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TTLL12 | LOW QUALITY PROTEIN: tubulin--tyrosine ligase-like protein 12. (626 aa) | ||||
ACADSB | Short/branched chain specific acyl-CoA dehydrogenase, mitochondrial isoform X1. (432 aa) | ||||
BCAT2 | LOW QUALITY PROTEIN: branched-chain-amino-acid aminotransferase, mitochondrial. (528 aa) | ||||
MCCC1 | methylcrotonoyl-CoA carboxylase subunit alpha, mitochondrial isoform X1. (725 aa) | ||||
ALDH16A1 | Aldehyde dehydrogenase family 16 member A1. (802 aa) | ||||
IL4I1 | L-amino-acid oxidase. (588 aa) | ||||
BCKDHA | 2-oxoisovalerate dehydrogenase subunit alpha; The branched-chain alpha-keto dehydrogenase complex catalyzes the overall conversion of alpha-keto acids to acyl-CoA and CO(2). It contains multiple copies of three enzymatic components: branched-chain alpha-keto acid decarboxylase (E1), lipoamide acyltransferase (E2) and lipoamide dehydrogenase (E3). (445 aa) | ||||
EHHADH | Peroxisomal bifunctional enzyme. (723 aa) | ||||
TNPO2 | Transportin-2 isoform X1. (990 aa) | ||||
ACAT1 | acetyl-CoA acetyltransferase, mitochondrial; Belongs to the thiolase-like superfamily. Thiolase family. (427 aa) | ||||
HMGCL | hydroxymethylglutaryl-CoA lyase, mitochondrial isoform X1. (325 aa) | ||||
MUT | methylmalonyl-CoA mutase, mitochondrial. (750 aa) | ||||
HADHB | Trifunctional enzyme subunit beta, mitochondrial isoform X1; Belongs to the thiolase-like superfamily. Thiolase family. (491 aa) | ||||
HMGCS2 | 3-hydroxy-3-methylglutaryl coenzyme A synthase; This enzyme condenses acetyl-CoA with acetoacetyl-CoA to form HMG-CoA, which is the substrate for HMG-CoA reductase. (553 aa) | ||||
HADHA | Trifunctional enzyme subunit alpha, mitochondrial; Belongs to the enoyl-CoA hydratase/isomerase family. (763 aa) | ||||
ECHS1 | enoyl-CoA hydratase, mitochondrial; Belongs to the enoyl-CoA hydratase/isomerase family. (293 aa) | ||||
ACAD11 | acyl-CoA dehydrogenase family member 11 isoform X1. (781 aa) | ||||
ABAT | 4-aminobutyrate aminotransferase, mitochondrial isoform X1; Belongs to the class-III pyridoxal-phosphate-dependent aminotransferase family. (513 aa) | ||||
AACS | acetoacetyl-CoA synthetase isoform X1. (672 aa) | ||||
SETD3 | Protein-histidine N-methyltransferase. (601 aa) | ||||
SETD4 | SET domain-containing protein 4 isoform X1. (440 aa) | ||||
ACAD10 | acyl-CoA dehydrogenase family member 10 isoform X1. (1086 aa) | ||||
BCKDHB | 2-oxoisovalerate dehydrogenase subunit beta, mitochondrial isoform X1. (395 aa) | ||||
HSD17B10 | 3-hydroxyacyl-CoA dehydrogenase type-2; Belongs to the short-chain dehydrogenases/reductases (SDR) family. (261 aa) | ||||
ALDH7A1 | Alpha-aminoadipic semialdehyde dehydrogenase; Belongs to the aldehyde dehydrogenase family. (539 aa) | ||||
AOX1 | Aldehyde oxidase. (1338 aa) | ||||
ACAD8 | isobutyryl-CoA dehydrogenase, mitochondrial isoform X1. (450 aa) | ||||
ACAA2 | 3-ketoacyl-CoA thiolase, mitochondrial isoform X1; Belongs to the thiolase-like superfamily. Thiolase family. (398 aa) | ||||
CARTPT | Cocaine- and amphetamine-regulated transcript protein. (116 aa) | ||||
ACAA1 | 3-ketoacyl-CoA thiolase, peroxisomal; Belongs to the thiolase-like superfamily. Thiolase family. (426 aa) | ||||
MCCC2 | methylcrotonoyl-CoA carboxylase beta chain, mitochondrial. (563 aa) | ||||
