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TM2D2 | TM2 domain containing 2. (209 aa) | ||||
SARDH | Sarcosine dehydrogenase. (876 aa) | ||||
PC | Pyruvate carboxylase. (722 aa) | ||||
MRPL38 | Mitochondrial ribosomal protein L38. (406 aa) | ||||
MRPS30 | Mitochondrial ribosomal protein S30. (440 aa) | ||||
BCKDHB | Branched chain keto acid dehydrogenase E1 subunit beta. (217 aa) | ||||
MDH2 | Malate dehydrogenase. (337 aa) | ||||
TRMT5 | tRNA (guanine(37)-N1)-methyltransferase; Specifically methylates the N1 position of guanosine-37 in various cytoplasmic and mitochondrial tRNAs. Methylation is not dependent on the nature of the nucleoside 5' of the target nucleoside. This is the first step in the biosynthesis of wybutosine (yW), a modified base adjacent to the anticodon of tRNAs and required for accurate decoding; Belongs to the TRM5 / TYW2 family. (445 aa) | ||||
PPP1R26 | PPP1R26_N domain-containing protein. (861 aa) | ||||
MRPS12 | Mitochondrial ribosomal protein S12; Belongs to the universal ribosomal protein uS12 family. (160 aa) | ||||
MRPS15 | Mitochondrial ribosomal protein S15; Belongs to the universal ribosomal protein uS15 family. (269 aa) | ||||
REXO2 | RNA exonuclease 2. (243 aa) | ||||
MRPL21 | Mitochondrial ribosomal protein L21. (206 aa) | ||||
NFS1 | NFS1 cysteine desulfurase. (449 aa) | ||||
SIRT4 | NAD-dependent protein deacylase; NAD-dependent protein deacylase. Catalyzes the NAD-dependent hydrolysis of acyl groups from lysine residues; Belongs to the sirtuin family. Class II subfamily. (315 aa) | ||||
BCKDHA | 2-oxoisovalerate dehydrogenase subunit alpha; The branched-chain alpha-keto dehydrogenase complex catalyzes the overall conversion of alpha-keto acids to acyl-CoA and CO(2). It contains multiple copies of three enzymatic components: branched-chain alpha-keto acid decarboxylase (E1), lipoamide acyltransferase (E2) and lipoamide dehydrogenase (E3). (446 aa) | ||||
MRPS18A | Mitochondrial ribosomal protein S18A. (171 aa) | ||||
MRPL33 | Mitochondrial ribosomal protein L33. (65 aa) | ||||
MRPS36 | Mitochondrial ribosomal protein S36. (100 aa) | ||||
MRPS2 | Mitochondrial ribosomal protein S2. (279 aa) | ||||
MRPS17 | Mitochondrial ribosomal protein S17. (143 aa) | ||||
CS | Citrate synthase; Belongs to the citrate synthase family. (468 aa) | ||||
MRPL20 | Mitochondrial ribosomal protein L20; Belongs to the bacterial ribosomal protein bL20 family. (149 aa) | ||||
MRPS16 | Mitochondrial ribosomal protein S16. (137 aa) | ||||
ACADS | Acyl-CoA dehydrogenase short chain. (410 aa) | ||||
MRPL45 | Mitochondrial ribosomal protein L45. (321 aa) | ||||
POLG | DNA polymerase gamma, catalytic subunit. (1194 aa) | ||||
MRM1 | Mitochondrial rRNA methyltransferase 1. (292 aa) | ||||
H3BDU0_LATCH | NAD-dependent protein deacetylase; NAD-dependent protein deacetylase. (318 aa) | ||||
C3orf18 | Chromosome 3 open reading frame 18. (120 aa) | ||||
LACTB2 | Lactamase beta 2. (288 aa) | ||||
CLPX | Caseinolytic mitochondrial matrix peptidase chaperone subunit. (633 aa) | ||||
NAGK | N-acetylglucosamine kinase. (284 aa) | ||||
TEFM | Transcription elongation factor, mitochondrial. (362 aa) | ||||
MRPL10 | Mitochondrial ribosomal protein L10. (265 aa) | ||||
UQCRC1 | Ubiquinol-cytochrome c reductase core protein 1. (466 aa) | ||||
TIMM44 | Mitochondrial import inner membrane translocase subunit TIM44; Essential component of the PAM complex, a complex required for the translocation of transit peptide-containing proteins from the inner membrane into the mitochondrial matrix in an ATP-dependent manner; Belongs to the Tim44 family. (434 aa) | ||||
