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PCCA | propionyl-CoA carboxylase alpha chain, mitochondrial isoform X1. (728 aa) | ||||
ECI2 | enoyl-CoA delta isomerase 2, mitochondrial isoform X2. (364 aa) | ||||
MCAT | malonyl-CoA-acyl carrier protein transacylase, mitochondrial isoform X1. (386 aa) | ||||
LOC103270912 | S-(hydroxymethyl)glutathione dehydrogenase; Belongs to the zinc-containing alcohol dehydrogenase family. Class-III subfamily. (374 aa) | ||||
CPT2 | Carnitine O-palmitoyltransferase 2, mitochondrial; Belongs to the carnitine/choline acetyltransferase family. (658 aa) | ||||
HMGCL | hydroxymethylglutaryl-CoA lyase, mitochondrial isoform X1. (325 aa) | ||||
LOC103251566 | Non-specific lipid-transfer protein; Belongs to the thiolase-like superfamily. Thiolase family. (354 aa) | ||||
PEX7 | Peroxisomal biogenesis factor 7. (323 aa) | ||||
ETFB | Electron transfer flavoprotein subunit beta isoform X1. (294 aa) | ||||
ACAA2 | 3-ketoacyl-CoA thiolase, mitochondrial; Belongs to the thiolase-like superfamily. Thiolase family. (397 aa) | ||||
ETFDH | Electron transfer flavoprotein-ubiquinone oxidoreductase; Accepts electrons from ETF and reduces ubiquinone. (617 aa) | ||||
ACSM2B | Acyl-coenzyme A synthetase ACSM2B, mitochondrial. (577 aa) | ||||
LOC103272380 | S-(hydroxymethyl)glutathione dehydrogenase; Belongs to the zinc-containing alcohol dehydrogenase family. Class-III subfamily. (379 aa) | ||||
MCCC2 | methylcrotonoyl-CoA carboxylase beta chain, mitochondrial. (563 aa) | ||||
ACADVL | Very long-chain specific acyl-CoA dehydrogenase, mitochondrial isoform X6. (654 aa) | ||||
ALDH7A1 | Alpha-aminoadipic semialdehyde dehydrogenase isoform X1; Belongs to the aldehyde dehydrogenase family. (556 aa) | ||||
ALDH3A2 | Aldehyde dehydrogenase; Belongs to the aldehyde dehydrogenase family. (507 aa) | ||||
LOC103260222 | Alcohol dehydrogenase 1C. (366 aa) | ||||
ACSM6 | Acyl-coenzyme A synthetase ACSM6, mitochondrial. (309 aa) | ||||
ECH1 | delta(3,5)-Delta(2,4)-dienoyl-CoA isomerase, mitochondrial; Belongs to the enoyl-CoA hydratase/isomerase family. (320 aa) | ||||
ACAT2 | acetyl-CoA acetyltransferase, cytosolic; Belongs to the thiolase-like superfamily. Thiolase family. (397 aa) | ||||
GCDH | glutaryl-CoA dehydrogenase, mitochondrial isoform X1. (435 aa) | ||||
SBSPON | somatomedin-B and thrombospondin type-1 domain-containing protein. (244 aa) | ||||
AUH | methylglutaconyl-CoA hydratase, mitochondrial; Belongs to the enoyl-CoA hydratase/isomerase family. (339 aa) | ||||
LOC103249515 | WW domain-containing oxidoreductase-like. (185 aa) | ||||
ACSS2 | Acetyl-coenzyme A synthetase, cytoplasmic isoform X1. (714 aa) | ||||
ACOX2 | Acyl-coenzyme A oxidase; Belongs to the acyl-CoA oxidase family. (680 aa) | ||||
LOC103272372 | Malic enzyme. (260 aa) | ||||
ACAD10 | acyl-CoA dehydrogenase family member 10. (1059 aa) | ||||
AASDHPPT | L-aminoadipate-semialdehyde dehydrogenase-phosphopantetheinyl transferase. (309 aa) | ||||
