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LOC106601552 | Branched-chain-amino-acid aminotransferase; Belongs to the class-IV pyridoxal-phosphate-dependent aminotransferase family. (462 aa) | ||||
aldh6a1 | Methylmalonate-semialdehyde dehydrogenase [acylating], mitochondrial isoform X2. (525 aa) | ||||
LOC106564456 | 4-aminobutyrate aminotransferase, mitochondrial-like; Belongs to the class-III pyridoxal-phosphate-dependent aminotransferase family. (499 aa) | ||||
acadm | Medium-chain specific Acyl-CoA dehydrogenase, mitochondrial. (422 aa) | ||||
LOC106575684 | propionyl-CoA carboxylase alpha chain, mitochondrial-like. (442 aa) | ||||
LOC106594657 | propionyl-CoA carboxylase alpha chain, mitochondrial-like. (724 aa) | ||||
dbt | Dihydrolipoamide acetyltransferase component of pyruvate dehydrogenase complex. (500 aa) | ||||
aldh16a1 | Aldehyde dehydrogenase family 16 member A1. (793 aa) | ||||
LOC106605051 | 2-oxoisovalerate dehydrogenase subunit beta, mitochondrial-like. (489 aa) | ||||
ENSSSAP00000022496 | 3-hydroxyisobutyrate dehydrogenase, mitochondrial-like. (187 aa) | ||||
GABT-2 | 4-aminobutyrate aminotransferase / (S)-3-amino-2-methylpropionate transaminase. (312 aa) | ||||
LOC106574493 | 3-hydroxyisobutyrate dehydrogenase, mitochondrial-like. (155 aa) | ||||
aldh7a1 | Aldehyde dehydrogenase family 7 member A1 homolog; Belongs to the aldehyde dehydrogenase family. (548 aa) | ||||
mmsa | Methylmalonate-semialdehyde dehydrogenase. (554 aa) | ||||
ACADSB | Short/branched chain specific acyl-CoA dehydrogenase, mitochondrial-like. (456 aa) | ||||
LOC106575224 | Aldehyde oxidase 1-like. (1339 aa) | ||||
HCD2 | 3-hydroxyacyl-CoA dehydrogenase type-2; Belongs to the short-chain dehydrogenases/reductases (SDR) family. (255 aa) | ||||
BCAT1 | Branched-chain-amino-acid aminotransferase; Belongs to the class-IV pyridoxal-phosphate-dependent aminotransferase family. (485 aa) | ||||
mccc2 | methylcrotonoyl-CoA carboxylase beta chain, mitochondrial isoform X1. (566 aa) | ||||
LOC106602847 | Aldehyde dehydrogenase; Belongs to the aldehyde dehydrogenase family. (552 aa) | ||||
LOC106613594 | Dihydrolipoamide acetyltransferase component of pyruvate dehydrogenase complex. (495 aa) | ||||
LOC106613311 | Aldehyde dehydrogenase; Belongs to the aldehyde dehydrogenase family. (510 aa) | ||||
LOC106580430 | 3-ketoacyl-CoA thiolase, mitochondrial-like; Belongs to the thiolase-like superfamily. Thiolase family. (404 aa) | ||||
LOC106585052 | 3-ketoacyl-CoA thiolase, mitochondrial-like; Belongs to the thiolase-like superfamily. Thiolase family. (397 aa) | ||||
aldh9a1 | Aldehyde dehydrogenase family 9 member A1-A; Belongs to the aldehyde dehydrogenase family. (509 aa) | ||||
LOC106563087 | Short-chain specific acyl-CoA dehydrogenase, mitochondrial-like isoform X1. (405 aa) | ||||
ECHP | Peroxisomal bifunctional enzyme. (530 aa) | ||||
bckdha | 2-oxoisovalerate dehydrogenase subunit alpha; The branched-chain alpha-keto dehydrogenase complex catalyzes the overall conversion of alpha-keto acids to acyl-CoA and CO(2). It contains multiple copies of three enzymatic components: branched-chain alpha-keto acid decarboxylase (E1), lipoamide acyltransferase (E2) and lipoamide dehydrogenase (E3). (554 aa) | ||||
agxt2 | Alanine--glyoxylate aminotransferase 2, mitochondrial; Belongs to the class-III pyridoxal-phosphate-dependent aminotransferase family. (518 aa) | ||||
