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| | LOC101730957 | Uncharacterized protein; Belongs to the thiolase-like superfamily. Thiolase family. (439 aa) |
| | ndufa5 | Uncharacterized protein. (110 aa) |
| | hadha | Uncharacterized protein; Belongs to the enoyl-CoA hydratase/isomerase family. (771 aa) |
| | hadhb | Trifunctional enzyme subunit beta, mitochondrial; Belongs to the thiolase-like superfamily. Thiolase family. (470 aa) |
| | ndufs1 | Zinc finger protein 33B; Belongs to the complex I 75 kDa subunit family. (736 aa) |
| | ndufb7 | Uncharacterized protein. (116 aa) |
| | mrps15 | Uncharacterized protein; Belongs to the universal ribosomal protein uS15 family. (277 aa) |
| | heatr5a | HEAT repeat-containing protein 5A; Belongs to the HEATR5 family. (2030 aa) |
| | ndufb9 | Uncharacterized protein; Belongs to the complex I LYR family. (170 aa) |
| | atp5f1b | ATP synthase subunit beta; Produces ATP from ADP in the presence of a proton gradient across the membrane. (541 aa) |
| | mrps28 | Superoxide dismutase 2. (169 aa) |
| | mrpl53 | Uncharacterized protein. (171 aa) |
| | mrpl51 | 39S ribosomal protein L51, mitochondrial; Belongs to the mitochondrion-specific ribosomal protein mL51 family. (125 aa) |
| | chchd3 | MICOS complex subunit; Component of the MICOS complex, a large protein complex of the mitochondrial inner membrane that plays crucial roles in the maintenance of crista junctions, inner membrane architecture, and formation of contact sites to the outer membrane. (251 aa) |
| | stoml2-2 | Uncharacterized protein. (99 aa) |
| | ndufb5 | Uncharacterized protein. (186 aa) |
| | mrps16 | Mitochondrial ribosomal protein S16. (141 aa) |
| | Agk | Uncharacterized protein. (109 aa) |
| | tomm70 | TPR_REGION domain-containing protein. (578 aa) |
| | slc25a40 | Solute carrier family 25 member 40. (341 aa) |
| | ndufs3 | Complex1_30kDa domain-containing protein; Belongs to the complex I 30 kDa subunit family. (236 aa) |
| | mrpl55 | Uncharacterized protein. (134 aa) |
| | polrmt | DNA-directed RNA polymerase; DNA-dependent RNA polymerase catalyzes the transcription of DNA into RNA using the four ribonucleoside triphosphates as substrates. Belongs to the phage and mitochondrial RNA polymerase family. (1231 aa) |
| | sh3rf1 | E3 ubiquitin-protein ligase SH3RF1; Has E3 ubiquitin-protein ligase activity. In the absence of an external substrate, it can catalyze self-ubiquitination. Acts as a scaffold protein that contributes to the effective activation of the JNK signaling pathway; Belongs to the SH3RF family. (873 aa) |
| | LOC100127750 | Mastermind like transcriptional coactivator 1. (180 aa) |
| | mrpl22 | 39S ribosomal protein L22, mitochondrial; Belongs to the universal ribosomal protein uL22 family. (204 aa) |
| | mrpl21 | Novel protein. (201 aa) |
| | eif4a3.1 | Eukaryotic initiation factor 4A-III; ATP-dependent RNA helicase. Involved in pre-mRNA splicing as component of the spliceosome. Core component of the splicing-dependent multiprotein exon junction complex (EJC) deposited at splice junctions on mRNAs. The EJC is a dynamic structure consisting of core proteins and several peripheral nuclear and cytoplasmic associated factors that join the complex only transiently either during EJC assembly or during subsequent mRNA metabolism. The EJC marks the position of the exon-exon junction in the mature mRNA for the gene expression machinery and the [...] (415 aa) |
| | mrpl28 | Mitochondrial ribosomal protein L28. (254 aa) |
| | MRPL52 | Mitochondrial ribosomal protein L52. (146 aa) |
| | LOC100497159 | Uncharacterized protein; Belongs to the peroxisomal membrane protein PXMP2/4 family. (213 aa) |
| | mrps31 | LOC779479 protein. (375 aa) |
| | bckdhb | Chymotrypsin like elastase 2A. (398 aa) |
| | ndufa2 | NADH dehydrogenase [ubiquinone] 1 alpha subcomplex subunit 2; Accessory subunit of the mitochondrial membrane respiratory chain NADH dehydrogenase (Complex I), that is believed not to be involved in catalysis. Complex I functions in the transfer of electrons from NADH to the respiratory chain. The immediate electron acceptor for the enzyme is believed to be ubiquinone. (100 aa) |