AKR1A1 | Alcohol dehydrogenase [NADP(+)]. (323 aa) | ||||
HLCS | Biotin--protein ligase. (727 aa) | ||||
ACOX3 | Acyl-coenzyme A oxidase; Belongs to the acyl-CoA oxidase family. (693 aa) | ||||
HSD17B14 | 17-beta-hydroxysteroid dehydrogenase 14; Belongs to the short-chain dehydrogenases/reductases (SDR) family. (229 aa) | ||||
MECR | Enoyl-[acyl-carrier-protein] reductase, mitochondrial. (373 aa) | ||||
ACSM5 | Acyl-coenzyme A synthetase ACSM5, mitochondrial. (579 aa) | ||||
AASDH | acyl-CoA synthetase family member 4 isoform X1. (1092 aa) | ||||
HADHA | Trifunctional enzyme subunit alpha, mitochondrial isoform X2; Belongs to the enoyl-CoA hydratase/isomerase family. (763 aa) | ||||
ACADM | Medium-chain specific acyl-CoA dehydrogenase, mitochondrial. (438 aa) | ||||
ACADL | Long-chain specific acyl-CoA dehydrogenase, mitochondrial. (430 aa) | ||||
ADH4 | LOW QUALITY PROTEIN: alcohol dehydrogenase 4. (375 aa) | ||||
DHRS7B | Dehydrogenase/reductase SDR family member 7B; Belongs to the short-chain dehydrogenases/reductases (SDR) family. (325 aa) | ||||
ALDH1B1 | Aldehyde dehydrogenase X, mitochondrial; Belongs to the aldehyde dehydrogenase family. (517 aa) | ||||
LOC103272478 | LOW QUALITY PROTEIN: acyl-coenzyme A synthetase ACSM1, mitochondrial-like. (567 aa) | ||||
ADHFE1 | Hydroxyacid-oxoacid transhydrogenase, mitochondrial. (447 aa) | ||||
ACSS3 | acyl-CoA synthetase short-chain family member 3, mitochondrial. (687 aa) | ||||
AMACR | alpha-methylacyl-CoA racemase isoform X1. (396 aa) | ||||
PEX13 | Peroxisome biogenesis factor 13. (400 aa) | ||||
HMGCLL1 | 3-hydroxymethyl-3-methylglutaryl-CoA lyase, cytoplasmic isoform X1. (370 aa) | ||||
LOC103251086 | PEX5-related protein. (318 aa) | ||||
LOC103272785 | Aldehyde dehydrogenase, mitochondrial; Belongs to the aldehyde dehydrogenase family. (363 aa) | ||||
ACBD7 | acyl-CoA-binding domain-containing protein 7. (88 aa) | ||||
ENSTSYP00000009240 | annotation not available (338 aa) | ||||
ACSF3 | acyl-CoA synthetase family member 3, mitochondrial. (569 aa) | ||||
HACL1 | 2-hydroxyacyl-CoA lyase 1. (516 aa) | ||||
BCAT1 | Branched-chain-amino-acid aminotransferase; Belongs to the class-IV pyridoxal-phosphate-dependent aminotransferase family. (386 aa) | ||||
HADH | Hydroxyacyl-coenzyme A dehydrogenase, mitochondrial isoform X1. (383 aa) | ||||
ABHD14A | Protein ABHD14A isoform X2. (268 aa) | ||||
DIP2A | Disco-interacting protein 2 homolog A isoform X1. (1570 aa) | ||||
IVD | isovaleryl-CoA dehydrogenase, mitochondrial isoform X4. (429 aa) | ||||
ALDH9A1 | 4-trimethylaminobutyraldehyde dehydrogenase isoform X3; Belongs to the aldehyde dehydrogenase family. (494 aa) | ||||
ECHDC1 | ethylmalonyl-CoA decarboxylase isoform X1; Belongs to the enoyl-CoA hydratase/isomerase family. (307 aa) | ||||
ACSM3 | Acyl-coenzyme A synthetase ACSM3, mitochondrial. (586 aa) | ||||
HIBCH | 3-hydroxyisobutyryl-CoA hydrolase, mitochondrial; Hydrolyzes 3-hydroxyisobutyryl-CoA (HIBYL-CoA), a saline catabolite; Belongs to the enoyl-CoA hydratase/isomerase family. (293 aa) | ||||