MRPL24 | Mitochondrial ribosomal protein L24. (216 aa) | ||||
NUDT1 | Nudix hydrolase 1. (107 aa) | ||||
TFB2M | rRNA adenine N(6)-methyltransferase; Belongs to the class I-like SAM-binding methyltransferase superfamily. rRNA adenine N(6)-methyltransferase family. (375 aa) | ||||
UQCC2 | Ubiquinol-cytochrome c reductase complex assembly factor 2. (138 aa) | ||||
TYMS | Thymidylate synthetase. (309 aa) | ||||
MRPL55 | Zgc:171480. (132 aa) | ||||
MRPL15 | Mitochondrial ribosomal protein L15. (296 aa) | ||||
DLAT | Acetyltransferase component of pyruvate dehydrogenase complex; The pyruvate dehydrogenase complex catalyzes the overall conversion of pyruvate to acetyl-CoA and CO(2). (629 aa) | ||||
SOD2 | Superoxide dismutase; Destroys radicals which are normally produced within the cells and which are toxic to biological systems. Belongs to the iron/manganese superoxide dismutase family. (223 aa) | ||||
PDE12 | Phosphodiesterase 12. (587 aa) | ||||
MRPL13 | Mitochondrial ribosomal protein L13; Belongs to the universal ribosomal protein uL13 family. (175 aa) | ||||
OAT | Ornithine aminotransferase; Belongs to the class-III pyridoxal-phosphate-dependent aminotransferase family. (443 aa) | ||||
MRPL2 | Mitochondrial ribosomal protein L2. (288 aa) | ||||
HSPE1 | Heat shock protein family E (Hsp10) member 1; Belongs to the GroES chaperonin family. (114 aa) | ||||
H3B695_LATCH | 2Fe-2S ferredoxin-type domain-containing protein. (105 aa) | ||||
MRPL17 | Mitochondrial ribosomal protein L17; Belongs to the bacterial ribosomal protein bL17 family. (180 aa) | ||||
METTL4 | Methyltransferase like 4; Belongs to the MT-A70-like family. (321 aa) | ||||
MRPL27 | Mitochondrial ribosomal protein L27. (150 aa) | ||||
MRPL57 | Mitochondrial ribosomal protein L57. (108 aa) | ||||
POLG2 | DNA polymerase gamma 2, accessory subunit. (465 aa) | ||||
LONP1 | Lon protease homolog; Belongs to the peptidase S16 family. (975 aa) | ||||
LRRC59 | Leucine rich repeat containing 59. (311 aa) | ||||
MRPL40 | Mitochondrial ribosomal protein L40. (203 aa) | ||||
MRPS23 | Mitochondrial ribosomal protein S23. (188 aa) | ||||
MRPL41 | Mitochondrial ribosomal protein L41. (135 aa) | ||||
MRPL47 | Mitochondrial ribosomal protein L47. (257 aa) | ||||
H3B3M7_LATCH | Uncharacterized protein. (320 aa) | ||||
MRPS27 | Mitochondrial ribosomal protein S27. (418 aa) | ||||
MRPL54 | Mitochondrial ribosomal protein L54. (134 aa) | ||||
MRPS9 | Mitochondrial ribosomal protein S9; Belongs to the universal ribosomal protein uS9 family. (233 aa) | ||||
DNA2 | DNA replication helicase/nuclease 2. (925 aa) | ||||
MRPL32 | Mitochondrial ribosomal protein L32. (179 aa) | ||||
DBT | Dihydrolipoamide acetyltransferase component of pyruvate dehydrogenase complex. (492 aa) | ||||
MPV17L2 | MPV17 mitochondrial inner membrane protein like 2; Belongs to the peroxisomal membrane protein PXMP2/4 family. (218 aa) | ||||
MRPS34 | Mitochondrial ribosomal protein S34. (219 aa) | ||||
ETFBKMT | Electron transfer flavoprotein subunit beta lysine methyltransferase. (222 aa) | ||||
MRPL30 | Mitochondrial ribosomal protein L30. (160 aa) | ||||
TRAP1 | TNF receptor associated protein 1. (718 aa) | ||||
ACSS3 | Acyl-CoA synthetase short chain family member 3. (714 aa) | ||||
TFB1M | rRNA adenine N(6)-methyltransferase; Belongs to the class I-like SAM-binding methyltransferase superfamily. rRNA adenine N(6)-methyltransferase family. (352 aa) | ||||
PITRM1 | Pitrilysin metallopeptidase 1. (1066 aa) | ||||
ERAL1 | Era like 12S mitochondrial rRNA chaperone 1. (476 aa) | ||||