| | smdt1 | Essential MCU regulator, mitochondrial; Essential regulatory subunit of the mitochondrial calcium uniporter complex (uniplex), a complex that mediates calcium uptake into mitochondria. Plays a central role in regulating the uniplex complex response to intracellular calcium signaling. (99 aa) |
| | ndufab1 | Acyl carrier protein; Carrier of the growing fatty acid chain in fatty acid biosynthesis. (149 aa) |
| | mrpl20 | Membrane associated ring-CH-type finger 7; Belongs to the bacterial ribosomal protein bL20 family. (149 aa) |
| | cox5a | Cytochrome c oxidase, subunit Va. (148 aa) |
| | mrpl24 | AP2-associated kinase 1. (216 aa) |
| | mrps5 | Apoptosis inducing factor, mitochondria associated 3; Belongs to the universal ribosomal protein uS5 family. (400 aa) |
| | mrpl3 | Mitochondrial ribosomal protein L3; Belongs to the universal ribosomal protein uL3 family. (341 aa) |
| | bckdk | Protein-serine/threonine kinase. (415 aa) |
| | dap3 | Uncharacterized protein. (391 aa) |
| | idh3b | Isocitrate dehydrogenase [NAD] subunit, mitochondrial. (381 aa) |
| | uqcr10 | Ubiquinol-cytochrome c reductase complex (7.2 kD) (Ucrc). (62 aa) |
| | MRPL57 | Mitochondrial ribosomal protein L57. (104 aa) |
| | hsd17b10 | Uncharacterized protein; Belongs to the short-chain dehydrogenases/reductases (SDR) family. (294 aa) |
| | ndufa4 | Uncharacterized protein. (98 aa) |
| | apool | MICOS complex subunit; Component of the MICOS complex, a large protein complex of the mitochondrial inner membrane that plays crucial roles in the maintenance of crista junctions, inner membrane architecture, and formation of contact sites to the outer membrane. (310 aa) |
| | samm50 | Sorting and assembly machinery component 50 homolog. (360 aa) |
| | ndufs5 | Uncharacterized protein. (134 aa) |
| | atp5pf | Uncharacterized protein. (125 aa) |
| | TOMM40L | Translocase of outer mitochondrial membrane 40 like. (251 aa) |
| | mrps22 | NCK-associated protein 5-like. (326 aa) |
| | mrpl39 | Cyclin T1. (356 aa) |
| | romo1 | Reactive oxygen species modulator 1; Has antibacterial activity against a variety of bacteria including S.aureus, P.aeruginosa and M.tuberculosis. Acts by inducing bacterial membrane breakage (By similarity). (79 aa) |
| | sdhc | URB1 ribosome biogenesis 1 homolog (S. cerevisiae). (190 aa) |
| | atp5md | Spermatogenesis associated 20. (59 aa) |
| | ndufa13 | NADH:ubiquinone oxidoreductase core subunit S1. (144 aa) |
| | ndufb3 | NADH dehydrogenase (Ubiquinone) 1 beta subcomplex, 3, 12kDa. (97 aa) |
| | timm23 | Mitochondrial import inner membrane translocase subunit Tim23; Essential component of the TIM23 complex, a complex that mediates the translocation of transit peptide-containing proteins across the mitochondrial inner membrane (By similarity). Plays an essential role in early embryonic development. (209 aa) |
| | MICU2 | Mitochondrial calcium uptake 2. (485 aa) |
| | mrpl44 | Hypothetical LOC496841. (322 aa) |
| | atp5f1a | ATP synthase subunit alpha; Produces ATP from ADP in the presence of a proton gradient across the membrane. (553 aa) |
| | TRMT10B | tRNA methyltransferase 10B. (246 aa) |
| | atp5mc1 | ATP-synt_C domain-containing protein; Belongs to the ATPase C chain family. (170 aa) |
| | cox7a1 | Uncharacterized protein. (82 aa) |
| | mrpl43 | L51_S25_CI-B8 domain-containing protein. (202 aa) |
| | mrpl23 | Uncharacterized protein. (159 aa) |
| | mrpl12 | Mitochondrial ribosomal protein L12. (189 aa) |
| | apoo | MICOS complex subunit; Component of the MICOS complex, a large protein complex of the mitochondrial inner membrane that plays crucial roles in the maintenance of crista junctions, inner membrane architecture, and formation of contact sites to the outer membrane. (225 aa) |
| | ndufs7 | DEAD-box helicase 31; Belongs to the complex I 20 kDa subunit family. (217 aa) |
| | timm29 | Uncharacterized protein. (238 aa) |
| | mrps23 | Castor zinc finger 1. (187 aa) |