LOC106610807 | hydroxymethylglutaryl-CoA lyase, mitochondrial-like. (341 aa) | ||||
LOC106613885 | methylcrotonoyl-CoA carboxylase beta chain, mitochondrial-like isoform X1. (610 aa) | ||||
al3a2 | Aldehyde dehydrogenase; Belongs to the aldehyde dehydrogenase family. (502 aa) | ||||
LOC106570522 | 3-hydroxyisobutyrate dehydrogenase; Belongs to the HIBADH-related family. (336 aa) | ||||
LOC106574294 | Aldehyde oxidase 1-like. (1346 aa) | ||||
acad8 | isobutyryl-CoA dehydrogenase, mitochondrial. (425 aa) | ||||
LOC106611334 | Trifunctional enzyme subunit alpha, mitochondrial-like; Belongs to the enoyl-CoA hydratase/isomerase family. (841 aa) | ||||
LOC106584300 | methylcrotonoyl-CoA carboxylase subunit alpha, mitochondrial-like. (727 aa) | ||||
LOC106612549 | Amine oxidase. (514 aa) | ||||
ACADSB-2 | Short/branched chain specific acyl-CoA dehydrogenase, mitochondrial-like. (442 aa) | ||||
LOC106587249 | methylmalonyl-CoA epimerase, mitochondrial-like isoform X1. (174 aa) | ||||
aldh3a2 | Aldehyde dehydrogenase; Belongs to the aldehyde dehydrogenase family. (564 aa) | ||||
acat1 | acetyl-CoA acetyltransferase, mitochondrial; Belongs to the thiolase-like superfamily. Thiolase family. (526 aa) | ||||
LOC106613934 | methylcrotonoyl-CoA carboxylase subunit alpha, mitochondrial-like. (723 aa) | ||||
acsf3 | acyl-CoA synthetase family member 3, mitochondrial isoform X2. (583 aa) | ||||
mcee | methylmalonyl-CoA epimerase, mitochondrial-like. (180 aa) | ||||
LOC106608228 | isovaleryl-CoA dehydrogenase, mitochondrial-like. (450 aa) | ||||
mmut | methylmalonyl-CoA mutase, mitochondrial isoform X1. (761 aa) | ||||
LOC106613017 | isobutyryl-CoA dehydrogenase, mitochondrial-like. (461 aa) | ||||
LOC106575421 | propionyl-CoA carboxylase beta chain, mitochondrial-like. (551 aa) | ||||
LOC106580620 | Succinyl-CoA:3-ketoacid-coenzyme A transferase; Key enzyme for ketone body catabolism. Transfers the CoA moiety from succinate to acetoacetate. Formation of the enzyme-CoA intermediate proceeds via an unstable anhydride species formed between the carboxylate groups of the enzyme and substrate. (565 aa) | ||||
hibch | 3-hydroxyisobutyryl-CoA hydrolase, mitochondrial; Hydrolyzes 3-hydroxyisobutyryl-CoA (HIBYL-CoA), a saline catabolite; Belongs to the enoyl-CoA hydratase/isomerase family. (418 aa) | ||||
aacs | acetoacetyl-CoA synthetase. (673 aa) | ||||
auh | methylglutaconyl-CoA hydratase, mitochondrial; Belongs to the enoyl-CoA hydratase/isomerase family. (326 aa) | ||||
LOC106561133 | L-amino-acid oxidase-like. (511 aa) | ||||
LOC106603767 | Trifunctional enzyme subunit alpha, mitochondrial-like isoform X1; Belongs to the enoyl-CoA hydratase/isomerase family. (783 aa) | ||||
LOC106589805 | 3-hydroxymethyl-3-methylglutaryl-CoA lyase, cytoplasmic-like isoform X2. (338 aa) | ||||
echs1 | Enoyl Coenzyme A hydratase short chain 1 mitochondrial; Belongs to the enoyl-CoA hydratase/isomerase family. (298 aa) | ||||
LOC106561021 | Dihydrolipoyl dehydrogenase. (508 aa) | ||||
LOC106563327 | Succinyl-CoA:3-ketoacid-coenzyme A transferase; Key enzyme for ketone body catabolism. Transfers the CoA moiety from succinate to acetoacetate. Formation of the enzyme-CoA intermediate proceeds via an unstable anhydride species formed between the carboxylate groups of the enzyme and substrate. (531 aa) |