280 aa) | ||||
MRPL57 | Mitochondrial ribosomal protein L57. (102 aa) | ||||
MIEF1 | Mitochondrial elongation factor 1. (463 aa) | ||||
TRAP1 | TNF receptor associated protein 1. (706 aa) | ||||
MRPS33 | Mitochondrial ribosomal protein S33. (106 aa) | ||||
FDX1 | Ferredoxin 1. (124 aa) | ||||
DLAT | Acetyltransferase component of pyruvate dehydrogenase complex; The pyruvate dehydrogenase complex catalyzes the overall conversion of pyruvate to acetyl-CoA and CO(2). (650 aa) | ||||
MRPL12 | Mitochondrial ribosomal protein L12. (199 aa) | ||||
MRPS10 | Mitochondrial ribosomal protein S10. (201 aa) | ||||
MPV17L2 | MPV17 mitochondrial inner membrane protein like 2; Belongs to the peroxisomal membrane protein PXMP2/4 family. (210 aa) | ||||
MRPL21 | Mitochondrial ribosomal protein L21. (209 aa) | ||||
GRPEL2 | GrpE protein homolog; Essential component of the PAM complex, a complex required for the translocation of transit peptide-containing proteins from the inner membrane into the mitochondrial matrix in an ATP-dependent manner; Belongs to the GrpE family. (225 aa) | ||||
MRPL33 | Mitochondrial ribosomal protein L33. (65 aa) | ||||
NSUN3 | NOP2/Sun RNA methyltransferase 3; Belongs to the class I-like SAM-binding methyltransferase superfamily. RsmB/NOP family. (334 aa) | ||||
ENSCPOP00000033036 | Uncharacterized protein; Belongs to the GroES chaperonin family. (85 aa) | ||||
MRPL20 | Mitochondrial ribosomal protein L20; Belongs to the bacterial ribosomal protein bL20 family. (149 aa) | ||||
PRDX1 | Peroxiredoxin 1. (199 aa) | ||||
LRRC59 | Leucine rich repeat containing 59. (307 aa) | ||||
MRPS36 | Mitochondrial ribosomal protein S36. (100 aa) | ||||
PCCB | Propionyl-CoA carboxylase subunit beta. (539 aa) | ||||
HAGH | Hydroxyacylglutathione hydrolase. (260 aa) | ||||
TM2D2 | TM2 domain containing 2. (214 aa) | ||||
MRPS22 | Mitochondrial ribosomal protein S22. (361 aa) | ||||
MRPS24 | Mitochondrial ribosomal protein S24. (166 aa) | ||||
AK4 | Adenylate kinase 4, mitochondrial; Involved in maintaining the homeostasis of cellular nucleotides by catalyzing the interconversion of nucleoside phosphates. Efficiently phosphorylates AMP and dAMP using ATP as phosphate donor, but phosphorylates only AMP when using GTP as phosphate donor. Also displays broad nucleoside diphosphate kinase activity. (223 aa) | ||||
MTG1 | Mitochondrial GTPase 1; Plays a role in the regulation of the mitochondrial ribosome assembly and of translational activity. Displays mitochondrial GTPase activity; Belongs to the TRAFAC class YlqF/YawG GTPase family. MTG1 subfamily. (333 aa) | ||||
MRPL50 | Mitochondrial ribosomal protein L50. (158 aa) | ||||
PAM16 | Presequence translocase associated motor 16. (121 aa) | ||||
MRPS12 | Mitochondrial ribosomal protein S12; Belongs to the universal ribosomal protein uS12 family. (139 aa) | ||||
ENSCPOP00000025122 | Uncharacterized protein. (122 aa) | ||||
PC | Pyruvate carboxylase; Catalyzes a 2-step reaction, involving the ATP-dependent carboxylation of the covalently attached biotin in the first step and the transfer of the carboxyl group to pyruvate in the second. (1219 aa) | ||||
MRPL15 | Mitochondrial ribosomal protein L15. (296 aa) | ||||