| | atp5f1d | ATP synthase, H+ transporting, mitochondrial F1 complex, delta subunit. (162 aa) |
| | ndufc2 | NADH dehydrogenase [ubiquinone] 1 subunit C2; Accessory subunit of the mitochondrial membrane respiratory chain NADH dehydrogenase (Complex I), that is believed not to be involved in catalysis. Complex I functions in the transfer of electrons from NADH to the respiratory chain. The immediate electron acceptor for the enzyme is believed to be ubiquinone. (110 aa) |
| | chchd6 | MICOS complex subunit mic25; Component of the MICOS complex, a large protein complex of the mitochondrial inner membrane that plays crucial roles in the maintenance of crista junctions, inner membrane architecture, and formation of contact sites to the outer membrane. Belongs to the MICOS complex subunit Mic19 family. Metazoan Mic25 subfamily. (282 aa) |
| | ENSXETP00000021445 | annotation not available (104 aa) |
| | ND2 | NADH-ubiquinone oxidoreductase chain 2; Core subunit of the mitochondrial membrane respiratory chain NADH dehydrogenase (Complex I) that is believed to belong to the minimal assembly required for catalysis. Complex I functions in the transfer of electrons from NADH to the respiratory chain. The immediate electron acceptor for the enzyme is believed to be ubiquinone. (345 aa) |
| | COX1 | Cytochrome c oxidase subunit 1; Cytochrome c oxidase is the component of the respiratory chain that catalyzes the reduction of oxygen to water. Subunits 1-3 form the functional core of the enzyme complex. CO I is the catalytic subunit of the enzyme. Electrons originating in cytochrome c are transferred via the copper A center of subunit 2 and heme A of subunit 1 to the bimetallic center formed by heme A3 and copper B. (518 aa) |
| | COX2 | Cytochrome c oxidase subunit 2; Cytochrome c oxidase is the component of the respiratory chain that catalyzes the reduction of oxygen to water. Subunits 1-3 form the functional core of the enzyme complex. Subunit 2 transfers the electrons from cytochrome c via its binuclear copper A center to the bimetallic center of the catalytic subunit 1. (229 aa) |
| | ATP8 | ATP synthase protein 8. (55 aa) |
| | ATP6 | ATP synthase subunit a. (227 aa) |
| | COX3 | Cytochrome c oxidase subunit 3; Subunits I, II and III form the functional core of the enzyme complex. (261 aa) |
| | ND3 | NADH-ubiquinone oxidoreductase chain 3; Core subunit of the mitochondrial membrane respiratory chain NADH dehydrogenase (Complex I) that is believed to belong to the minimal assembly required for catalysis. Complex I functions in the transfer of electrons from NADH to the respiratory chain. The immediate electron acceptor for the enzyme is believed to be ubiquinone. (114 aa) |
| | ND4 | NADH-ubiquinone oxidoreductase chain 4; Core subunit of the mitochondrial membrane respiratory chain NADH dehydrogenase (Complex I) that is believed to belong to the minimal assembly required for catalysis. Complex I functions in the transfer of electrons from NADH to the respiratory chain. The immediate electron acceptor for the enzyme is believed to be ubiquinone. (459 aa) |
| | ND5 | NADH-ubiquinone oxidoreductase chain 5; Core subunit of the mitochondrial membrane respiratory chain NADH dehydrogenase (Complex I) that is believed to belong to the minimal assembly required for catalysis. Complex I functions in the transfer of electrons from NADH to the respiratory chain. The immediate electron acceptor for the enzyme is believed to be ubiquinone. (605 aa) |
| | ndufb8 | Uncharacterized protein. (199 aa) |
| | cox6a1 | Cytochrome c oxidase subunit 6A, mitochondrial. (112 aa) |
| | mrpl13 | Kinesin family member 14. (179 aa) |
| | POLG2 | DNA polymerase gamma 2, accessory subunit. (332 aa) |
| | immt | MICOS complex subunit MIC60; Component of the MICOS complex, a large protein complex of the mitochondrial inner membrane that plays crucial roles in the maintenance of crista junctions, inner membrane architecture, and formation of contact sites to the outer membrane. (766 aa) |
