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| | COX3 | Cytochrome c oxidase subunit 3; Component of the cytochrome c oxidase, the last enzyme in the mitochondrial electron transport chain which drives oxidative phosphorylation. The respiratory chain contains 3 multisubunit complexes succinate dehydrogenase (complex II, CII), ubiquinol- cytochrome c oxidoreductase (cytochrome b-c1 complex, complex III, CIII) and cytochrome c oxidase (complex IV, CIV), that cooperate to transfer electrons derived from NADH and succinate to molecular oxygen, creating an electrochemical gradient over the inner membrane that drives transmembrane transport and t [...] (261 aa) |
| | SLC25A14 | Solute carrier family 25 member 14; Belongs to the mitochondrial carrier (TC 2.A.29) family. (360 aa) |
| | NDUFS3 | NADH:ubiquinone oxidoreductase core subunit S3; Belongs to the complex I 30 kDa subunit family. (264 aa) |
| | DLST | Dihydrolipoamide S-succinyltransferase. (453 aa) |
| | ENSPPAP00000016543 | Uncharacterized protein. (78 aa) |
| | SLC16A8 | Solute carrier family 16 member 8. (504 aa) |
| | BSG | Basigin (Ok blood group). (362 aa) |
| | NDUFS4 | NADH:ubiquinone oxidoreductase subunit S4. (175 aa) |
| | FAHD1 | Fumarylacetoacetate hydrolase domain containing 1. (224 aa) |
| | NDUFS1 | NADH:ubiquinone oxidoreductase core subunit S1; Belongs to the complex I 75 kDa subunit family. (741 aa) |
| | ENSPPAP00000025500 | Uncharacterized protein. (156 aa) |
| | ENSPPAP00000025587 | Uncharacterized protein. (111 aa) |
| | ENSPPAP00000025753 | Uncharacterized protein. (251 aa) |
| | DESI2 | Desumoylating isopeptidase 2. (194 aa) |
| | SCO1 | SCO cytochrome c oxidase assembly protein 1. (301 aa) |
| | GLO1 | Lactoylglutathione lyase; Catalyzes the conversion of hemimercaptal, formed from methylglyoxal and glutathione, to S-lactoylglutathione. (184 aa) |
| | ENSPPAP00000026400 | Uncharacterized protein. (248 aa) |
| | COX19 | Cytochrome c oxidase assembly factor COX19. (90 aa) |
| | ME2 | Malic enzyme. (584 aa) |
| | ENSPPAP00000026755 | ATP-synt_C domain-containing protein. (121 aa) |
| | ATP5MC3 | ATP synthase membrane subunit c locus 3; Belongs to the ATPase C chain family. (142 aa) |
| | ATP5PD | ATP synthase subunit d, mitochondrial; Mitochondrial membrane ATP synthase (F(1)F(0) ATP synthase or Complex V) produces ATP from ADP in the presence of a proton gradient across the membrane which is generated by electron transport complexes of the respiratory chain. F-type ATPases consist of two structural domains, F(1) - containing the extramembraneous catalytic core, and F(0) - containing the membrane proton channel, linked together by a central stalk and a peripheral stalk. During catalysis, ATP synthesis in the catalytic domain of F(1) is coupled via a rotary mechanism of the cent [...] (161 aa) |
| | SDHB | Succinate dehydrogenase [ubiquinone] iron-sulfur subunit, mitochondrial; Iron-sulfur protein (IP) subunit of succinate dehydrogenase (SDH) that is involved in complex II of the mitochondrial electron transport chain and is responsible for transferring electrons from succinate to ubiquinone (coenzyme Q). (280 aa) |
| | CS | Citrate synthase; Belongs to the citrate synthase family. (466 aa) |
| | ETFB | Electron transfer flavoprotein subunit beta. (293 aa) |
| | DMAC2 | Distal membrane arm assembly complex 2. (263 aa) |
| | ATP5MF | Uncharacterized protein. (102 aa) |
| | ENSPPAP00000027991 | Uncharacterized protein. (79 aa) |
| | NDUFAF4 | NADH:ubiquinone oxidoreductase complex assembly factor 4. (175 aa) |
| | ENSPPAP00000028304 | Uncharacterized protein. (153 aa) |