SIRT5 | NAD-dependent protein deacylase sirtuin-5, mitochondrial; NAD-dependent lysine demalonylase, desuccinylase and deglutarylase that specifically removes malonyl, succinyl and glutaryl groups on target proteins. Activates CPS1 and contributes to the regulation of blood ammonia levels during prolonged fasting: acts by mediating desuccinylation and deglutarylation of CPS1, thereby increasing CPS1 activity in response to elevated NAD levels during fasting. Activates SOD1 by mediating its desuccinylation, leading to reduced reactive oxygen species. Modulates ketogenesis through the desuccinyl [...] (309 aa) | ||||
MRPL41 | Mitochondrial ribosomal protein L41. (135 aa) | ||||
MRPS26 | Mitochondrial ribosomal protein S26. (248 aa) | ||||
MRPL14 | Mitochondrial ribosomal protein L14. (145 aa) | ||||
BCKDHB | Branched chain keto acid dehydrogenase E1 subunit beta. (392 aa) | ||||
BCKDK | Protein-serine/threonine kinase. (412 aa) | ||||
MRPL53 | Mitochondrial ribosomal protein L53. (112 aa) | ||||
DNA2 | DNA replication helicase/nuclease 2. (1021 aa) | ||||
MRPS14 | Mitochondrial ribosomal protein S14. (128 aa) | ||||
DHX30 | DExH-box helicase 30. (1218 aa) | ||||
MRPL49 | Mitochondrial ribosomal protein L49. (166 aa) | ||||
IDH3G | Isocitrate dehydrogenase [NAD] subunit, mitochondrial. (393 aa) | ||||
MRPL3 | Mitochondrial ribosomal protein L3; Belongs to the universal ribosomal protein uL3 family. (348 aa) | ||||
MRPL58 | Mitochondrial ribosomal protein L58. (206 aa) | ||||
Mrpl42 | Uncharacterized protein. (143 aa) | ||||
CREB1 | cAMP responsive element binding protein 1. (341 aa) | ||||
SOD2 | Superoxide dismutase [Mn], mitochondrial; Destroys superoxide anion radicals which are normally produced within the cells and which are toxic to biological systems. Belongs to the iron/manganese superoxide dismutase family. (222 aa) | ||||
PDK1 | Protein-serine/threonine kinase. (436 aa) | ||||
ENSCPOP00000021625 | Josephin domain-containing protein. (177 aa) | ||||
LYRM7 | LYR motif containing 7; Belongs to the complex I LYR family. (104 aa) | ||||
HAGHL | Hydroxyacylglutathione hydrolase like. (228 aa) | ||||
MRPL1 | Mitochondrial ribosomal protein L1. (324 aa) | ||||
DAP3 | Death associated protein 3. (397 aa) | ||||
ENSCPOP00000021986 | Uncharacterized protein. (224 aa) | ||||
CLPX | Caseinolytic mitochondrial matrix peptidase chaperone subunit. (633 aa) | ||||
GRPEL1 | GrpE protein homolog; Essential component of the PAM complex, a complex required for the translocation of transit peptide-containing proteins from the inner membrane into the mitochondrial matrix in an ATP-dependent manner; Belongs to the GrpE family. (217 aa) | ||||
PPIF | Peptidyl-prolyl cis-trans isomerase; PPIases accelerate the folding of proteins. It catalyzes the cis-trans isomerization of proline imidic peptide bonds in oligopeptides; Belongs to the cyclophilin-type PPIase family. (210 aa) | ||||
DDX28 | DEAD-box helicase 28. (537 aa) | ||||
ALKBH7 | AlkB homolog 7. (218 aa) | ||||
MRPS9 | Mitochondrial ribosomal protein S9; Belongs to the universal ribosomal protein uS9 family. (396 aa) | ||||
Parl | Rhomboid domain-containing protein. (379 aa) | ||||
MRPL55 | Mitochondrial ribosomal protein L55. (128 aa) | ||||
