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| | FH | Succinate dehydrogenase [ubiquinone] flavoprotein subunit, mitochondrial; Flavoprotein (FP) subunit of succinate dehydrogenase (SDH) that is involved in complex II of the mitochondrial electron transport chain and is responsible for transferring electrons from succinate to ubiquinone (coenzyme Q). (1165 aa) |
| | DGUOK | Deoxyguanosine kinase, mitochondrial isoform B. (251 aa) |
| | NDUFA12 | NADH dehydrogenase [ubiquinone] 1 alpha subcomplex subunit 12; Accessory subunit of the mitochondrial membrane respiratory chain NADH dehydrogenase (Complex I), that is believed not to be involved in catalysis. Complex I functions in the transfer of electrons from NADH to the respiratory chain. The immediate electron acceptor for the enzyme is believed to be ubiquinone. (146 aa) |
| | CYC1 | Cytochrome c1, heme protein, mitochondrial. (312 aa) |
| | SLC25A12 | Calcium-binding mitochondrial carrier protein Aralar1; Belongs to the mitochondrial carrier (TC 2.A.29) family. (677 aa) |
| | ATP5BL | ATP synthase subunit beta, mitochondrial. (362 aa) |
| | CUNH1orf198 | DUF4706 domain-containing protein. (332 aa) |
| | COA6 | Cytochrome c oxidase assembly factor 6-like protein. (79 aa) |
| | MTFR2 | Mitochondrial fission regulator 2 isoform A. (438 aa) |
| | UQCRQ | Cytochrome b-c1 complex subunit 8. (82 aa) |
| | LYRM7 | Complex III assembly factor LYRM7; Belongs to the complex I LYR family. (106 aa) |
| | FXN | Frataxin, mitochondrial. (173 aa) |
| | ETFA | Electron transfer flavoprotein subunit alpha, mitochondrial. (334 aa) |
| | IREB2 | Uncharacterized protein; Belongs to the aconitase/IPM isomerase family. (965 aa) |
| | IDH3A | Isocitrate dehydrogenase [NAD] subunit, mitochondrial. (366 aa) |
| | Y1Q_0001631 | ATP synthase subunit O, mitochondrial-like. (85 aa) |
| | NDUFS3 | NADH dehydrogenase [ubiquinone] iron-sulfur protein 3, mitochondrial; Belongs to the complex I 30 kDa subunit family. (246 aa) |
| | CAT | Catalase; Occurs in almost all aerobically respiring organisms and serves to protect cells from the toxic effects of hydrogen peroxide. (528 aa) |
| | ATP5O | ATP synthase subunit O, mitochondrial. (82 aa) |
| | NDUFA8 | NADH dehydrogenase [ubiquinone] 1 alpha subcomplex subunit 8; Accessory subunit of the mitochondrial membrane respiratory chain NADH dehydrogenase (Complex I), that is believed not to be involved in catalysis. Complex I functions in the transfer of electrons from NADH to the respiratory chain. The immediate electron acceptor for the enzyme is believed to be ubiquinone. (172 aa) |
| | COX6B2 | Cytochrome c oxidase subunit 6B2. (107 aa) |
| | MDH1 | Malate dehydrogenase. (334 aa) |
| | SUCLA2 | Succinate--CoA ligase [ADP-forming] subunit beta, mitochondrial; ATP-specific succinyl-CoA synthetase functions in the citric acid cycle (TCA), coupling the hydrolysis of succinyl-CoA to the synthesis of ATP and thus represents the only step of substrate-level phosphorylation in the TCA. The beta subunit provides nucleotide specificity of the enzyme and binds the substrate succinate, while the binding sites for coenzyme A and phosphate are found in the alpha subunit. (455 aa) |
| | DNAJC15 | DnaJ-like protein subfamily C member 15. (145 aa) |
| | Y1Q_0004580 | Uncharacterized protein. (191 aa) |
| | PINK1 | Serine/threonine-protein kinase PINK1, mitochondrial; Belongs to the arginase family. (851 aa) |
| | SDHB | Succinate dehydrogenase [ubiquinone] iron-sulfur subunit, mitochondrial; Iron-sulfur protein (IP) subunit of succinate dehydrogenase (SDH) that is involved in complex II of the mitochondrial electron transport chain and is responsible for transferring electrons from succinate to ubiquinone (coenzyme Q). (277 aa) |