| | ndufa10 | NADH dehydrogenase [ubiquinone] 1 alpha subcomplex subunit 10, mitochondrial; Accessory subunit of the mitochondrial membrane respiratory chain NADH dehydrogenase (Complex I), that is believed not to be involved in catalysis. Complex I functions in the transfer of electrons from NADH to the respiratory chain. The immediate electron acceptor for the enzyme is believed to be ubiquinone. (384 aa) |
| | clpx | Uncharacterized protein. (624 aa) |
| | LOC100495196 | NADH dehydrogenase [ubiquinone] 1 alpha subcomplex subunit 2; Accessory subunit of the mitochondrial membrane respiratory chain NADH dehydrogenase (Complex I), that is believed not to be involved in catalysis. Complex I functions in the transfer of electrons from NADH to the respiratory chain. The immediate electron acceptor for the enzyme is believed to be ubiquinone. (104 aa) |
| | tomm22 | Translocase of outer mitochondrial membrane 22 homolog (Yeast). (126 aa) |
| | mrpl33 | RAD23 homolog B, nucleotide excision repair protein. (65 aa) |
| | st18-2 | ST18 C2H2C-type zinc finger transcription factor. (92 aa) |
| | mrpl17 | Mitochondrial ribosomal protein L17; Belongs to the bacterial ribosomal protein bL17 family. (169 aa) |
| | afg3l1p | Fucosyltransferase 1 (H blood group). (785 aa) |
| | timm50 | Mitochondrial import inner membrane translocase subunit TIM50; Essential component of the TIM23 complex, a complex that mediates the translocation of transit peptide-containing proteins across the mitochondrial inner membrane. (390 aa) |
| | mrps10 | Ribosomal_S10 domain-containing protein. (203 aa) |
| | micu3 | Transmembrane protein 170A. (506 aa) |
| | mrpl41 | KH domain-containing, RNA-binding, signal transduction-associated protein 2. (135 aa) |
| | gtpbp6-2 | GTP-binding protein 6 (putative). (236 aa) |
| | mrps12 | Chloride intracellular channel 3; Belongs to the universal ribosomal protein uS12 family. (149 aa) |
| | NSUN3 | NOP2/Sun RNA methyltransferase 3; Belongs to the class I-like SAM-binding methyltransferase superfamily. RsmB/NOP family. (322 aa) |
| | mcm2-2 | Uncharacterized protein. (63 aa) |
| | mrpl38 | E3 ubiquitin-protein ligase TM129. (420 aa) |
| | ndufb6 | NADH dehydrogenase (Ubiquinone) 1 beta subcomplex, 6. (128 aa) |
| | immp1l | Mitochondrial inner membrane protease subunit 1; Catalyzes the removal of transit peptides required for the targeting of proteins from the mitochondrial matrix, across the inner membrane, into the inter-membrane space. (167 aa) |
| | mrpl32 | Uncharacterized protein. (181 aa) |
| | timm17a | Parathyroid hormone 1 receptor. (167 aa) |
| | spg7 | Tetraspanin 31. (768 aa) |
| | mcub | Large 60S subunit nuclear export GTPase 1. (319 aa) |
| | atp5me | ATP synthase, H+ transporting, mitochondrial F1F0 complex, subunit e. (71 aa) |
| | SUPV3L1 | Suv3 like RNA helicase. (828 aa) |
| | atp5mg | ATP synthase subunit; Mitochondrial membrane ATP synthase (F1F0 ATP synthase or Complex V) produces ATP from ADP in the presence of a proton gradient across the membrane which is generated by electron transport complexes of the respiratory chain. F-type ATPases consist of two structural domains, F1 - containing the extramembraneous catalytic core, and F0 - containing the membrane proton channel, linked together by a central stalk and a peripheral stalk. During catalysis, ATP synthesis in the catalytic domain of F1 is coupled via a rotary mechanism of the central stalk subunits to proto [...] (107 aa) |
| | timm21 | Novel protein. (234 aa) |
| | mrps6 | LOC100038272 protein. (122 aa) |
| | mrpl11 | Mitochondrial ribosomal protein L11; Belongs to the universal ribosomal protein uL11 family. (192 aa) |
| | atp5po | 5-hydroxytryptamine (serotonin) receptor 2B, G protein-coupled. (227 aa) |
| | UQCRB | Cytochrome b-c1 complex subunit 7; Component of the ubiquinol-cytochrome c reductase complex (complex III or cytochrome b-c1 complex), which is part of the mitochondrial respiratory chain; Belongs to the UQCRB/QCR7 family. (111 aa) |
| | mrpl48 | P450 (cytochrome) oxidoreductase. (219 aa) |