MRPS11 | Mitochondrial ribosomal protein S11; Belongs to the universal ribosomal protein uS11 family. (192 aa) | ||||
NUDT1 | Nudix hydrolase 1; Belongs to the Nudix hydrolase family. (156 aa) | ||||
Nfs1 | Aminotran_5 domain-containing protein. (436 aa) | ||||
MRPL24 | Mitochondrial ribosomal protein L24; Belongs to the universal ribosomal protein uL24 family. (216 aa) | ||||
MMUT | Methylmalonyl-CoA mutase. (749 aa) | ||||
CS | Citrate synthase; Belongs to the citrate synthase family. (466 aa) | ||||
ACAT1 | Acetyl-CoA acetyltransferase 1; Belongs to the thiolase-like superfamily. Thiolase family. (427 aa) | ||||
IDH3B | Isocitrate dehydrogenase [NAD] subunit, mitochondrial. (383 aa) | ||||
FDPS | Farnesyl diphosphate synthase; Belongs to the FPP/GGPP synthase family. (352 aa) | ||||
MRPS18B | Mitochondrial ribosomal protein S18B. (259 aa) | ||||
ACADS | Acyl-CoA dehydrogenase short chain. (413 aa) | ||||
TYMS | Thymidylate synthetase. (314 aa) | ||||
MRPL19 | Mitochondrial ribosomal protein L19. (292 aa) | ||||
Wee2 | Wee1-like protein kinase. (557 aa) | ||||
MARS2 | Methionyl-tRNA synthetase 2, mitochondrial; Belongs to the class-I aminoacyl-tRNA synthetase family. (592 aa) | ||||
ACADVL | Acyl-CoA dehydrogenase very long chain. (633 aa) | ||||
TST | Sulfurtransferase. (297 aa) | ||||
PPP1R26 | Protein phosphatase 1 regulatory subunit 26. (1240 aa) | ||||
ATAD3A | ATPase family AAA domain containing 3A. (584 aa) | ||||
MRPL9 | Mitochondrial ribosomal protein L9. (270 aa) | ||||
MRPL40 | Mitochondrial ribosomal protein L40. (205 aa) | ||||
MTERF4 | Mitochondrial transcription termination factor 4. (341 aa) | ||||
DTYMK | Deoxythymidylate kinase. (212 aa) | ||||
MRPS25 | Mitochondrial ribosomal protein S25. (173 aa) | ||||
HSPD1 | Uncharacterized protein; Belongs to the chaperonin (HSP60) family. (574 aa) | ||||
MRPL27 | Mitochondrial ribosomal protein L27. (148 aa) | ||||
MRPS16 | Mitochondrial ribosomal protein S16. (135 aa) | ||||
MRPL39 | Mitochondrial ribosomal protein L39. (335 aa) | ||||
PDK2 | Protein-serine/threonine kinase. (407 aa) | ||||
MRPL38 | Mitochondrial ribosomal protein L38. (380 aa) | ||||
ACSS1 | Acetyl-coenzyme A synthetase. (647 aa) | ||||
FASTKD5 | FAST kinase domains 5. (795 aa) | ||||
MRPS18A | Mitochondrial ribosomal protein S18A. (196 aa) | ||||
MRPS21 | Mitochondrial ribosomal protein S21. (87 aa) | ||||
IVD | Isovaleryl-CoA dehydrogenase. (426 aa) | ||||
MTG2 | Mitochondrial ribosome associated GTPase 2. (459 aa) | ||||
Mrpl23 | Uncharacterized protein. (149 aa) | ||||
LOC100715002 | Uncharacterized protein; Belongs to the GroES chaperonin family. (102 aa) | ||||
MRPL34 | Mitochondrial ribosomal protein L34. (86 aa) | ||||
MRPL54 | Mitochondrial ribosomal protein L54. (138 aa) | ||||
ACSM1 | Acyl-CoA synthetase medium chain family member 1. (524 aa) | ||||
UQCC2 | Ubiquinol-cytochrome c reductase complex assembly factor 2. (136 aa) | ||||
MIPEP | Mitochondrial intermediate peptidase. (713 aa) | ||||
MRPL18 | Mitochondrial ribosomal protein L18. (204 aa) | ||||
TFAM | Transcription factor A, mitochondrial. (235 aa) | ||||
MRPS2 | Mitochondrial ribosomal protein S2. (285 aa) | ||||