| | LACE1 | Lactation elevated protein 1 isoform B. (499 aa) |
| | SUCLG2 | Succinate--CoA ligase [GDP-forming] subunit beta, mitochondrial; GTP-specific succinyl-CoA synthetase functions in the citric acid cycle (TCA), coupling the hydrolysis of succinyl-CoA to the synthesis of GTP and thus represents the only step of substrate-level phosphorylation in the TCA. The beta subunit provides nucleotide specificity of the enzyme and binds the substrate succinate, while the binding sites for coenzyme A and phosphate are found in the alpha subunit. (405 aa) |
| | PDHB | Pyruvate dehydrogenase E1 component subunit beta; The pyruvate dehydrogenase complex catalyzes the overall conversion of pyruvate to acetyl-CoA and CO2. (270 aa) |
| | NDUFB8 | NADH dehydrogenase [ubiquinone] 1 beta subcomplex subunit 8, mitochondrial; Accessory subunit of the mitochondrial membrane respiratory chain NADH dehydrogenase (Complex I), that is believed not to be involved in catalysis. Complex I functions in the transfer of electrons from NADH to the respiratory chain. The immediate electron acceptor for the enzyme is believed to be ubiquinone. (184 aa) |
| | OGDHL | 2-oxoglutarate dehydrogenase-like, mitochondrial isoform B. (967 aa) |
| | MTFR1L | Mitochondrial fission regulator 1-like. (287 aa) |
| | MTFR1 | Mitochondrial fission regulator 1. (306 aa) |
| | BLOC1S1 | Biogenesis of lysosome-related organelles complex 1 subunit 1. (106 aa) |
| | SLC25A13 | Uncharacterized protein; Belongs to the mitochondrial carrier (TC 2.A.29) family. (497 aa) |
| | Y1Q_0019264 | Cytochrome c; Electron carrier protein. The oxidized form of the cytochrome c heme group can accept an electron from the heme group of the cytochrome c1 subunit of cytochrome reductase. Cytochrome c then transfers this electron to the cytochrome oxidase complex, the final protein carrier in the mitochondrial electron-transport chain. (129 aa) |
| | COQ9 | Ubiquinone biosynthesis protein; Lipid-binding protein involved in the biosynthesis of coenzyme Q, also named ubiquinone, an essential lipid-soluble electron transporter for aerobic cellular respiration. (311 aa) |
| | DLST | annotation not available (423 aa) |
| | OGDHL-2 | Transket_pyr domain-containing protein. (1086 aa) |
| | COX7A2 | Cytochrome c oxidase subunit 7A2, mitochondrial. (89 aa) |
| | NDUFAF1 | Complex I intermediate-associated protein 30, mitochondrial. (172 aa) |
| | ETFB | Electron transfer flavoprotein subunit beta. (257 aa) |
| | ATP5A1 | ATP synthase subunit alpha; Produces ATP from ADP in the presence of a proton gradient across the membrane. (548 aa) |
| | NDUFS4 | NADH dehydrogenase [ubiquinone] iron-sulfur protein 4, mitochondrial. (165 aa) |
| | COX6C | Cytochrome c oxidase subunit 6C. (105 aa) |
| | SUCLG1 | Succinate--CoA ligase [ADP/GDP-forming] subunit alpha, mitochondrial; Succinyl-CoA synthetase functions in the citric acid cycle (TCA), coupling the hydrolysis of succinyl-CoA to the synthesis of either ATP or GTP and thus represents the only step of substrate-level phosphorylation in the TCA. The alpha subunit of the enzyme binds the substrates coenzyme A and phosphate, while succinate binding and specificity for either ATP or GTP is provided by different beta subunits. (330 aa) |
| | IDH3B | Isocitrate dehydrogenase [NAD] subunit beta, mitochondrial. (255 aa) |
| | PDHA1 | Pyruvate dehydrogenase E1 component subunit alpha; The pyruvate dehydrogenase complex catalyzes the overall conversion of pyruvate to acetyl-CoA and CO(2). (395 aa) |
| | ATP5J2 | ATP synthase subunit f, mitochondrial. (244 aa) |
| | POLG2 | DNA polymerase subunit gamma-2, mitochondrial. (397 aa) |