HIBADH | 3-hydroxyisobutyrate dehydrogenase, mitochondrial. (336 aa) | ||||
HMGCLL1 | 3-hydroxymethyl-3-methylglutaryl-CoA lyase, cytoplasmic isoform X1. (340 aa) | ||||
AGXT2 | Alanine--glyoxylate aminotransferase 2, mitochondrial isoform X1; Belongs to the class-III pyridoxal-phosphate-dependent aminotransferase family. (514 aa) | ||||
ALDH3A2 | Aldehyde dehydrogenase; Belongs to the aldehyde dehydrogenase family. (485 aa) | ||||
DBT | Dihydrolipoamide acetyltransferase component of pyruvate dehydrogenase complex. (482 aa) | ||||
ACAT2 | acetyl-CoA acetyltransferase, cytosolic; Belongs to the thiolase-like superfamily. Thiolase family. (397 aa) | ||||
LOC112401269 | LOW QUALITY PROTEIN: methylglutaconyl-CoA hydratase, mitochondrial-like. (323 aa) | ||||
PCCB | propionyl-CoA carboxylase beta chain, mitochondrial. (540 aa) | ||||
LOC112399533 | Amine oxidase. (529 aa) | ||||
MCEE | methylmalonyl-CoA epimerase, mitochondrial. (176 aa) | ||||
ACADS | Short-chain specific acyl-CoA dehydrogenase, mitochondrial isoform X1. (412 aa) | ||||
DLD | Dihydrolipoyl dehydrogenase. (509 aa) | ||||
ALDH9A1 | 4-trimethylaminobutyraldehyde dehydrogenase; Belongs to the aldehyde dehydrogenase family. (518 aa) | ||||
HADH | Hydroxyacyl-coenzyme A dehydrogenase, mitochondrial. (314 aa) | ||||
OXCT1 | Succinyl-CoA:3-ketoacid-coenzyme A transferase; Key enzyme for ketone body catabolism. Transfers the CoA moiety from succinate to acetoacetate. Formation of the enzyme-CoA intermediate proceeds via an unstable anhydride species formed between the carboxylate groups of the enzyme and substrate. (520 aa) | ||||
ALDH2 | Aldehyde dehydrogenase, mitochondrial; Belongs to the aldehyde dehydrogenase family. (519 aa) | ||||
PCCA | propionyl-CoA carboxylase alpha chain, mitochondrial. (730 aa) | ||||
HMGCS1 | 3-hydroxy-3-methylglutaryl coenzyme A synthase; This enzyme condenses acetyl-CoA with acetoacetyl-CoA to form HMG-CoA, which is the substrate for HMG-CoA reductase. (552 aa) | ||||
ECHDC2 | enoyl-CoA hydratase domain-containing protein 2, mitochondrial isoform X1; Belongs to the enoyl-CoA hydratase/isomerase family. (296 aa) | ||||
ALDH6A1 | Methylmalonate-semialdehyde dehydrogenase [acylating], mitochondrial. (479 aa) | ||||
OXCT2 | succinyl-CoA:3-ketoacid coenzyme A transferase 2, mitochondrial. (349 aa) | ||||
ACSF3 | acyl-CoA synthetase family member 3, mitochondrial. (628 aa) | ||||
ACADM | Medium-chain specific acyl-CoA dehydrogenase, mitochondrial isoform X1. (421 aa) | ||||
HIBCH | 3-hydroxyisobutyryl-CoA hydrolase, mitochondrial; Hydrolyzes 3-hydroxyisobutyryl-CoA (HIBYL-CoA), a saline catabolite; Belongs to the enoyl-CoA hydratase/isomerase family. (386 aa) | ||||
ALDH1B1 | LOW QUALITY PROTEIN: aldehyde dehydrogenase X, mitochondrial; Belongs to the aldehyde dehydrogenase family. (517 aa) | ||||
BCAT1 | Branched-chain-amino-acid aminotransferase; Belongs to the class-IV pyridoxal-phosphate-dependent aminotransferase family. (458 aa) | ||||
IVD | isovaleryl-CoA dehydrogenase, mitochondrial. (426 aa) | ||||
AUH | methylglutaconyl-CoA hydratase, mitochondrial isoform X1; Belongs to the enoyl-CoA hydratase/isomerase family. (339 aa) | ||||
TNPO1 | Transportin-1 isoform X1. (898 aa) |