ENSCPOP00000029518 | Uncharacterized protein. (106 aa) | ||||
SARDH | Sarcosine dehydrogenase. (919 aa) | ||||
GLRX2 | Glutaredoxin 2. (160 aa) | ||||
MRPL43 | Mitochondrial ribosomal protein L43. (159 aa) | ||||
MRPL35 | Mitochondrial ribosomal protein L35. (201 aa) | ||||
MRPL32 | Mitochondrial ribosomal protein L32. (184 aa) | ||||
MRPL36 | Ribosomal protein; Belongs to the bacterial ribosomal protein bL36 family. (102 aa) | ||||
MRPL17 | Mitochondrial ribosomal protein L17; Belongs to the bacterial ribosomal protein bL17 family. (176 aa) | ||||
MRPS6 | Mitochondrial ribosomal protein S6. (109 aa) | ||||
TFB1M | rRNA adenine N(6)-methyltransferase; Belongs to the class I-like SAM-binding methyltransferase superfamily. rRNA adenine N(6)-methyltransferase family. (346 aa) | ||||
CCDC32 | Coiled-coil domain containing 32. (178 aa) | ||||
LONP1 | Lon protease homolog, mitochondrial; ATP-dependent serine protease that mediates the selective degradation of misfolded, unassembled or oxidatively damaged polypeptides as well as certain short-lived regulatory proteins in the mitochondrial matrix. May also have a chaperone function in the assembly of inner membrane protein complexes. Participates in the regulation of mitochondrial gene expression and in the maintenance of the integrity of the mitochondrial genome. Binds to mitochondrial promoters and RNA in a single-stranded, site-specific, and strand- specific manner. May regulate mi [...] (1003 aa) | ||||
SIRT3 | NAD-dependent protein deacetylase; NAD-dependent protein deacetylase. (257 aa) | ||||
MRPL44 | Mitochondrial ribosomal protein L44. (332 aa) | ||||
OGDHL | Oxoglutarate dehydrogenase like. (1022 aa) | ||||
H0W9P9_CAVPO | Wee1-like protein kinase. (551 aa) | ||||
DNAJC19 | DnaJ heat shock protein family (Hsp40) member C19. (130 aa) | ||||
H0WAF5_CAVPO | Iso_dh domain-containing protein. (332 aa) | ||||
Mrpl2 | Mitochondrial ribosomal protein L2. (305 aa) | ||||
ACOT13 | Acyl-CoA thioesterase 13. (140 aa) | ||||
LOC100725076 | Iso_dh domain-containing protein. (377 aa) | ||||
GSTK1 | Glutathione S-transferase kappa. (226 aa) | ||||
C3orf18 | Chromosome 3 open reading frame 18. (154 aa) | ||||
Mrps17 | Uncharacterized protein. (30 aa) | ||||
TOP1MT | DNA topoisomerase I; Releases the supercoiling and torsional tension of DNA introduced during the DNA replication and transcription by transiently cleaving and rejoining one strand of the DNA duplex. Introduces a single-strand break via transesterification at the specific target site 5'-[CT]CCTTp site in duplex DNA. The scissile phosphodiester is attacked by the catalytic tyrosine of the enzyme, resulting in the formation of a DNA-(3'-phosphotyrosyl)-enzyme intermediate and the expulsion of a 5'-OH DNA strand. The free DNA strand then undergoes passage around the unbroken strand thus r [...] (629 aa) | ||||
MRPS27 | Mitochondrial ribosomal protein S27. (415 aa) | ||||
SUCLG2 | Succinate--CoA ligase [GDP-forming] subunit beta, mitochondrial; GTP-specific succinyl-CoA synthetase functions in the citric acid cycle (TCA), coupling the hydrolysis of succinyl-CoA to the synthesis of GTP and thus represents the only step of substrate-level phosphorylation in the TCA. The beta subunit provides nucleotide specificity of the enzyme and binds the substrate succinate, while the binding sites for coenzyme A and phosphate are found in the alpha subunit. (404 aa) | ||||