| | micos13 | MICOS complex subunit MIC13; Component of the MICOS complex, a large protein complex of the mitochondrial inner membrane that plays crucial roles in the maintenance of crista junctions, inner membrane architecture, and formation of contact sites to the outer membrane. (111 aa) |
| | mettl22-2 | Methyltransferase like 22. (98 aa) |
| | mrps18b | Uncharacterized protein. (169 aa) |
| | cox6c | Cytochrome c oxidase subunit VIc. (79 aa) |
| | cyc1 | Uncharacterized protein. (309 aa) |
| | ndufa6 | NADH dehydrogenase [ubiquinone] 1 alpha subcomplex subunit 6; Accessory subunit of the mitochondrial membrane respiratory chain NADH dehydrogenase (Complex I), that is believed to be not involved in catalysis. Complex I functions in the transfer of electrons from NADH to the respiratory chain. The immediate electron acceptor for the enzyme is believed to be ubiquinone. (127 aa) |
| | aurkaip1 | Insulin like growth factor 2 mRNA binding protein 3. (197 aa) |
| | MRPL34 | Mitochondrial ribosomal protein L34. (112 aa) |
| | MRPS33 | Mitochondrial ribosomal protein S33. (106 aa) |
| | bax | BCL2-associated X protein. (221 aa) |
| | dbt | Dihydrolipoamide acetyltransferase component of pyruvate dehydrogenase complex. (540 aa) |
| | mrps25 | 5-azacytidine induced 2. (173 aa) |
| | cox7c | Nipsnap homolog 1. (118 aa) |
| | LOC101732332 | Uncharacterized loc100124842. (198 aa) |
| | ndufv2 | NADH dehydrogenase (Ubiquinone) flavoprotein 2, 24kDa. (243 aa) |
| | uqcrfs1 | Cytochrome b-c1 complex subunit Rieske, mitochondrial; Component of the ubiquinol-cytochrome c reductase complex (complex III or cytochrome b-c1 complex), which is a respiratory chain that generates an electrochemical potential coupled to ATP synthesis. (273 aa) |
| | mrpl14 | FAT atypical cadherin 4. (122 aa) |
| | ndufa3 | Zinc finger, BED-type-containing 9. (96 aa) |
| | cox6a2 | Cytochrome c oxidase subunit 6A, mitochondrial. (105 aa) |
| | LOC100127850 | Cytochrome c oxidase subunit VIIa polypeptide 2 like (Prov). (118 aa) |
| | uqcr11 | Uncharacterized protein. (56 aa) |
| | sdhd | Succinate dehydrogenase [ubiquinone] cytochrome b small subunit, mitochondrial; Membrane-anchoring subunit of succinate dehydrogenase (SDH) that is involved in complex II of the mitochondrial electron transport chain and is responsible for transferring electrons from succinate to ubiquinone (coenzyme Q). (152 aa) |
| | tomm6 | Cell migration inducing hyaluronidase 1. (68 aa) |
| | sdha | Succinate dehydrogenase [ubiquinone] flavoprotein subunit, mitochondrial; Flavoprotein (FP) subunit of succinate dehydrogenase (SDH) that is involved in complex II of the mitochondrial electron transport chain and is responsible for transferring electrons from succinate to ubiquinone (coenzyme Q); Belongs to the FAD-dependent oxidoreductase 2 family. FRD/SDH subfamily. (695 aa) |
| | mrpl40 | Uncharacterized protein. (225 aa) |
| | grpel1 | GrpE protein homolog; Essential component of the PAM complex, a complex required for the translocation of transit peptide-containing proteins from the inner membrane into the mitochondrial matrix in an ATP-dependent manner; Belongs to the GrpE family. (216 aa) |
| | mrps21 | Uncharacterized protein. (105 aa) |
| | mrps17 | Mitochondrial ribosomal protein S17. (141 aa) |
| | mrps9 | Zinc finger E-box binding homeobox 2; Belongs to the universal ribosomal protein uS9 family. (384 aa) |
| | dnajc15 | DnaJ homolog subfamily C member 15; Negative regulator of the mitochondrial respiratory chain (By similarity). Plays a role in the translocation of proteins across the mitochondrial inner membrane (By similarity). Involved in pronephric kidney development at the early tadpole stage. (187 aa) |
| | mcu | Tryptase alpha/beta 1. (320 aa) |
| | LOC108648166 | Uncharacterized protein. (176 aa) |
| | micu1 | Calcium uptake protein 1, mitochondrial; Key regulator of mitochondrial calcium uniporter (MCU) that senses calcium level via its EF-hand domains. micu1 and micu2 form a disulfide-linked heterodimer that stimulates and inhibits mcu activity, depending on the concentration of calcium. Micu1 acts both as an activator or inhibitor of mitochondrial calcium uptake. Acts as a gatekeeper of mcu at low concentration of calcium, preventing channel opening. Enhances mcu opening at high calcium concentration, allowing a rapid response of mitochondria to calcium signals generated in the cytoplasm. (475 aa) |