| | NDUFA6 | NADH:ubiquinone oxidoreductase subunit A6; Belongs to the complex I LYR family. (154 aa) |
| | ENSPPAP00000028403 | Uncharacterized protein. (274 aa) |
| | TMEM186 | Transmembrane protein 186. (213 aa) |
| | VDAC1 | Voltage dependent anion channel 1. (289 aa) |
| | ATP5F1B | ATP synthase subunit beta; Produces ATP from ADP in the presence of a proton gradient across the membrane. (529 aa) |
| | SUCLA2 | Succinate--CoA ligase [ADP-forming] subunit beta, mitochondrial; ATP-specific succinyl-CoA synthetase functions in the citric acid cycle (TCA), coupling the hydrolysis of succinyl-CoA to the synthesis of ATP and thus represents the only step of substrate-level phosphorylation in the TCA. The beta subunit provides nucleotide specificity of the enzyme and binds the substrate succinate, while the binding sites for coenzyme A and phosphate are found in the alpha subunit. (463 aa) |
| | ECSIT | ECSIT signalling integrator. (431 aa) |
| | UQCRH | Cytochrome b-c1 complex subunit 6; This is a component of the ubiquinol-cytochrome c reductase complex (complex III or cytochrome b-c1 complex), which is part of the mitochondrial respiratory chain. This protein may mediate formation of the complex between cytochromes c and c1. Belongs to the UQCRH/QCR6 family. (91 aa) |
| | NDUFAF3 | NADH:ubiquinone oxidoreductase complex assembly factor 3. (184 aa) |
| | ENSPPAP00000029278 | Uncharacterized protein. (123 aa) |
| | ATP5MC2 | ATP-synt_C domain-containing protein; Belongs to the ATPase C chain family. (198 aa) |
| | NDUFA10 | NADH dehydrogenase [ubiquinone] 1 alpha subcomplex subunit 10, mitochondrial; Accessory subunit of the mitochondrial membrane respiratory chain NADH dehydrogenase (Complex I), that is believed not to be involved in catalysis. Complex I functions in the transfer of electrons from NADH to the respiratory chain. The immediate electron acceptor for the enzyme is believed to be ubiquinone. (404 aa) |
| | LOC100985422 | Uncharacterized protein. (232 aa) |
| | LDHC | L-lactate dehydrogenase; Belongs to the LDH/MDH superfamily. (332 aa) |
| | COX16 | Cytochrome c oxidase assembly factor COX16. (106 aa) |
| | NDUFB6 | NADH:ubiquinone oxidoreductase subunit B6. (113 aa) |
| | COX7B | Cytochrome c oxidase subunit 7B. (80 aa) |
| | ENSPPAP00000030325 | Cytochrome b-c1 complex subunit 6; This is a component of the ubiquinol-cytochrome c reductase complex (complex III or cytochrome b-c1 complex), which is part of the mitochondrial respiratory chain. This protein may mediate formation of the complex between cytochromes c and c1. Belongs to the UQCRH/QCR6 family. (90 aa) |
| | NDUFA9 | NADH:ubiquinone oxidoreductase subunit A9. (377 aa) |
| | LOC100994201 | L-lactate dehydrogenase; Belongs to the LDH/MDH superfamily. (363 aa) |
| | SUCLG2-2 | Succinate--CoA ligase [GDP-forming] subunit beta, mitochondrial; GTP-specific succinyl-CoA synthetase functions in the citric acid cycle (TCA), coupling the hydrolysis of succinyl-CoA to the synthesis of GTP and thus represents the only step of substrate-level phosphorylation in the TCA. The beta subunit provides nucleotide specificity of the enzyme and binds the substrate succinate, while the binding sites for coenzyme A and phosphate are found in the alpha subunit. (426 aa) |
| | PPARD | Peroxisome proliferator activated receptor delta. (441 aa) |
| | ATP5ME | ATP synthase membrane subunit e. (57 aa) |
| | WBP2NL | WBP2 N-terminal like. (302 aa) |
| | NDUFS6 | zf-CHCC domain-containing protein. (171 aa) |
| | ENSPPAP00000032095 | Uncharacterized protein; Belongs to the LDH/MDH superfamily. (310 aa) |