NAGK | N-acetylglucosamine kinase. (345 aa) | ||||
MRPL48 | Mitochondrial ribosomal protein L48. (212 aa) | ||||
Tfb2m | rRNA adenine N(6)-methyltransferase; Belongs to the class I-like SAM-binding methyltransferase superfamily. rRNA adenine N(6)-methyltransferase family. (392 aa) | ||||
MTHFD1 | Methylenetetrahydrofolate dehydrogenase, cyclohydrolase and formyltetrahydrofolate synthetase 1. (928 aa) | ||||
CAPN10 | Calpain 10; Belongs to the peptidase C2 family. (667 aa) | ||||
PTCD3 | Pentatricopeptide repeat domain 3. (690 aa) | ||||
SIRT4 | NAD-dependent protein lipoamidase sirtuin-4, mitochondrial; Acts as NAD-dependent protein lipoamidase, ADP-ribosyl transferase and deacetylase. Catalyzes more efficiently removal of lipoyl- and biotinyl- than acetyl-lysine modifications. Inhibits the pyruvate dehydrogenase complex (PDH) activity via the enzymatic hydrolysis of the lipoamide cofactor from the E2 component, DLAT, in a phosphorylation-independent manner. Catalyzes the transfer of ADP- ribosyl groups onto target proteins, including mitochondrial GLUD1, inhibiting GLUD1 enzyme activity. Acts as a negative regulator of mitoc [...] (314 aa) | ||||
AK3 | GTP:AMP phosphotransferase AK3, mitochondrial; Involved in maintaining the homeostasis of cellular nucleotides by catalyzing the interconversion of nucleoside phosphates. Has GTP:AMP phosphotransferase and ITP:AMP phosphotransferase activities. (228 aa) | ||||
TEFM | Transcription elongation factor, mitochondrial. (356 aa) | ||||
MRPL37 | Mitochondrial ribosomal protein L37. (419 aa) | ||||
GRSF1 | G-rich RNA sequence binding factor 1. (471 aa) | ||||
PCCA | Propionyl-CoA carboxylase subunit alpha. (728 aa) | ||||
ACADM | Acyl-CoA dehydrogenase medium chain. (363 aa) | ||||
Atxn3 | Josephin domain-containing protein. (351 aa) | ||||
MRPS15 | Mitochondrial ribosomal protein S15; Belongs to the universal ribosomal protein uS15 family. (254 aa) | ||||
MCCC1 | Methylcrotonoyl-CoA carboxylase 1. (725 aa) | ||||
Mrpl30 | Ribosomal_L30 domain-containing protein. (155 aa) | ||||
MRPS35 | Mitochondrial ribosomal protein S35. (288 aa) | ||||
REXO2 | RNA exonuclease 2. (237 aa) | ||||
TUFM | Elongation factor Tu; This protein promotes the GTP-dependent binding of aminoacyl- tRNA to the A-site of ribosomes during protein biosynthesis. (452 aa) | ||||
OAT | Ornithine aminotransferase; Belongs to the class-III pyridoxal-phosphate-dependent aminotransferase family. (439 aa) | ||||
DGLUCY | D-glutamate cyclase. (554 aa) | ||||
NDUFA9 | NADH:ubiquinone oxidoreductase subunit A9. (377 aa) | ||||
MDH2 | Malate dehydrogenase. (338 aa) | ||||
SUPV3L1 | Suv3 like RNA helicase. (786 aa) | ||||
ACADL | Acyl-CoA dehydrogenase long chain. (432 aa) | ||||
ERAL1 | Era like 12S mitochondrial rRNA chaperone 1. (437 aa) | ||||
MRPL52 | Mitochondrial ribosomal protein L52. (123 aa) | ||||
SLC25A5 | Solute carrier family 25 member 5; Belongs to the mitochondrial carrier (TC 2.A.29) family. (298 aa) | ||||