| | atp5mf | Uncharacterized protein. (147 aa) |
| | ndufb2 | Chromosome 14 open reading frame 28. (102 aa) |
| | NDUFS6 | NADH:ubiquinone oxidoreductase subunit S6. (165 aa) |
| | mgst1-2 | Ribosomal protein; Belongs to the bacterial ribosomal protein bL36 family. (167 aa) |
| | slc25a4 | Solute carrier family 25 (Mitochondrial carrier; adenine nucleotide translocator), member 4; Belongs to the mitochondrial carrier (TC 2.A.29) family. (298 aa) |
| | suclg2 | Succinate--CoA ligase [GDP-forming] subunit beta, mitochondrial; GTP-specific succinyl-CoA synthetase functions in the citric acid cycle (TCA), coupling the hydrolysis of succinyl-CoA to the synthesis of GTP and thus represents the only step of substrate-level phosphorylation in the TCA. The beta subunit provides nucleotide specificity of the enzyme and binds the substrate succinate, while the binding sites for coenzyme A and phosphate are found in the alpha subunit. (431 aa) |
| | tomm5 | Uncharacterized protein. (51 aa) |
| | ndufb4 | Uncharacterized protein. (141 aa) |
| | MRPL19 | Mitochondrial ribosomal protein L19. (305 aa) |
| | phb2 | Prohibitin-2; Acts as a mediator of transcriptional repression by nuclear hormone receptors via recruitment of histone deacetylases. Functions as an estrogen receptor (ER)-selective coregulator that potentiates the inhibitory activities of antiestrogens and represses the activity of estrogens. Competes with NCOA1 for modulation of ER transcriptional activity. Probably involved in regulating mitochondrial respiration activity and in aging (By similarity); Belongs to the prohibitin family. (301 aa) |
| | ndufs2 | Beta-1,3-glucuronyltransferase 3; Belongs to the complex I 49 kDa subunit family. (478 aa) |
| | ndufv1 | NADH dehydrogenase [ubiquinone] flavoprotein 1, mitochondrial; Core subunit of the mitochondrial membrane respiratory chain NADH dehydrogenase (Complex I) that is believed to belong to the minimal assembly required for catalysis. Complex I functions in the transfer of electrons from NADH to the respiratory chain. (475 aa) |
| | bckdha | 2-oxoisovalerate dehydrogenase subunit alpha; The branched-chain alpha-keto dehydrogenase complex catalyzes the overall conversion of alpha-keto acids to acyl-CoA and CO(2). It contains multiple copies of three enzymatic components: branched-chain alpha-keto acid decarboxylase (E1), lipoamide acyltransferase (E2) and lipoamide dehydrogenase (E3). (433 aa) |
| | dnajc19 | Homolog of yeast TIM14. (115 aa) |
| | cox7a2 | Intraflagellar transport 52. (83 aa) |
| | ndufs8 | Microtubule-associated protein RP/EB family member 1. (210 aa) |
| | cox7a2l | Uncharacterized protein. (175 aa) |
| | mrps34 | Leucine rich repeat containing 15. (215 aa) |
| | uqcrc1 | Zinc finger protein, FOG family member 2. (432 aa) |
| | uqcrq | Uncharacterized protein. (82 aa) |
| | mrpl10 | Peptidylprolyl isomerase like 1. (249 aa) |
| | atp5mc3 | ATP synthase, H+ transporting, mitochondrial F0 complex, subunit C3 (Subunit 9); Belongs to the ATPase C chain family. (142 aa) |
| | polg | Tyrosylprotein sulfotransferase 1. (1197 aa) |
| | mtx2 | DDB1 and CUL4 associated factor 17. (274 aa) |
| | nsun4 | 5-methylcytosine rRNA methyltransferase NSUN4; Involved in mitochondrial ribosome large subunit biogenesis. Belongs to the class I-like SAM-binding methyltransferase superfamily. RsmB/NOP family. (406 aa) |
| | uqcrh | TOPBP1-interacting checkpoint and replication regulator. (94 aa) |
| | mrps11 | Uncharacterized protein; Belongs to the universal ribosomal protein uS11 family. (195 aa) |
| | mrpl46 | LOC100125128 protein. (278 aa) |
| | MRPL54 | Mitochondrial ribosomal protein L54. (122 aa) |
| | pmpcb | Zinc finger and BTB domain containing 9; Belongs to the peptidase M16 family. (517 aa) |
| | prorp | Chromosome 1 open reading frame 21. (583 aa) |