| | NDUFC2 | NADH dehydrogenase [ubiquinone] 1 subunit C2; Accessory subunit of the mitochondrial membrane respiratory chain NADH dehydrogenase (Complex I), that is believed not to be involved in catalysis. Complex I functions in the transfer of electrons from NADH to the respiratory chain. The immediate electron acceptor for the enzyme is believed to be ubiquinone. (118 aa) |
| | NDUFS8 | NADH:ubiquinone oxidoreductase core subunit S8. (210 aa) |
| | ETFA | Electron transfer flavoprotein subunit alpha. (333 aa) |
| | ENSPPAP00000033125 | L-lactate dehydrogenase; Belongs to the LDH/MDH superfamily. (350 aa) |
| | NDUFB9 | NADH:ubiquinone oxidoreductase subunit B9; Belongs to the complex I LYR family. (179 aa) |
| | NDUFB2 | NADH:ubiquinone oxidoreductase subunit B2. (105 aa) |
| | COX6B1 | Cytochrome c oxidase subunit; Belongs to the cytochrome c oxidase subunit 6B. (86 aa) |
| | ENSPPAP00000034038 | Uncharacterized protein. (256 aa) |
| | ATP5MC1 | ATP synthase membrane subunit c locus 1; Belongs to the ATPase C chain family. (136 aa) |
| | NDUFB10 | NADH:ubiquinone oxidoreductase subunit B10. (172 aa) |
| | ATP5PB | Uncharacterized protein. (250 aa) |
| | SDHD | Succinate dehydrogenase [ubiquinone] cytochrome b small subunit; Membrane-anchoring subunit of succinate dehydrogenase (SDH) that is involved in complex II of the mitochondrial electron transport chain and is responsible for transferring electrons from succinate to ubiquinone (coenzyme Q); Belongs to the CybS family. (159 aa) |
| | COX4I1 | Cytochrome c oxidase subunit 4I1. (169 aa) |
| | OGDH | Oxoglutarate dehydrogenase. (1038 aa) |
| | IDH3A | Isocitrate dehydrogenase [NAD] subunit, mitochondrial. (373 aa) |
| | COX4I2 | Cytochrome c oxidase subunit 4I2. (171 aa) |
| | COX11 | Cytochrome c oxidase copper chaperone COX11. (276 aa) |
| | NDUFB3 | NADH:ubiquinone oxidoreductase subunit B3. (98 aa) |
| | LRPPRC | PPR_long domain-containing protein. (1388 aa) |
| | GSTZ1 | Glutathione S-transferase zeta 1; Belongs to the GST superfamily. (216 aa) |
| | ENSPPAP00000037199 | Uncharacterized protein. (247 aa) |
| | ACAD9 | Acyl-CoA dehydrogenase family member 9. (583 aa) |
| | COX5B | Cytochrome c oxidase subunit 5B. (129 aa) |
| | ENSPPAP00000037934 | FAA_hydrolase domain-containing protein. (209 aa) |
| | ENSPPAP00000037963 | Cytochrome c domain-containing protein; Electron carrier protein. The oxidized form of the cytochrome c heme group can accept an electron from the heme group of the cytochrome c1 subunit of cytochrome reductase. Cytochrome c then transfers this electron to the cytochrome oxidase complex, the final protein carrier in the mitochondrial electron-transport chain. (110 aa) |
| | LOC100994026 | Uncharacterized protein. (311 aa) |
| | ENSPPAP00000038557 | Uncharacterized protein. (523 aa) |
| | ME1 | Malic enzyme. (572 aa) |
| | IDH3G | Isocitrate dehydrogenase [NAD] subunit, mitochondrial. (393 aa) |
| | COX6C | Cytochrome c oxidase subunit 6C. (75 aa) |
| | RXRA | Retinoid X receptor alpha. (472 aa) |
| | ENSPPAP00000039026 | Uncharacterized protein; Belongs to the ATPase C chain family. (135 aa) |
| | PM20D1 | Peptidase M20 domain containing 1. (428 aa) |
| | COX18 | Cytochrome c oxidase assembly factor COX18. (334 aa) |
| | COX5A | Uncharacterized protein. (139 aa) |
| | PDK1 | Protein-serine/threonine kinase. (456 aa) |
| | COX6A1 | Cytochrome c oxidase subunit 6A, mitochondrial. (109 aa) |
| | UCP3 | Uncoupling protein 3; Belongs to the mitochondrial carrier (TC 2.A.29) family. (312 aa) |
| | ENSPPAP00000041077 | Uncharacterized protein. (261 aa) |
