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LOC100194712 | 2-oxoisovalerate dehydrogenase subunit beta, mitochondrial. (437 aa) | ||||
LOC106605051 | 2-oxoisovalerate dehydrogenase subunit beta, mitochondrial-like. (489 aa) | ||||
bckdha | 2-oxoisovalerate dehydrogenase subunit alpha; The branched-chain alpha-keto dehydrogenase complex catalyzes the overall conversion of alpha-keto acids to acyl-CoA and CO(2). It contains multiple copies of three enzymatic components: branched-chain alpha-keto acid decarboxylase (E1), lipoamide acyltransferase (E2) and lipoamide dehydrogenase (E3). (554 aa) |