MRPS18C | Mitochondrial ribosomal protein S18C; Belongs to the bacterial ribosomal protein bS18 family. (144 aa) | ||||
ELAC2 | ElaC ribonuclease Z 2. (833 aa) | ||||
ACSM3 | Acyl-CoA synthetase medium chain family member 3. (585 aa) | ||||
MRPS23 | Mitochondrial ribosomal protein S23. (140 aa) | ||||
DNAJA3 | DnaJ heat shock protein family (Hsp40) member A3. (479 aa) | ||||
MRPL51 | Mitochondrial ribosomal protein L51. (128 aa) | ||||
PMPCB | Peptidase, mitochondrial processing beta subunit; Belongs to the peptidase M16 family. (490 aa) | ||||
POLG | DNA polymerase gamma, catalytic subunit. (1206 aa) | ||||
PMPCA | Peptidase, mitochondrial processing alpha subunit; Belongs to the peptidase M16 family. (527 aa) | ||||
MRPL28 | Mitochondrial ribosomal protein L28. (256 aa) | ||||
POLG2 | DNA polymerase gamma 2, accessory subunit. (482 aa) | ||||
MTERF2 | Mitochondrial transcription termination factor 2. (389 aa) | ||||
C3orf20 | Chromosome 3 open reading frame 20. (898 aa) | ||||
NSUN4 | NOP2/Sun RNA methyltransferase 4; Belongs to the class I-like SAM-binding methyltransferase superfamily. RsmB/NOP family. (381 aa) | ||||
DBT | Dihydrolipoamide acetyltransferase component of pyruvate dehydrogenase complex. (482 aa) | ||||
MRPL22 | Mitochondrial ribosomal protein L22; Belongs to the universal ribosomal protein uL22 family. (210 aa) | ||||
PDHB | Pyruvate dehydrogenase E1 component subunit beta; The pyruvate dehydrogenase complex catalyzes the overall conversion of pyruvate to acetyl-CoA and CO2. (359 aa) | ||||
MRPL4 | Mitochondrial ribosomal protein L4. (296 aa) | ||||
HMGCS2 | 3-hydroxy-3-methylglutaryl coenzyme A synthase; This enzyme condenses acetyl-CoA with acetoacetyl-CoA to form HMG-CoA, which is the substrate for HMG-CoA reductase. (508 aa) | ||||
COASY | Coenzyme A synthase. (563 aa) | ||||
HADHA | Hydroxyacyl-CoA dehydrogenase trifunctional multienzyme complex subunit alpha; Belongs to the enoyl-CoA hydratase/isomerase family. (762 aa) | ||||
METTL4 | Methyltransferase like 4; Belongs to the MT-A70-like family. (470 aa) | ||||
MRPL13 | Mitochondrial ribosomal protein L13; Belongs to the universal ribosomal protein uL13 family. (178 aa) | ||||
FASTKD2 | FAST kinase domains 2. (673 aa) | ||||
HADHB | Hydroxyacyl-CoA dehydrogenase trifunctional multienzyme complex subunit beta; Belongs to the thiolase-like superfamily. Thiolase family. (487 aa) | ||||
MRPS34 | Mitochondrial ribosomal protein S34. (218 aa) | ||||
Glud1 | Glutamate dehydrogenase; Belongs to the Glu/Leu/Phe/Val dehydrogenases family. (540 aa) | ||||
MRPL16 | Mitochondrial ribosomal protein L16; Belongs to the universal ribosomal protein uL16 family. (251 aa) | ||||
H0V3Y8_CAVPO | PRORP domain-containing protein. (566 aa) | ||||
ACAA2 | Acetyl-CoA acyltransferase 2; Belongs to the thiolase-like superfamily. Thiolase family. (397 aa) | ||||
MRPS5 | Mitochondrial ribosomal protein S5; Belongs to the universal ribosomal protein uS5 family. (431 aa) | ||||
MRM1 | Mitochondrial rRNA methyltransferase 1. (350 aa) | ||||
CPS1 | Carbamoyl-phosphate synthase 1. (1499 aa) | ||||
ETFBKMT | Electron transfer flavoprotein subunit beta lysine methyltransferase. (254 aa) | ||||
MTERF1 | Mitochondrial transcription termination factor 1. (409 aa) |