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ACAT1 | Acetyl-CoA acetyltransferase 1; Belongs to the thiolase-like superfamily. Thiolase family. (337 aa) | ||||
HMGCL | 3-hydroxy-3-methylglutaryl-CoA lyase. (327 aa) | ||||
IVD | Isovaleryl-CoA dehydrogenase. (371 aa) | ||||
U3JFH3_FICAL | Uncharacterized protein. (422 aa) | ||||
HMGCLL1 | 3-hydroxymethyl-3-methylglutaryl-CoA lyase like 1. (245 aa) | ||||
OXCT1 | Succinyl-CoA:3-ketoacid-coenzyme A transferase; Key enzyme for ketone body catabolism. Transfers the CoA moiety from succinate to acetoacetate. Formation of the enzyme-CoA intermediate proceeds via an unstable anhydride species formed between the carboxylate groups of the enzyme and substrate. (517 aa) | ||||
AGXT2 | Alanine--glyoxylate aminotransferase 2; Belongs to the class-III pyridoxal-phosphate-dependent aminotransferase family. (467 aa) | ||||
ALDH7A1 | Aldehyde dehydrogenase 7 family member A1; Belongs to the aldehyde dehydrogenase family. (475 aa) | ||||
BCAT1 | Branched-chain-amino-acid aminotransferase; Belongs to the class-IV pyridoxal-phosphate-dependent aminotransferase family. (443 aa) | ||||
BCKDHB | Branched chain keto acid dehydrogenase E1 subunit beta. (322 aa) | ||||
ACSF3 | Acyl-CoA synthetase family member 3. (580 aa) | ||||
HMGCS2 | 3-hydroxy-3-methylglutaryl coenzyme A synthase; This enzyme condenses acetyl-CoA with acetoacetyl-CoA to form HMG-CoA, which is the substrate for HMG-CoA reductase. (504 aa) | ||||
ABAT | 4-aminobutyrate aminotransferase; Belongs to the class-III pyridoxal-phosphate-dependent aminotransferase family. (500 aa) | ||||
AOX1 | Aldehyde oxidase 1. (1348 aa) | ||||
PCCA | Propionyl-CoA carboxylase subunit alpha. (707 aa) | ||||
HIBCH | 3-hydroxyisobutyryl-CoA hydrolase, mitochondrial; Hydrolyzes 3-hydroxyisobutyryl-CoA (HIBYL-CoA), a saline catabolite; Belongs to the enoyl-CoA hydratase/isomerase family. (409 aa) | ||||
AUH | AU RNA binding methylglutaconyl-CoA hydratase; Belongs to the enoyl-CoA hydratase/isomerase family. (290 aa) | ||||
ACAD8 | Acyl-CoA dehydrogenase family member 8. (455 aa) | ||||
ALDH6A1 | Aldehyde dehydrogenase 6 family member A1. (535 aa) | ||||
ACAA1 | Acetyl-CoA acyltransferase 1; Belongs to the thiolase-like superfamily. Thiolase family. (429 aa) | ||||
ACADS | Acyl-CoA dehydrogenase short chain. (373 aa) | ||||
ALDH9A1 | Aldehyde dehydrogenase 9 family member A1; Belongs to the aldehyde dehydrogenase family. (427 aa) | ||||
MCCC1 | Methylcrotonoyl-CoA carboxylase 1. (715 aa) | ||||
IL4I1 | Amine oxidase. (530 aa) | ||||
ACAA2 | Acetyl-CoA acyltransferase 2; Belongs to the thiolase-like superfamily. Thiolase family. (338 aa) | ||||
ALDH2 | Aldedh domain-containing protein; Belongs to the aldehyde dehydrogenase family. (490 aa) | ||||
ACADM | Acyl-CoA dehydrogenase medium chain. (414 aa) | ||||
HIBADH | 3-hydroxyisobutyrate dehydrogenase; Belongs to the HIBADH-related family. (301 aa) | ||||
AACS | Acetoacetyl-CoA synthetase. (641 aa) | ||||
DLD | Dihydrolipoyl dehydrogenase. (508 aa) | ||||
HMGCS1 | 3-hydroxy-3-methylglutaryl coenzyme A synthase; This enzyme condenses acetyl-CoA with acetoacetyl-CoA to form HMG-CoA, which is the substrate for HMG-CoA reductase. (522 aa) | ||||
ACAT2 | Acetyl-CoA acetyltransferase 2; Belongs to the thiolase-like superfamily. Thiolase family. (394 aa) | ||||
MCCC2 | Methylcrotonoyl-CoA carboxylase 2. (577 aa) | ||||
HADH | Hydroxyacyl-CoA dehydrogenase. (271 aa) | ||||
HADHA | Hydroxyacyl-CoA dehydrogenase trifunctional multienzyme complex subunit alpha; Belongs to the enoyl-CoA hydratase/isomerase family. (754 aa) | ||||
MCEE | Methylmalonyl-CoA epimerase. (172 aa) | ||||
HADHB | Hydroxyacyl-CoA dehydrogenase trifunctional multienzyme complex subunit beta; Belongs to the thiolase-like superfamily. Thiolase family. (473 aa) | ||||
MMUT | Methylmalonyl-CoA mutase. (740 aa) | ||||
LOC101808861 | Uncharacterized protein. (631 aa) | ||||
ECHS1 | Enoyl-CoA hydratase, short chain 1; Belongs to the enoyl-CoA hydratase/isomerase family. (292 aa) | ||||
EHHADH | Enoyl-CoA hydratase and 3-hydroxyacyl CoA dehydrogenase; Belongs to the enoyl-CoA hydratase/isomerase family. (725 aa) |