| | ATP5H | ATP synthase subunit d, mitochondrial; Mitochondrial membrane ATP synthase (F(1)F(0) ATP synthase or Complex V) produces ATP from ADP in the presence of a proton gradient across the membrane which is generated by electron transport complexes of the respiratory chain. F-type ATPases consist of two structural domains, F(1) - containing the extramembraneous catalytic core, and F(0) - containing the membrane proton channel, linked together by a central stalk and a peripheral stalk. During catalysis, ATP synthesis in the catalytic domain of F(1) is coupled via a rotary mechanism of the cent [...] (185 aa) |
| | TEFM | Transcription elongation factor, mitochondrial. (235 aa) |
| | NDUFV1 | NADH dehydrogenase [ubiquinone] flavoprotein 1, mitochondrial. (792 aa) |
| | NDUFC2 | NADH dehydrogenase [ubiquinone] 1 subunit C2; Accessory subunit of the mitochondrial membrane respiratory chain NADH dehydrogenase (Complex I), that is believed not to be involved in catalysis. Complex I functions in the transfer of electrons from NADH to the respiratory chain. The immediate electron acceptor for the enzyme is believed to be ubiquinone. (110 aa) |
| | COX6A1 | Cytochrome c oxidase subunit 6A, mitochondrial. (95 aa) |
| | MDH2 | Malate dehydrogenase. (329 aa) |
| | MYBBP1A | Myb-binding protein 1A. (1143 aa) |
| | UQCRFS1 | Cytochrome b-c1 complex subunit Rieske, mitochondrial; Component of the ubiquinol-cytochrome c reductase complex (complex III or cytochrome b-c1 complex), which is a respiratory chain that generates an electrochemical potential coupled to ATP synthesis. (278 aa) |
| | Y1Q_0008596 | Coenzyme Q-binding COQ10-like protein B, mitochondrial-like. (225 aa) |
| | NDUFS1 | NADH-ubiquinone oxidoreductase subunit, mitochondrial; Belongs to the complex I 75 kDa subunit family. (766 aa) |
| | MDH1B | Putative malate dehydrogenase 1B isoform B. (548 aa) |
| | IDH1-2 | Isocitrate dehydrogenase [NADP]; Belongs to the isocitrate and isopropylmalate dehydrogenases family. (435 aa) |
| | NDUFA10 | NADH dehydrogenase [ubiquinone] 1 alpha subcomplex subunit 10, mitochondrial; Accessory subunit of the mitochondrial membrane respiratory chain NADH dehydrogenase (Complex I), that is believed not to be involved in catalysis. Complex I functions in the transfer of electrons from NADH to the respiratory chain. The immediate electron acceptor for the enzyme is believed to be ubiquinone. (357 aa) |
| | COQ10B | Coenzyme Q-binding COQ10-like protein B, mitochondrial. (246 aa) |
| | CUNH2orf69 | Uncharacterized protein. (349 aa) |
| | TAZ | Tafazzin family protein; Belongs to the taffazin family. (277 aa) |
| | NDUFA7-1 | NADH dehydrogenase [ubiquinone] 1 alpha subcomplex subunit 7 isoform B. (223 aa) |
| | NDUFS6 | NADH dehydrogenase [ubiquinone] iron-sulfur protein 6, mitochondrial. (150 aa) |
| | Y1Q_0018516 | Ig-like domain-containing protein. (208 aa) |
| | ATP5I | ATP synthase subunit e, mitochondrial. (71 aa) |
| | NDUFB6 | NADH dehydrogenase [ubiquinone] 1 beta subcomplex subunit 6. (128 aa) |
| | ACO1 | Cytoplasmic aconitate hydratase; Belongs to the aconitase/IPM isomerase family. (889 aa) |
| | NDUFV2 | NADH dehydrogenase [ubiquinone] flavoprotein 2, mitochondrial. (245 aa) |
| | DLAT | Acetyltransferase component of pyruvate dehydrogenase complex; The pyruvate dehydrogenase complex catalyzes the overall conversion of pyruvate to acetyl-CoA and CO(2). (544 aa) |
| | SDHD | Succinate dehydrogenase [ubiquinone] cytochrome b small subunit; Membrane-anchoring subunit of succinate dehydrogenase (SDH) that is involved in complex II of the mitochondrial electron transport chain and is responsible for transferring electrons from succinate to ubiquinone (coenzyme Q); Belongs to the CybS family. (163 aa) |
