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CLCR_02965 | Isovaleryl-CoA dehydrogenase, mitochondrial. (438 aa) | ||||
auh | Methylglutaconyl-CoA hydratase, mitochondrial. (301 aa) | ||||
DIN4 | 2-oxoisovalerate dehydrogenase subunit beta 2, mitochondrial. (391 aa) | ||||
Aldh6a1 | Methylmalonate-semialdehyde dehydrogenase [acylating], mitochondrial. (566 aa) | ||||
CLCR_06443 | Uncharacterized protein. (119 aa) | ||||
CLCR_06362 | Uncharacterized protein. (177 aa) | ||||
hibch | 3-hydroxyisobutyryl-CoA hydrolase, mitochondrial; Hydrolyzes 3-hydroxyisobutyryl-CoA (HIBYL-CoA), a saline catabolite; Belongs to the enoyl-CoA hydratase/isomerase family. (483 aa) | ||||
Hibadh | 3-hydroxyisobutyrate dehydrogenase, mitochondrial. (358 aa) | ||||
CLCR_06194 | 3-hydroxypropionyl-coenzyme A dehydratase. (277 aa) | ||||
caiD | Carnitinyl-CoA dehydratase; Belongs to the enoyl-CoA hydratase/isomerase family. (282 aa) | ||||
CLCR_01622 | Putative 3-hydroxyisobutyrate dehydrogenase, mitochondrial. (340 aa) | ||||
CLCR_00486 | Putative methylcrotonoyl-CoA carboxylase beta chain, mitochondrial. (338 aa) | ||||
CLCR_00520 | CoA carboxyltransferase C-terminal domain-containing protein. (202 aa) | ||||
caiD-2 | Carnitinyl-CoA dehydratase; Belongs to the enoyl-CoA hydratase/isomerase family. (273 aa) | ||||
TOXF | Putative branched-chain-amino-acid aminotransferase TOXF. (380 aa) | ||||
CLCR_02025 | Putative 3-hydroxyisobutyrate dehydrogenase, mitochondrial. (329 aa) | ||||
CLCR_02467 | Putative 3-hydroxyisobutyrate dehydrogenase, mitochondrial. (335 aa) | ||||
caiD-3 | Carnitinyl-CoA dehydratase. (225 aa) | ||||
mmgC | Acyl-CoA dehydrogenase. (465 aa) | ||||
HQD2 | Catechol 1,2-dioxygenase. (320 aa) | ||||
CLCR_11319 | 3-hydroxypropionyl-coenzyme A dehydratase. (316 aa) | ||||
HSD17B10 | 3-hydroxyacyl-CoA dehydrogenase type-2. (294 aa) | ||||
CLCR_07399 | Uncharacterized protein. (310 aa) | ||||
CLCR_06971 | Putative methylcrotonoyl-CoA carboxylase beta chain, mitochondrial. (572 aa) | ||||
caiD-4 | Carnitinyl-CoA dehydratase. (293 aa) | ||||
echs1 | Putative enoyl-CoA hydratase, mitochondrial; Belongs to the enoyl-CoA hydratase/isomerase family. (310 aa) | ||||
BAT1-3 | Branched-chain-amino-acid aminotransferase; Belongs to the class-IV pyridoxal-phosphate-dependent aminotransferase family. (424 aa) | ||||
BAT1-4 | Branched-chain-amino-acid aminotransferase; Belongs to the class-IV pyridoxal-phosphate-dependent aminotransferase family. (450 aa) | ||||
Dbt | Dihydrolipoamide acetyltransferase component of pyruvate dehydrogenase complex. (478 aa) | ||||
CLCR_08696 | Uncharacterized protein. (394 aa) | ||||
CLCR_08496 | Putative oxidoreductase,short chain dehydrogenase. (330 aa) | ||||
CLCR_10980 | Enoyl-CoA hydratase. (141 aa) | ||||
CLCR_10968 | Uncharacterized protein. (145 aa) | ||||
PKP2 | Protein-serine/threonine kinase. (440 aa) | ||||
mmsB | 3-hydroxyisobutyrate dehydrogenase. (337 aa) | ||||
CLCR_10624 | 3-hydroxybutyryl-CoA dehydratase-like protein, mitochondrial; Belongs to the enoyl-CoA hydratase/isomerase family. (295 aa) | ||||
CLCR_10096 | Protein-serine/threonine kinase. (484 aa) | ||||
CLCR_00290 | 2-oxoisovalerate dehydrogenase subunit alpha; The branched-chain alpha-keto dehydrogenase complex catalyzes the overall conversion of alpha-keto acids to acyl-CoA and CO(2). It contains multiple copies of three enzymatic components: branched-chain alpha-keto acid decarboxylase (E1), lipoamide acyltransferase (E2) and lipoamide dehydrogenase (E3). (396 aa) |