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bckdha | 2-oxoisovalerate dehydrogenase subunit alpha; The branched-chain alpha-keto dehydrogenase complex catalyzes the overall conversion of alpha-keto acids to acyl-CoA and CO(2). It contains multiple copies of three enzymatic components: branched-chain alpha-keto acid decarboxylase (E1), lipoamide acyltransferase (E2) and lipoamide dehydrogenase (E3). (407 aa) | ||||
LOC107091208 | Aldehyde dehydrogenase; Belongs to the aldehyde dehydrogenase family. (492 aa) | ||||
LOC107103271 | Amine oxidase. (530 aa) | ||||
echs1 | Enoyl CoA hydratase, short chain, 1, mitochondrial; Belongs to the enoyl-CoA hydratase/isomerase family. (291 aa) | ||||
ehhadh | Enoyl-CoA, hydratase/3-hydroxyacyl CoA dehydrogenase; Belongs to the enoyl-CoA hydratase/isomerase family. (733 aa) | ||||
bckdhb | Branched chain keto acid dehydrogenase E1 subunit beta. (337 aa) | ||||
aldh7a1 | Aldehyde dehydrogenase 7 family, member A1; Belongs to the aldehyde dehydrogenase family. (542 aa) | ||||
acaa1 | Acetyl-CoA acyltransferase 1; Belongs to the thiolase-like superfamily. Thiolase family. (425 aa) | ||||
acads | Acyl-CoA dehydrogenase short chain. (411 aa) | ||||
hmgcl | 3-hydroxy-3-methylglutaryl-CoA lyase. (339 aa) | ||||
LOC107099634 | Amino_oxidase domain-containing protein. (445 aa) | ||||
ENSCVAP00000007227 | Amino_oxidase domain-containing protein. (267 aa) | ||||
LOC107099636 | Amine oxidase. (520 aa) | ||||
oxct1 | Succinyl-CoA:3-ketoacid-coenzyme A transferase; Key enzyme for ketone body catabolism. Transfers the CoA moiety from succinate to acetoacetate. Formation of the enzyme-CoA intermediate proceeds via an unstable anhydride species formed between the carboxylate groups of the enzyme and substrate. (527 aa) | ||||
aacs | Acetoacetyl-CoA synthetase. (677 aa) | ||||
mccc2 | Methylcrotonoyl-CoA carboxylase 2 (beta). (564 aa) | ||||
aldh9a1 | Aldehyde dehydrogenase 9 family, member A1a, tandem duplicate 1; Belongs to the aldehyde dehydrogenase family. (505 aa) | ||||
mmut | Methylmalonyl CoA mutase. (754 aa) | ||||
LOC107083604 | Aldehyde dehydrogenase 9 family, member A1b; Belongs to the aldehyde dehydrogenase family. (513 aa) | ||||
aldh16a1 | Aldehyde dehydrogenase 16 family, member A1. (788 aa) | ||||
auh | AU RNA binding protein/enoyl-CoA hydratase; Belongs to the enoyl-CoA hydratase/isomerase family. (211 aa) | ||||
LOC107097097 | Branched-chain-amino-acid aminotransferase; Belongs to the class-IV pyridoxal-phosphate-dependent aminotransferase family. (390 aa) | ||||
aldh2 | Aldehyde dehydrogenase 2 family member, tandem duplicate 2; Belongs to the aldehyde dehydrogenase family. (517 aa) | ||||
LOC107090866 | Aldedh domain-containing protein. (481 aa) | ||||
mcee | Methylmalonyl CoA epimerase. (173 aa) | ||||
acadsb | Acyl-CoA dehydrogenase short/branched chain. (432 aa) | ||||
agxt2 | Alanine--glyoxylate aminotransferase 2; Belongs to the class-III pyridoxal-phosphate-dependent aminotransferase family. (517 aa) | ||||
dbt | Dihydrolipoamide acetyltransferase component of pyruvate dehydrogenase complex. (496 aa) | ||||
acat1 | Acetyl-CoA acetyltransferase 1; Belongs to the thiolase-like superfamily. Thiolase family. (420 aa) | ||||
pccb | Propionyl-CoA carboxylase subunit beta. (560 aa) | ||||
aox1 | Aldehyde oxidase 6. (1332 aa) | ||||
LOC107099278 | Branched-chain-amino-acid aminotransferase; Belongs to the class-IV pyridoxal-phosphate-dependent aminotransferase family. (374 aa) | ||||
acat2 | Acetyl-CoA acetyltransferase 2; Belongs to the thiolase-like superfamily. Thiolase family. (438 aa) | ||||
hadh | Hydroxyacyl-CoA dehydrogenase. (309 aa) | ||||
LOC107091209 | Aldehyde dehydrogenase; Belongs to the aldehyde dehydrogenase family. (507 aa) | ||||
LOC107099633 | Amine oxidase. (497 aa) | ||||
ENSCVAP00000024643 | Amino_oxidase domain-containing protein. (280 aa) | ||||
LOC107084328 | 3-hydroxyisobutyrate dehydrogenase; Belongs to the HIBADH-related family. (329 aa) | ||||
hsd17b10 | Hydroxysteroid (17-beta) dehydrogenase 10; Belongs to the short-chain dehydrogenases/reductases (SDR) family. (260 aa) | ||||
pcca | Propionyl-CoA carboxylase subunit alpha. (624 aa) | ||||
dld | Dihydrolipoyl dehydrogenase. (508 aa) | ||||
ivd | Isovaleryl-CoA dehydrogenase. (425 aa) | ||||
hibadh | 3-hydroxyisobutyrate dehydrogenase; Belongs to the HIBADH-related family. (329 aa) | ||||
LOC107084159 | Aldehyde dehydrogenase; Belongs to the aldehyde dehydrogenase family. (515 aa) | ||||
mccc1 | Methylcrotonoyl-CoA carboxylase 1 (alpha). (711 aa) | ||||
ACSF3 | Acyl-CoA synthetase family member 3. (588 aa) | ||||
ENSCVAP00000029853 | Acyl-CoA_dh_N domain-containing protein. (137 aa) | ||||
acaa2 | Acetyl-CoA acyltransferase 2; Belongs to the thiolase-like superfamily. Thiolase family. (397 aa) | ||||
abat | 4-aminobutyrate aminotransferase; Belongs to the class-III pyridoxal-phosphate-dependent aminotransferase family. (317 aa) | ||||
LOC107102750 | 3-hydroxy-3-methylglutaryl coenzyme A synthase; This enzyme condenses acetyl-CoA with acetoacetyl-CoA to form HMG-CoA, which is the substrate for HMG-CoA reductase. (554 aa) | ||||
ENSCVAP00000032261 | Amine oxidase. (533 aa) | ||||
hadha | Hydroxyacyl-CoA dehydrogenase trifunctional multienzyme complex subunit alpha b; Belongs to the enoyl-CoA hydratase/isomerase family. (643 aa) | ||||
hibch | 3-hydroxyisobutyryl-CoA hydrolase, mitochondrial; Hydrolyzes 3-hydroxyisobutyryl-CoA (HIBYL-CoA), a saline catabolite; Belongs to the enoyl-CoA hydratase/isomerase family. (382 aa) | ||||
aldh6a1 | Aldehyde dehydrogenase 6 family member A1. (526 aa) |