| | CS | Citrate synthase; Belongs to the citrate synthase family. (465 aa) |
| | IDH1 | Isocitrate dehydrogenase [NADP]; Belongs to the isocitrate and isopropylmalate dehydrogenases family. (372 aa) |
| | ACO2 | Aconitate hydratase, mitochondrial; Belongs to the aconitase/IPM isomerase family. (783 aa) |
| | SLC25A18 | Mitochondrial glutamate carrier 2 isoform B; Belongs to the mitochondrial carrier (TC 2.A.29) family. (323 aa) |
| | LYRM5 | LYR motif-containing protein 5; Belongs to the complex I LYR family. (88 aa) |
| | SDHC | Succinate dehydrogenase cytochrome b560 subunit, mitochondrial. (169 aa) |
| | COX7B | Cytochrome c oxidase subunit 7B, mitochondrial. (79 aa) |
| | COX5B | Cytochrome c oxidase subunit 5B, mitochondrial. (130 aa) |
| | SEC61A1 | Protein transport protein Sec61 subunit alpha. (1366 aa) |
| | NDUFV3-1 | NADH dehydrogenase [ubiquinone] flavoprotein 3, mitochondrial isoform B. (136 aa) |
| | OR10W1 | Olfactory receptor. (317 aa) |
| | MRPS36 | 28S ribosomal protein S36, mitochondrial. (107 aa) |
| | B3GNTL1 | UDP-GlcNAc:betaGal beta-1,3-N-acetylglucosaminyltransferase-like protein 1 isoform A. (408 aa) |
| | COX10 | Protoheme IX farnesyltransferase, mitochondrial; Converts protoheme IX and farnesyl diphosphate to heme O. Belongs to the ubiA prenyltransferase family. (495 aa) |
| | MSH2 | DNA mismatch repair protein; Component of the post-replicative DNA mismatch repair system (MMR). (937 aa) |
| | SLC25A22 | Mitochondrial glutamate carrier 1; Belongs to the mitochondrial carrier (TC 2.A.29) family. (320 aa) |
| | COX8A | Cytochrome c oxidase subunit 8A, mitochondrial. (70 aa) |
| | PPP1R32 | Succinate dehydrogenase assembly factor 2, mitochondrial; Plays an essential role in the assembly of succinate dehydrogenase (SDH), an enzyme complex (also referred to as respiratory complex II) that is a component of both the tricarboxylic acid (TCA) cycle and the mitochondrial electron transport chain, and which couples the oxidation of succinate to fumarate with the reduction of ubiquinone (coenzyme Q) to ubiquinol. Required for flavinylation (covalent attachment of FAD) of the flavoprotein subunit SDHA of the SDH catalytic dimer. (596 aa) |
| | SIRT3-1 | NAD-dependent protein deacetylase; NAD-dependent protein deacetylase. (390 aa) |
| | AIFM2 | Apoptosis-inducing factor 2 isoform B. (522 aa) |
| | Y1Q_0020518 | Cytochrome c oxidase subunit 6A2, mitochondrial; Belongs to the cytochrome c oxidase subunit 6A family. (107 aa) |
| | COX7A2L | Cytochrome c oxidase subunit VIIa polypeptide 2 like. (116 aa) |
| | COQ10A | Coenzyme Q-binding COQ10-like protein A, mitochondrial. (162 aa) |
| | ATP5D | ATP synthase subunit delta, mitochondrial. (137 aa) |
| | PPARGC1A | Peroxisome proliferator-activated receptor gamma coactivator 1-alpha isoform A. (555 aa) |
| | ETFDH | Electron transfer flavoprotein-ubiquinone oxidoreductase; Accepts electrons from ETF and reduces ubiquinone. (618 aa) |
| | ATP5B | ATP synthase subunit beta; Produces ATP from ADP in the presence of a proton gradient across the membrane. (493 aa) |
| | NDUFA5 | NADH dehydrogenase [ubiquinone] 1 alpha subcomplex subunit 5. (116 aa) |
| | IMMP2LL | Mitochondrial inner membrane protease subunit 2. (90 aa) |
| | IMMP2L | Mitochondrial inner membrane protease subunit 2 isoform A. (129 aa) |
| | NDUFS2 | NADH dehydrogenase [ubiquinone] iron-sulfur protein 2, mitochondrial; Belongs to the complex I 49 kDa subunit family. (455 aa) |
| | NDUFS7 | NADH dehydrogenase [ubiquinone] iron-sulfur protein 7, mitochondrial; Belongs to the complex I 20 kDa subunit family. (204 aa) |
| | STOML2 | Stomatin-like protein 2, mitochondrial. (326 aa) |
| | Y1Q_0017874 | Tetraspanin; Belongs to the tetraspanin (TM4SF) family. (478 aa) |