| | ENSPPAP00000041551 | Uncharacterized protein. (69 aa) |
| | LDHA | L-lactate dehydrogenase; Belongs to the LDH/MDH superfamily. (361 aa) |
| | COX7A1 | Cytochrome c oxidase subunit 7A1. (79 aa) |
| | NDUFV1 | NADH dehydrogenase [ubiquinone] flavoprotein 1, mitochondrial; Core subunit of the mitochondrial membrane respiratory chain NADH dehydrogenase (Complex I) that is believed to belong to the minimal assembly required for catalysis. Complex I functions in the transfer of electrons from NADH to the respiratory chain. (464 aa) |
| | PDK3 | Protein-serine/threonine kinase. (417 aa) |
| | NDUFB1 | NADH:ubiquinone oxidoreductase subunit B1. (105 aa) |
| | NDUFA5 | NADH:ubiquinone oxidoreductase subunit A5. (116 aa) |
| | ENSPPAP00000018449 | Cytochrome c domain-containing protein; Electron carrier protein. The oxidized form of the cytochrome c heme group can accept an electron from the heme group of the cytochrome c1 subunit of cytochrome reductase. Cytochrome c then transfers this electron to the cytochrome oxidase complex, the final protein carrier in the mitochondrial electron-transport chain. (90 aa) |
| | ENSPPAP00000018580 | Uncharacterized protein. (51 aa) |
| | MPC2 | Mitochondrial pyruvate carrier; Mediates the uptake of pyruvate into mitochondria. Belongs to the mitochondrial pyruvate carrier (MPC) (TC 2.A.105) family. (127 aa) |
| | IDH2 | Isocitrate dehydrogenase [NADP]; Belongs to the isocitrate and isopropylmalate dehydrogenases family. (428 aa) |
| | NDUFB5 | NADH:ubiquinone oxidoreductase subunit B5. (189 aa) |
| | NDUFV2 | Uncharacterized protein. (252 aa) |
| | ENSPPAP00000019251 | Uncharacterized protein. (62 aa) |
| | ENSPPAP00000019421 | Uncharacterized protein. (75 aa) |
| | COX20 | Cytochrome c oxidase assembly factor COX20. (130 aa) |
| | ENSPPAP00000019695 | Uncharacterized protein. (80 aa) |
| | PDHA1 | Pyruvate dehydrogenase E1 component subunit alpha; The pyruvate dehydrogenase complex catalyzes the overall conversion of pyruvate to acetyl-CoA and CO(2). (463 aa) |
| | ENSPPAP00000020079 | Uncharacterized protein. (80 aa) |
| | SUCLG2 | Succinate--CoA ligase [GDP-forming] subunit beta, mitochondrial; GTP-specific succinyl-CoA synthetase functions in the citric acid cycle (TCA), coupling the hydrolysis of succinyl-CoA to the synthesis of GTP and thus represents the only step of substrate-level phosphorylation in the TCA. The beta subunit provides nucleotide specificity of the enzyme and binds the substrate succinate, while the binding sites for coenzyme A and phosphate are found in the alpha subunit. (433 aa) |
| | NDUFA3 | Uncharacterized protein. (84 aa) |
| | ATP6 | ATP synthase subunit a; Mitochondrial membrane ATP synthase (F(1)F(0) ATP synthase or Complex V) produces ATP from ADP in the presence of a proton gradient across the membrane which is generated by electron transport complexes of the respiratory chain. F-type ATPases consist of two structural domains, F(1) - containing the extramembraneous catalytic core and F(0) - containing the membrane proton channel, linked together by a central stalk and a peripheral stalk. During catalysis, ATP synthesis in the catalytic domain of F(1) is coupled via a rotary mechanism of the central stalk subuni [...] (226 aa) |
| | ATP8 | ATP synthase protein 8; Mitochondrial membrane ATP synthase (F(1)F(0) ATP synthase or Complex V) produces ATP from ADP in the presence of a proton gradient across the membrane which is generated by electron transport complexes of the respiratory chain. F-type ATPases consist of two structural domains, F(1) - containing the extramembraneous catalytic core and F(0) - containing the membrane proton channel, linked together by a central stalk and a peripheral stalk. During catalysis, ATP synthesis in the catalytic domain of F(1) is coupled via a rotary mechanism of the central stalk subuni [...] (68 aa) |