PDHB | Pyruvate dehydrogenase E1 component subunit beta; The pyruvate dehydrogenase complex catalyzes the overall conversion of pyruvate to acetyl-CoA and CO2. (393 aa) | ||||
MRPS33 | Mitochondrial ribosomal protein S33. (106 aa) | ||||
MRPS26 | Mitochondrial ribosomal protein S26. (205 aa) | ||||
LYRM7 | LYR motif containing 7; Belongs to the complex I LYR family. (105 aa) | ||||
MRPL18 | Mitochondrial ribosomal protein L18. (191 aa) | ||||
MRPS24 | Mitochondrial ribosomal protein S24. (132 aa) | ||||
MRPS6 | Mitochondrial ribosomal protein S6. (123 aa) | ||||
MRPL23 | Mitochondrial ribosomal protein L23. (163 aa) | ||||
PCCB | Propionyl-CoA carboxylase subunit beta. (555 aa) | ||||
MRPS18C | Mitochondrial ribosomal protein S18C; Belongs to the bacterial ribosomal protein bS18 family. (128 aa) | ||||
DNAJC19 | DnaJ heat shock protein family (Hsp40) member C19. (115 aa) | ||||
PTCD1 | Pentatricopeptide repeat domain 1. (706 aa) | ||||
MRPS21 | Mitochondrial ribosomal protein S21. (87 aa) | ||||
H3ASI5_LATCH | Reverse transcriptase domain-containing protein. (258 aa) | ||||
MIPEP | Mitochondrial intermediate peptidase. (698 aa) | ||||
HADHA | Hydroxyacyl-CoA dehydrogenase trifunctional multienzyme complex subunit alpha; Belongs to the enoyl-CoA hydratase/isomerase family. (766 aa) | ||||
H3ARW9_LATCH | Uncharacterized protein. (323 aa) | ||||
GCDH | Glutaryl-CoA dehydrogenase. (437 aa) | ||||
GRPEL1 | GrpE protein homolog; Essential component of the PAM complex, a complex required for the translocation of transit peptide-containing proteins from the inner membrane into the mitochondrial matrix in an ATP-dependent manner; Belongs to the GrpE family. (220 aa) | ||||
H3AR93_LATCH | Uncharacterized protein. (257 aa) | ||||
H3AR80_LATCH | Reverse transcriptase domain-containing protein. (305 aa) | ||||
MRPL19 | Mitochondrial ribosomal protein L19. (295 aa) | ||||
MRPL28 | Mitochondrial ribosomal protein L28. (265 aa) | ||||
MTERF1 | Mitochondrial transcription termination factor 1. (397 aa) | ||||
MRPL14 | Mitochondrial ribosomal protein L14. (145 aa) | ||||
MRPS14 | Mitochondrial ribosomal protein S14. (143 aa) | ||||
GRSF1 | G-rich RNA sequence binding factor 1. (420 aa) | ||||
MRPS31 | Mitochondrial ribosomal protein S31. (350 aa) | ||||
DHX30 | DExH-box helicase 30. (805 aa) | ||||
MRPS22 | Mitochondrial ribosomal protein S22. (347 aa) | ||||
MRPL44 | Mitochondrial ribosomal protein L44. (325 aa) | ||||
MRPL4 | Mitochondrial ribosomal protein L4. (327 aa) | ||||
MRPL39 | Mitochondrial ribosomal protein L39. (295 aa) | ||||
LOC102362718 | Small integral membrane protein 29. (103 aa) | ||||
MMUT | Methylmalonyl-CoA mutase. (754 aa) | ||||
BCKDK | Protein-serine/threonine kinase. (408 aa) | ||||
MRPS25 | Mitochondrial ribosomal protein S25. (173 aa) | ||||
MRPL34 | Mitochondrial ribosomal protein L34. (134 aa) | ||||
MRPL53 | Mitochondrial ribosomal protein L53. (109 aa) | ||||
ACADM | Acyl-CoA dehydrogenase medium chain. (424 aa) | ||||
ALKBH7 | AlkB homolog 7. (231 aa) | ||||
MRPS10 | Mitochondrial ribosomal protein S10. (218 aa) | ||||
H3AIP4_LATCH | Reverse transcriptase domain-containing protein. (256 aa) | ||||
MRPL58 | Mitochondrial ribosomal protein L58. (202 aa) | ||||
TUFM | Elongation factor Tu; This protein promotes the GTP-dependent binding of aminoacyl- tRNA to the A-site of ribosomes during protein biosynthesis. (453 aa) | ||||
MRPL1 | Mitochondrial ribosomal protein L1. (328 aa) | ||||
TWNK | Twinkle mtDNA helicase. (620 aa) | ||||
H3AHP8_LATCH | TOPEUc domain-containing protein. (764 aa) | ||||
MRPL43 | Mitochondrial ribosomal protein L43. (146 aa) | ||||
SUPV3L1 | Suv3 like RNA helicase. (680 aa) | ||||