| | TOMM7 | Translocase of outer mitochondrial membrane 7. (112 aa) |
| | mrps24 | Rho GTPase activating protein 10. (214 aa) |
| | idh3a | Isocitrate dehydrogenase [NAD] subunit, mitochondrial. (384 aa) |
| | mrpl45 | 39S ribosomal protein L45, mitochondrial; Belongs to the mitochondrion-specific ribosomal protein mL45 family. (349 aa) |
| | phb | Prohibitin. (272 aa) |
| | cox5b.2 | Novel protein similar to cytochrome c oxidase subunit Vb. (131 aa) |
| | LOC100497391 | LanC like 3. (582 aa) |
| | ndufa8 | NADH dehydrogenase [ubiquinone] 1 alpha subcomplex subunit 8; Accessory subunit of the mitochondrial membrane respiratory chain NADH dehydrogenase (Complex I), that is believed not to be involved in catalysis. Complex I functions in the transfer of electrons from NADH to the respiratory chain. The immediate electron acceptor for the enzyme is believed to be ubiquinone. (172 aa) |
| | ndufa9 | Tetratricopeptide repeat domain 27. (380 aa) |
| | faf2 | FAS-associated factor 2; Plays an important role in endoplasmic reticulum associated degradation (ERAD) that mediates ubiquitin-dependent degradation of misfolded endoplasmic reticulum proteins. Involved in inhibition of lipid droplet degradation. (460 aa) |
| | mterf4 | Mitochondrial transcription termination factor 4. (322 aa) |
| | mrps18c | Novel protein similar to mitochondrial ribosomal protein S18C; Belongs to the bacterial ribosomal protein bS18 family. (131 aa) |
| | mrps14 | GTPase activating Rap/RanGAP domain-like 3. (137 aa) |
| | tomm20 | Mitochondrial import receptor subunit TOM20 homolog; Central component of the receptor complex responsible for the recognition and translocation of cytosolically synthesized mitochondrial preproteins. Together with tom22 functions as the transit peptide receptor at the surface of the mitochondrion outer membrane and facilitates the movement of preproteins into the tom40 translocation pore (By similarity). (164 aa) |
| | atp5f1c | ATP synthase subunit gamma. (297 aa) |
| | mrps35 | MRP-S28 domain-containing protein. (326 aa) |
| | mrpl30 | TIMP metallopeptidase inhibitor 2. (194 aa) |
| | atp5pb | ATP synthase, H+ transporting, mitochondrial F0 complex, subunit b, isoform 1. (250 aa) |
| | mpp7 | MAGUK p55 subfamily member 7; Acts as an important adapter that promotes epithelial cell polarity and tight junction formation. Involved in the assembly of protein complexes at sites of cell-cell contact (By similarity). Belongs to the MAGUK family. (576 aa) |
| | ndufa1 | LOC100135137 protein. (70 aa) |
| | slc25a5 | Adenine nucleotide translocase; Belongs to the mitochondrial carrier (TC 2.A.29) family. (298 aa) |
| | cox4i1 | Cytochrome c oxidase subunit IV isoform 1. (169 aa) |
| | ndufb10 | Xeroderma pigmentosum, complementation group A. (174 aa) |
| | mrps7 | Ubiquilin 4. (309 aa) |
| | atp5pd | ATP synthase subunit d, mitochondrial; Mitochondrial membrane ATP synthase (F(1)F(0) ATP synthase or Complex V) produces ATP from ADP in the presence of a proton gradient across the membrane which is generated by electron transport complexes of the respiratory chain. F-type ATPases consist of two structural domains, F(1) - containing the extramembraneous catalytic core, and F(0) - containing the membrane proton channel, linked together by a central stalk and a peripheral stalk. During catalysis, ATP synthesis in the catalytic domain of F(1) is coupled via a rotary mechanism of the cent [...] (170 aa) |
| | MRPL58 | Mitochondrial ribosomal protein L58. (216 aa) |
| | MRPL49 | Mitochondrial ribosomal protein L49. (165 aa) |
| | NDUFB1 | NADH:ubiquinone oxidoreductase subunit B1. (58 aa) |
| | MRPL37 | Mitochondrial ribosomal protein L37. (417 aa) |
| | mccc2 | Uncharacterized protein. (566 aa) |
| | mrps27 | Clusterin associated protein 1. (405 aa) |
| | grpel2 | Uncharacterized protein; Belongs to the GrpE family. (230 aa) |
| | mrpl27 | HOP homeobox. (136 aa) |
| | heatr5b | HEAT repeat-containing protein 5B; Belongs to the HEATR5 family. (2052 aa) |
| | pdhb | Pyruvate dehydrogenase E1 component subunit beta; The pyruvate dehydrogenase complex catalyzes the overall conversion of pyruvate to acetyl-CoA and CO2. (360 aa) |