| | COX2 | Cytochrome c oxidase subunit 2; Component of the cytochrome c oxidase, the last enzyme in the mitochondrial electron transport chain which drives oxidative phosphorylation. The respiratory chain contains 3 multisubunit complexes succinate dehydrogenase (complex II, CII), ubiquinol- cytochrome c oxidoreductase (cytochrome b-c1 complex, complex III, CIII) and cytochrome c oxidase (complex IV, CIV), that cooperate to transfer electrons derived from NADH and succinate to molecular oxygen, creating an electrochemical gradient over the inner membrane that drives transmembrane transport and t [...] (227 aa) |
| | COX1 | Cytochrome c oxidase subunit 1; Component of the cytochrome c oxidase, the last enzyme in the mitochondrial electron transport chain which drives oxidative phosphorylation. The respiratory chain contains 3 multisubunit complexes succinate dehydrogenase (complex II, CII), ubiquinol- cytochrome c oxidoreductase (cytochrome b-c1 complex, complex III, CIII) and cytochrome c oxidase (complex IV, CIV), that cooperate to transfer electrons derived from NADH and succinate to molecular oxygen, creating an electrochemical gradient over the inner membrane that drives transmembrane transport and t [...] (513 aa) |
| | ND2 | NADH-ubiquinone oxidoreductase chain 2; Core subunit of the mitochondrial membrane respiratory chain NADH dehydrogenase (Complex I) that is believed to belong to the minimal assembly required for catalysis. Complex I functions in the transfer of electrons from NADH to the respiratory chain. The immediate electron acceptor for the enzyme is believed to be ubiquinone (By similarity). (347 aa) |
| | MT-ND1 | NADH-ubiquinone oxidoreductase chain 1; Belongs to the complex I subunit 1 family. (318 aa) |
| | SLC16A1 | Solute carrier family 16 member 1. (500 aa) |
| | ENSPPAP00000015709 | Uncharacterized protein. (259 aa) |
| | ENSPPAP00000015707 | Uncharacterized protein. (74 aa) |
| | MBLAC2 | Metallo-beta-lactamase domain containing 2. (279 aa) |
| | PDHX | Dihydrolipoamide acetyltransferase component of pyruvate dehydrogenase complex. (501 aa) |
| | ENSPPAP00000014905 | Cytochrome b-c1 complex subunit 7; Component of the ubiquinol-cytochrome c reductase complex (complex III or cytochrome b-c1 complex), which is part of the mitochondrial respiratory chain; Belongs to the UQCRB/QCR7 family. (110 aa) |
| | SUCLG1 | Succinate--CoA ligase [ADP/GDP-forming] subunit alpha, mitochondrial; Succinyl-CoA synthetase functions in the citric acid cycle (TCA), coupling the hydrolysis of succinyl-CoA to the synthesis of either ATP or GTP and thus represents the only step of substrate-level phosphorylation in the TCA. The alpha subunit of the enzyme binds the substrates coenzyme A and phosphate, while succinate binding and specificity for either ATP or GTP is provided by different beta subunits. (336 aa) |
| | ENSPPAP00000020139 | Uncharacterized protein. (113 aa) |
| | ENSPPAP00000020455 | Uncharacterized protein. (103 aa) |
| | ENSPPAP00000020512 | Uncharacterized protein; Belongs to the LDH/MDH superfamily. (350 aa) |
| | NDUFAF1 | NADH:ubiquinone oxidoreductase complex assembly factor 1. (327 aa) |
| | ENSPPAP00000020770 | Uncharacterized protein. (67 aa) |
| | LDHB | L-lactate dehydrogenase; Belongs to the LDH/MDH superfamily. (334 aa) |