MCCC1 | methylcrotonoyl-CoA carboxylase subunit alpha, mitochondrial. (725 aa) | ||||
ACAT1 | acetyl-CoA acetyltransferase, mitochondrial; Belongs to the thiolase-like superfamily. Thiolase family. (430 aa) | ||||
ALDH6A1 | Methylmalonate-semialdehyde dehydrogenase [acylating], mitochondrial isoform X1. (533 aa) | ||||
ACSM4 | Acyl-coenzyme A synthetase ACSM4, mitochondrial. (579 aa) | ||||
PEX12 | Peroxisome assembly protein 12; Required for protein import into peroxisomes. Belongs to the pex2/pex10/pex12 family. (359 aa) | ||||
DIP2B | Disco-interacting protein 2 homolog B isoform X1. (1567 aa) | ||||
ACOT12 | LOW QUALITY PROTEIN: acyl-coenzyme A thioesterase 12. (165 aa) | ||||
ALDH3A1 | Aldehyde dehydrogenase; Belongs to the aldehyde dehydrogenase family. (453 aa) | ||||
ESD | S-formylglutathione hydrolase; Serine hydrolase involved in the detoxification of formaldehyde. (282 aa) | ||||
ACOXL | Acyl-coenzyme A oxidase; Belongs to the acyl-CoA oxidase family. (547 aa) | ||||
CHDH | Choline dehydrogenase, mitochondrial. (599 aa) | ||||
MCEE | methylmalonyl-CoA epimerase, mitochondrial. (180 aa) | ||||
ACACB | LOW QUALITY PROTEIN: acetyl-CoA carboxylase 2. (2433 aa) | ||||
OXCT1 | Succinyl-CoA:3-ketoacid-coenzyme A transferase; Key enzyme for ketone body catabolism. Transfers the CoA moiety from succinate to acetoacetate. Formation of the enzyme-CoA intermediate proceeds via an unstable anhydride species formed between the carboxylate groups of the enzyme and substrate. (520 aa) | ||||
ACADSB | Short/branched chain specific acyl-CoA dehydrogenase, mitochondrial. (432 aa) | ||||
ALDH1L2 | Mitochondrial 10-formyltetrahydrofolate dehydrogenase; Belongs to the aldehyde dehydrogenase family. (909 aa) | ||||
OXSM | 3-oxoacyl-[acyl-carrier-protein] synthase, mitochondrial; May play a role in the biosynthesis of lipoic acid as well as longer chain fatty acids required for optimal mitochondrial function. Belongs to the thiolase-like superfamily. Beta-ketoacyl-ACP synthases family. (460 aa) | ||||
LOC103256177 | Uncharacterized protein LOC103256177. (163 aa) | ||||
LOC103251152 | Dehydrogenase/reductase SDR family member 7 isoform X1; Belongs to the short-chain dehydrogenases/reductases (SDR) family. (350 aa) | ||||
PALB2 | Partner and localizer of BRCA2 isoform X1. (1177 aa) | ||||
LOC103262046 | Peroxisomal multifunctional enzyme type 2. (528 aa) | ||||
WWOX | WW domain-containing oxidoreductase. (186 aa) | ||||
ECHS1 | enoyl-CoA hydratase, mitochondrial isoform X1; Belongs to the enoyl-CoA hydratase/isomerase family. (290 aa) | ||||
ABHD10 | Mycophenolic acid acyl-glucuronide esterase, mitochondrial isoform X1. (306 aa) | ||||
CRAT | Carnitine O-acetyltransferase; Belongs to the carnitine/choline acetyltransferase family. (577 aa) | ||||
ETFA | Electron transfer flavoprotein subunit alpha, mitochondrial isoform X1. (333 aa) | ||||
FASN | Fatty acid synthase isoform X1. (2508 aa) | ||||