| | thdl18-2 | Uncharacterized protein. (44 aa) |
| | pnpt1 | F-box DNA helicase 1. (789 aa) |
| | mrpl18 | Uncharacterized protein. (179 aa) |
| | mrpl15 | Ras association (RalGDS/AF-6) domain family (N-terminal) member 10. (296 aa) |
| | mrpl42 | Actin related protein 2/3 complex subunit 5-like. (148 aa) |
| | mrps30 | BTB/POZ domain-containing protein kctd15. (539 aa) |
| | mrpl35 | Uncharacterized protein. (315 aa) |
| | suclg1 | Succinate--CoA ligase [ADP/GDP-forming] subunit alpha, mitochondrial; Succinyl-CoA synthetase functions in the citric acid cycle (TCA), coupling the hydrolysis of succinyl-CoA to the synthesis of either ATP or GTP and thus represents the only step of substrate-level phosphorylation in the TCA. The alpha subunit of the enzyme binds the substrates coenzyme A and phosphate, while succinate binding and specificity for either ATP or GTP is provided by different beta subunits. (346 aa) |
| | ndufa12 | NADH dehydrogenase [ubiquinone] 1 alpha subcomplex subunit 12; Accessory subunit of the mitochondrial membrane respiratory chain NADH dehydrogenase (Complex I), that is believed not to be involved in catalysis. Complex I functions in the transfer of electrons from NADH to the respiratory chain. The immediate electron acceptor for the enzyme is believed to be ubiquinone. (144 aa) |
| | timm10 | Mitochondrial import inner membrane translocase subunit Tim10; Mitochondrial intermembrane chaperone that participates in the import and insertion of multi-pass transmembrane proteins into the mitochondrial inner membrane. May also be required for the transfer of beta-barrel precursors from the TOM complex to the sorting and assembly machinery (SAM complex) of the outer membrane. Acts as a chaperone-like protein that protects the hydrophobic precursors from aggregation and guide them through the mitochondrial intermembrane space (By similarity); Belongs to the small Tim family. (125 aa) |
| | ndufa7 | Protein kinase N3. (115 aa) |
| | timm22 | Mitochondrial import inner membrane translocase subunit Tim22; Essential core component of the TIM22 complex, a complex that mediates the import and insertion of multi-pass transmembrane proteins into the mitochondrial inner membrane. In the TIM22 complex, it constitutes the voltage-activated and signal-gated channel. Forms a twin-pore translocase that uses the membrane potential as external driving force in 2 voltage-dependent steps (By similarity). (193 aa) |
| | ndufs4 | Uncharacterized protein. (169 aa) |
| | NDUFC1 | NADH:ubiquinone oxidoreductase subunit C1. (69 aa) |
| | afg3l2 | Uncharacterized protein. (808 aa) |
| | drap1-2 | DR1-associated protein 1 (negative cofactor 2 alpha). (162 aa) |
| | mrps36 | MARVEL domain-containing 1. (110 aa) |
| | vdac1 | Phosphatidylinositol 4-kinase type 2-alpha. (325 aa) |
| | cox5b.1 | ADAM metallopeptidase with thrombospondin type 1 motif 1. (126 aa) |
| | pdhx | Dihydrolipoamide acetyltransferase component of pyruvate dehydrogenase complex. (488 aa) |
| | nectin2 | Heat shock transcription factor 2 binding protein. (464 aa) |
| | tomm40 | Mitochondrial import receptor subunit TOM40 homolog; Channel-forming protein essential for import of protein precursors into mitochondria. (336 aa) |
| | dlat | Acetyltransferase component of pyruvate dehydrogenase complex; The pyruvate dehydrogenase complex catalyzes the overall conversion of pyruvate to acetyl-CoA and CO(2). (628 aa) |
| | idh3g | Isocitrate dehydrogenase [NAD] subunit, mitochondrial. (395 aa) |
| | mrpl4 | Uncharacterized protein. (326 aa) |
| | timm8a | Lysophosphatidylglycerol acyltransferase 1; Belongs to the small Tim family. (97 aa) |
| | mfn1 | Dynamin-type G domain-containing protein; Belongs to the TRAFAC class dynamin-like GTPase superfamily. Dynamin/Fzo/YdjA family. (756 aa) |
| | MTX3 | Metaxin. (326 aa) |
| | foxred1 | DAO domain-containing protein. (504 aa) |
| | LOC108645444 | Ubiquitin specific peptidase 37. (311 aa) |
| | mrpl47 | Chimerin 2. (250 aa) |