| | MDH2 | Malate dehydrogenase. (338 aa) |
| | COX7A2L | Cytochrome c oxidase subunit 7A2 like. (114 aa) |
| | COX7C | Cytochrome c oxidase subunit 7C, mitochondrial; Component of the cytochrome c oxidase, the last enzyme in the mitochondrial electron transport chain which drives oxidative phosphorylation. The respiratory chain contains 3 multisubunit complexes succinate dehydrogenase (complex II, CII), ubiquinol- cytochrome c oxidoreductase (cytochrome b-c1 complex, complex III, CIII) and cytochrome c oxidase (complex IV, CIV), that cooperate to transfer electrons derived from NADH and succinate to molecular oxygen, creating an electrochemical gradient over the inner membrane that drives transmembrane [...] (63 aa) |
| | ETFDH | Electron transfer flavoprotein-ubiquinone oxidoreductase; Accepts electrons from ETF and reduces ubiquinone. (619 aa) |
| | ENSPPAP00000021603 | Uncharacterized protein. (161 aa) |
| | COQ10A | Coenzyme Q10A. (247 aa) |
| | DLD | Dihydrolipoyl dehydrogenase. (538 aa) |
| | UQCRC2 | Ubiquinol-cytochrome c reductase core protein 2; Belongs to the peptidase M16 family. (453 aa) |
| | LOC100985927 | Uncharacterized protein. (229 aa) |
| | NDUFB11 | NADH:ubiquinone oxidoreductase subunit B11. (163 aa) |
| | SLC16A3 | Solute carrier family 16 member 3. (465 aa) |
| | NUBPL | Uncharacterized protein. (132 aa) |
| | MPC1 | Mitochondrial pyruvate carrier; Mediates the uptake of pyruvate into mitochondria. Belongs to the mitochondrial pyruvate carrier (MPC) (TC 2.A.105) family. (66 aa) |
| | TACO1 | Translational activator of cytochrome c oxidase I. (297 aa) |
| | ATP5PF | ATP synthase-coupling factor 6, mitochondrial; Mitochondrial membrane ATP synthase (F(1)F(0) ATP synthase or Complex V) produces ATP from ADP in the presence of a proton gradient across the membrane which is generated by electron transport complexes of the respiratory chain; Belongs to the eukaryotic ATPase subunit F6 family. (118 aa) |
| | UQCRC1 | Ubiquinol-cytochrome c reductase core protein 1. (480 aa) |
| | PNKD | PNKD metallo-beta-lactamase domain containing. (385 aa) |
| | DESI1 | Desumoylating isopeptidase 1. (168 aa) |
| | C1orf198 | Chromosome 1 open reading frame 198. (327 aa) |
| | TMEM126B | Uncharacterized protein. (147 aa) |
| | SDHA | Succinate dehydrogenase [ubiquinone] flavoprotein subunit, mitochondrial; Flavoprotein (FP) subunit of succinate dehydrogenase (SDH) that is involved in complex II of the mitochondrial electron transport chain and is responsible for transferring electrons from succinate to ubiquinone (coenzyme Q). (668 aa) |
| | LOC100979323 | Uncharacterized protein. (93 aa) |
| | OGDHL | Oxoglutarate dehydrogenase like. (1012 aa) |
| | ENSPPAP00000024731 | Cytochrome c domain-containing protein; Electron carrier protein. The oxidized form of the cytochrome c heme group can accept an electron from the heme group of the cytochrome c1 subunit of cytochrome reductase. Cytochrome c then transfers this electron to the cytochrome oxidase complex, the final protein carrier in the mitochondrial electron-transport chain. (117 aa) |
| | ENSPPAP00000042172 | Uncharacterized protein. (92 aa) |
| | DLAT | Acetyltransferase component of pyruvate dehydrogenase complex; The pyruvate dehydrogenase complex catalyzes the overall conversion of pyruvate to acetyl-CoA and CO(2). (646 aa) |
| | LOC100992849 | Succinate dehydrogenase [ubiquinone] cytochrome b small subunit; Membrane-anchoring subunit of succinate dehydrogenase (SDH) that is involved in complex II of the mitochondrial electron transport chain and is responsible for transferring electrons from succinate to ubiquinone (coenzyme Q); Belongs to the CybS family. (129 aa) |