ALDH3B1 | Aldehyde dehydrogenase family 3 member B1-like; Belongs to the aldehyde dehydrogenase family. (271 aa) | ||||
ENSTSYP00000015124 | annotation not available (311 aa) | ||||
ACAD8 | isobutyryl-CoA dehydrogenase, mitochondrial. (415 aa) | ||||
HIBCH-2 | 3-hydroxyisobutyryl-CoA hydrolase, mitochondrial; Hydrolyzes 3-hydroxyisobutyryl-CoA (HIBYL-CoA), a saline catabolite; Belongs to the enoyl-CoA hydratase/isomerase family. (89 aa) | ||||
ECI1 | enoyl-CoA delta isomerase 1, mitochondrial; Belongs to the enoyl-CoA hydratase/isomerase family. (243 aa) | ||||
DECR2 | Peroxisomal 2,4-dienoyl-CoA reductase. (294 aa) | ||||
CRYZ | Quinone oxidoreductase isoform X1. (330 aa) | ||||
EPHX2 | Bifunctional epoxide hydrolase 2. (521 aa) | ||||
LOC103272231 | Dehydrogenase/reductase SDR family member 1-like. (313 aa) | ||||
CRYZL1 | Quinone oxidoreductase-like protein 1 isoform X2. (349 aa) | ||||
LOC103262004 | Non-specific lipid-transfer protein isoform X1. (143 aa) | ||||
LOC103252664 | LOW QUALITY PROTEIN: quinone oxidoreductase-like. (315 aa) | ||||
PEX14 | Peroxisomal membrane protein PEX14 isoform X1. (377 aa) | ||||
HSD17B8 | Estradiol 17-beta-dehydrogenase 8. (259 aa) | ||||
HTRA4 | Serine protease HTRA4. (155 aa) | ||||
ILVBL | Acetolactate synthase-like protein; Belongs to the TPP enzyme family. (632 aa) | ||||
PAOX | Peroxisomal N(1)-acetyl-spermine/spermidine oxidase. (450 aa) | ||||
PC | Pyruvate carboxylase, mitochondrial. (298 aa) | ||||
BPHL | Valacyclovir hydrolase. (291 aa) | ||||
ENSTSYP00000020300 | annotation not available (186 aa) | ||||
ABHD11 | Protein ABHD11. (83 aa) | ||||
FAHD2A | Fumarylacetoacetate hydrolase domain-containing protein 2A. (314 aa) | ||||
PHYH | phytanoyl-CoA dioxygenase, peroxisomal. (328 aa) | ||||
HADHB | Trifunctional enzyme subunit beta, mitochondrial; Belongs to the thiolase-like superfamily. Thiolase family. (462 aa) | ||||
ACAD11 | acyl-CoA dehydrogenase family member 11. (781 aa) | ||||
ACSF2 | acyl-CoA synthetase family member 2, mitochondrial. (629 aa) | ||||
ENSTSYP00000023374 | annotation not available (199 aa) | ||||
ECHDC2 | enoyl-CoA hydratase domain-containing protein 2, mitochondrial isoform X1; Belongs to the enoyl-CoA hydratase/isomerase family. (251 aa) | ||||
RPP14-2 | Ribonuclease P protein subunit p14 isoform X1. (152 aa) | ||||
ALDH8A1 | Aldehyde dehydrogenase family 8 member A1 isoform X1; Belongs to the aldehyde dehydrogenase family. (487 aa) | ||||
FAM185A | Protein FAM185A isoform X1. (390 aa) | ||||
ACOX1 | Acyl-coenzyme A oxidase; Belongs to the acyl-CoA oxidase family. (661 aa) | ||||
AACS | acetoacetyl-CoA synthetase isoform X1. (672 aa) | ||||
LOC103253895 | NADP-dependent malic enzyme, mitochondrial. (271 aa) | ||||
CRYL1 | Lambda-crystallin homolog isoform X1. (308 aa) | ||||
ABAT | 4-aminobutyrate aminotransferase, mitochondrial isoform X1; Belongs to the class-III pyridoxal-phosphate-dependent aminotransferase family. (512 aa) | ||||
HSDL2 | Hydroxysteroid dehydrogenase-like protein 2 isoform X2. (418 aa) | ||||