MARS2 | Methionyl-tRNA synthetase 2, mitochondrial; Belongs to the class-I aminoacyl-tRNA synthetase family. (592 aa) | ||||
MRPL49 | Mitochondrial ribosomal protein L49. (164 aa) | ||||
MRPS11 | Mitochondrial ribosomal protein S11; Belongs to the universal ribosomal protein uS11 family. (198 aa) | ||||
PRIMPOL | Primase and DNA directed polymerase. (566 aa) | ||||
MRPL46 | Mitochondrial ribosomal protein L46. (188 aa) | ||||
COASY | Coenzyme A synthase. (544 aa) | ||||
MRPL42 | Mitochondrial ribosomal protein L42. (140 aa) | ||||
GRPEL2 | GrpE like 2, mitochondrial; Belongs to the GrpE family. (225 aa) | ||||
TFAM | Transcription factor A, mitochondrial. (277 aa) | ||||
H3AB33_LATCH | Reverse transcriptase domain-containing protein. (301 aa) | ||||
MTG2 | Mitochondrial ribosome associated GTPase 2. (301 aa) | ||||
PARL | Presenilin associated, rhomboid-like a. (373 aa) | ||||
METTL17 | Methyltransferase like 17. (365 aa) | ||||
SIRT3 | NAD-dependent protein deacetylase; NAD-dependent protein deacetylase. (389 aa) | ||||
NSUN3 | NOP2/Sun RNA methyltransferase 3; Belongs to the class I-like SAM-binding methyltransferase superfamily. RsmB/NOP family. (396 aa) | ||||
MRPL11 | Mitochondrial ribosomal protein L11; Belongs to the universal ribosomal protein uL11 family. (153 aa) | ||||
MRPS35 | Mitochondrial ribosomal protein S35. (208 aa) | ||||
WARS2 | Tryptophanyl tRNA synthetase 2, mitochondrial; Belongs to the class-I aminoacyl-tRNA synthetase family. (364 aa) | ||||
DDX28 | DEAD-box helicase 28. (573 aa) | ||||
PDK2 | Protein-serine/threonine kinase. (540 aa) | ||||
FDX2 | Ferredoxin 2. (182 aa) | ||||
FASTKD2 | FAST kinase domains 2. (553 aa) | ||||
DNAJC15 | DnaJ heat shock protein family (Hsp40) member C15. (146 aa) | ||||
H3A7M9_LATCH | Uncharacterized protein. (327 aa) | ||||
IDH3A | Isocitrate dehydrogenase [NAD] subunit, mitochondrial. (366 aa) | ||||
PAM16 | Presequence translocase associated motor 16. (129 aa) | ||||
DNAJA3 | DnaJ heat shock protein family (Hsp40) member A3. (480 aa) | ||||
LOC102356981 | Uncharacterized protein. (140 aa) | ||||
MRPS18B | Mitochondrial ribosomal protein S18B. (242 aa) | ||||
DAP3 | Death associated protein 3. (394 aa) | ||||
MRPL36 | Ribosomal protein; Belongs to the bacterial ribosomal protein bL36 family. (115 aa) | ||||
MRPL48 | Mitochondrial ribosomal protein L48. (212 aa) | ||||
MRPL37 | Mitochondrial ribosomal protein L37. (427 aa) | ||||
LOC102365031 | ApaG domain-containing protein. (345 aa) | ||||
MRPL52 | Mitochondrial ribosomal protein L52. (139 aa) | ||||
POLDIP2 | DNA polymerase delta interacting protein 2. (369 aa) | ||||
MRPL50 | Mitochondrial ribosomal protein L50. (165 aa) | ||||
MTERF2 | Mitochondrial transcription termination factor 2. (386 aa) | ||||
MRPL22 | Mitochondrial ribosomal protein L22; Belongs to the universal ribosomal protein uL22 family. (199 aa) | ||||
HAGH | Hydroxyacylglutathione hydrolase. (304 aa) | ||||
MRPS7 | Mitochondrial ribosomal protein S7. (242 aa) | ||||
ACADL | Acyl-CoA dehydrogenase long chain. (448 aa) | ||||
MTG1 | Mitochondrial ribosome associated GTPase 1. (182 aa) | ||||
PDK4 | Protein-serine/threonine kinase. (370 aa) | ||||
ACAT1 | Acetyl-CoA acetyltransferase 1; Belongs to the thiolase-like superfamily. Thiolase family. (422 aa) | ||||
MRPL35 | Mitochondrial ribosomal protein L35. (184 aa) | ||||
MRPL51 | Mitochondrial ribosomal protein L51. (102 aa) | ||||
MRPL16 | Mitochondrial ribosomal protein L16; Belongs to the universal ribosomal protein uL16 family. (251 aa) | ||||
TRMT10C | tRNA methyltransferase 10C, mitochondrial RNase P subunit. (380 aa) |