| | NDUFA7 | Uncharacterized protein. (113 aa) |
| | ADHFE1 | Fe-ADH domain-containing protein. (467 aa) |
| | NDUFB7 | NADH:ubiquinone oxidoreductase subunit B7. (137 aa) |
| | NDUFAF2 | Uncharacterized protein. (147 aa) |
| | ATP5F1D | ATP-synt_DE_N domain-containing protein. (163 aa) |
| | NDUFAF5 | NADH:ubiquinone oxidoreductase complex assembly factor 5. (345 aa) |
| | ENSPPAP00000014616 | Ldh_1_N domain-containing protein. (110 aa) |
| | COA1 | Cytochrome c oxidase assembly factor 1 homolog. (146 aa) |
| | TMEM126A | Transmembrane protein 126A. (195 aa) |
| | COX6A2 | Cytochrome c oxidase subunit 6A2. (87 aa) |
| | ATP5F1A | ATP synthase subunit alpha; Produces ATP from ADP in the presence of a proton gradient across the membrane. (570 aa) |
| | NDUFS5 | NADH:ubiquinone oxidoreductase subunit S5. (106 aa) |
| | NDUFS2 | NADH:ubiquinone oxidoreductase core subunit S2; Belongs to the complex I 49 kDa subunit family. (463 aa) |
| | FH | Fumarate hydratase. (510 aa) |
| | UQCRFS1 | Cytochrome b-c1 complex subunit Rieske, mitochondrial; [Cytochrome b-c1 complex subunit Rieske, mitochondrial]: Component of the ubiquinol-cytochrome c oxidoreductase, a multisubunit transmembrane complex that is part of the mitochondrial electron transport chain which drives oxidative phosphorylation. The respiratory chain contains 3 multisubunit complexes succinate dehydrogenase (complex II, CII), ubiquinol-cytochrome c oxidoreductase (cytochrome b- c1 complex, complex III, CIII) and cytochrome c oxidase (complex IV, CIV), that cooperate to transfer electrons derived from NADH and su [...] (274 aa) |
| | ENSPPAP00000013152 | Uncharacterized protein. (128 aa) |
| | NDUFA2 | L51_S25_CI-B8 domain-containing protein. (76 aa) |
| | SDHC | Succinate dehydrogenase complex subunit C. (169 aa) |
| | UQCR10 | Ubiquinol-cytochrome c reductase, complex III subunit X. (63 aa) |
| | NDUFA8 | NADH dehydrogenase [ubiquinone] 1 alpha subcomplex subunit 8; Accessory subunit of the mitochondrial membrane respiratory chain NADH dehydrogenase (Complex I), that is believed not to be involved in catalysis. Complex I functions in the transfer of electrons from NADH to the respiratory chain. The immediate electron acceptor for the enzyme is believed to be ubiquinone. (172 aa) |
| | SLC25A27 | Solute carrier family 25 member 27; Belongs to the mitochondrial carrier (TC 2.A.29) family. (323 aa) |
| | GATC | Glutamyl-tRNA(Gln) amidotransferase subunit C, mitochondrial; Allows the formation of correctly charged Gln-tRNA(Gln) through the transamidation of misacylated Glu-tRNA(Gln) in the mitochondria. The reaction takes place in the presence of glutamine and ATP through an activated gamma-phospho-Glu-tRNA(Gln). Belongs to the GatC family. (136 aa) |
| | PDHB | Pyruvate dehydrogenase E1 component subunit beta; The pyruvate dehydrogenase complex catalyzes the overall conversion of pyruvate to acetyl-CoA and CO2. (349 aa) |
| | COX5A-2 | Cytochrome c oxidase subunit 5A, mitochondrial; Component of the cytochrome c oxidase, the last enzyme in the mitochondrial electron transport chain which drives oxidative phosphorylation. The respiratory chain contains 3 multisubunit complexes succinate dehydrogenase (complex II, CII), ubiquinol- cytochrome c oxidoreductase (cytochrome b-c1 complex, complex III, CIII) and cytochrome c oxidase (complex IV, CIV), that cooperate to transfer electrons derived from NADH and succinate to molecular oxygen, creating an electrochemical gradient over the inner membrane that drives transmembrane [...] (138 aa) |