LOC103274681 | Peroxisomal multifunctional enzyme type 2-like; Belongs to the short-chain dehydrogenases/reductases (SDR) family. (603 aa) | ||||
PHYHD1 | phytanoyl-CoA dioxygenase domain-containing protein 1 isoform X1. (291 aa) | ||||
LOC103272233 | Dehydrogenase/reductase SDR family member 1. (313 aa) | ||||
HMGCS1 | 3-hydroxy-3-methylglutaryl coenzyme A synthase; This enzyme condenses acetyl-CoA with acetoacetyl-CoA to form HMG-CoA, which is the substrate for HMG-CoA reductase. (273 aa) | ||||
CENPV | Centromere protein V. (205 aa) | ||||
LOC103252009 | Synaptic vesicle membrane protein VAT-1 homolog. (151 aa) | ||||
PCCB | propionyl-CoA carboxylase subunit beta. (477 aa) | ||||
LOC103272258 | Peroxisomal bifunctional enzyme-like isoform X1; Belongs to the enoyl-CoA hydratase/isomerase family. (64 aa) | ||||
CROT | Peroxisomal carnitine O-octanoyltransferase; Belongs to the carnitine/choline acetyltransferase family. (612 aa) | ||||
ALDH16A1 | Aldehyde dehydrogenase family 16 member A1. (802 aa) | ||||
DERA | Deoxyribose-phosphate aldolase. (318 aa) | ||||
CBR4 | Carbonyl reductase family member 4. (214 aa) | ||||
ACAA1 | 3-ketoacyl-CoA thiolase, peroxisomal isoform X1; Belongs to the thiolase-like superfamily. Thiolase family. (432 aa) | ||||
ACADS | Short-chain specific acyl-CoA dehydrogenase, mitochondrial. (412 aa) | ||||
ALDH1L1 | 10-formyltetrahydrofolate dehydrogenase; In the C-terminal section; belongs to the aldehyde dehydrogenase family. ALDH1L subfamily. (902 aa) | ||||
PEX10 | Peroxisome biogenesis factor 10. (487 aa) | ||||
HIBADH | 3-hydroxyisobutyrate dehydrogenase, mitochondrial. (189 aa) | ||||
LOC103251243 | Dehydrogenase/reductase SDR family member 7-like isoform X1; Belongs to the short-chain dehydrogenases/reductases (SDR) family. (352 aa) | ||||
ABHD14B | Protein ABHD14B isoform X2. (210 aa) | ||||
BCAT2 | Branched-chain-amino-acid aminotransferase; Belongs to the class-IV pyridoxal-phosphate-dependent aminotransferase family. (292 aa) | ||||
LOC103272354 | Trifunctional enzyme subunit beta, mitochondrial; Belongs to the thiolase-like superfamily. Thiolase family. (462 aa) | ||||
ACACA | acetyl-CoA carboxylase 1. (2383 aa) | ||||
PEX5 | Peroxisomal biogenesis factor 5 isoform X1. (579 aa) | ||||
ENSTSYP00000032845 | annotation not available (302 aa) | ||||
OLAH | S-acyl fatty acid synthase thioesterase, medium chain. (312 aa) | ||||
ADH7 | Alcohol dehydrogenase class 4 mu/sigma chain. (405 aa) | ||||
LOC103271617 | Aldehyde dehydrogenase family 3 member B2-like. (133 aa) | ||||
TYSND1 | Peroxisomal leader peptide-processing protease. (401 aa) | ||||
VAT1L | Synaptic vesicle membrane protein VAT-1 homolog-like. (419 aa) | ||||
ALDH5A1 | Succinate-semialdehyde dehydrogenase; Belongs to the aldehyde dehydrogenase family. (488 aa) | ||||
LOC103272234 | Dehydrogenase/reductase SDR family member 1-like. (313 aa) | ||||
HSD17B11 | Estradiol 17-beta-dehydrogenase 11; Belongs to the short-chain dehydrogenases/reductases (SDR) family. (300 aa) |