| | IDH3B | Isocitrate dehydrogenase [NAD] subunit, mitochondrial. (408 aa) |
| | ENSPPAP00000010914 | Uncharacterized protein; Belongs to the LDH/MDH superfamily. (308 aa) |
| | ENSPPAP00000010571 | Uncharacterized protein. (191 aa) |
| | SURF1 | SURF1-like protein; Component of the MITRAC (mitochondrial translation regulation assembly intermediate of cytochrome c oxidase complex) complex, that regulates cytochrome c oxidase assembly. Belongs to the SURF1 family. (264 aa) |
| | ENSPPAP00000010061 | Uncharacterized protein. (71 aa) |
| | COX8A | Cytochrome c oxidase subunit 8A, mitochondrial; Component of the cytochrome c oxidase, the last enzyme in the mitochondrial electron transport chain which drives oxidative phosphorylation. The respiratory chain contains 3 multisubunit complexes succinate dehydrogenase (complex II, CII), ubiquinol- cytochrome c oxidoreductase (cytochrome b-c1 complex, complex III, CIII) and cytochrome c oxidase (complex IV, CIV), that cooperate to transfer electrons derived from NADH and succinate to molecular oxygen, creating an electrochemical gradient over the inner membrane that drives transmembrane [...] (69 aa) |
| | LOC100985683 | Cytochrome b-c1 complex subunit 7; Component of the ubiquinol-cytochrome c reductase complex (complex III or cytochrome b-c1 complex), which is part of the mitochondrial respiratory chain; Belongs to the UQCRB/QCR7 family. (111 aa) |
| | LOC100983016 | Cytochrome b-c1 complex subunit 7; Component of the ubiquinol-cytochrome c reductase complex (complex III or cytochrome b-c1 complex), which is part of the mitochondrial respiratory chain; Belongs to the UQCRB/QCR7 family. (101 aa) |
| | UQCRQ | Ubiquinol-cytochrome c reductase complex III subunit VII. (82 aa) |
| | ENSPPAP00000009644 | ATP-grasp_2 domain-containing protein. (399 aa) |
| | NDUFA1 | NADH dehydrogenase [ubiquinone] 1 alpha subcomplex subunit 1; Accessory subunit of the mitochondrial membrane respiratory chain NADH dehydrogenase (Complex I), that is believed not to be involved in catalysis. Complex I functions in the transfer of electrons from NADH to the respiratory chain. The immediate electron acceptor for the enzyme is believed to be ubiquinone. (70 aa) |
| | ENSPPAP00000009235 | Uncharacterized protein; Belongs to the LDH/MDH superfamily. (340 aa) |
| | NDUFB4 | NADH:ubiquinone oxidoreductase subunit B4. (129 aa) |
| | L2HGDH | L-2-hydroxyglutarate dehydrogenase. (463 aa) |
| | NDUFAF7 | Protein arginine methyltransferase NDUFAF7; Arginine methyltransferase involved in the assembly or stability of mitochondrial NADH:ubiquinone oxidoreductase complex (complex I). (441 aa) |
| | UCP1 | Uncoupling protein 1; Belongs to the mitochondrial carrier (TC 2.A.29) family. (307 aa) |
| | PDK2 | Protein-serine/threonine kinase. (407 aa) |
| | TIMMDC1 | Translocase of inner mitochondrial membrane domain containing 1. (285 aa) |
| | ENSPPAP00000008175 | Uncharacterized protein. (152 aa) |
| | ENSPPAP00000007948 | Uncharacterized protein. (475 aa) |
| | PDK4 | Protein-serine/threonine kinase. (411 aa) |
| | ME3 | Malic enzyme. (545 aa) |
| | HAGHL | Lactamase_B domain-containing protein. (270 aa) |
| | PDP1 | Pyruvate dehyrogenase phosphatase catalytic subunit 1. (596 aa) |
| | ENSPPAP00000007590 | Uncharacterized protein. (234 aa) |
| | ENSPPAP00000007522 | Uncharacterized protein. (128 aa) |
| | LOC103785895 | Cytochrome c domain-containing protein; Electron carrier protein. The oxidized form of the cytochrome c heme group can accept an electron from the heme group of the cytochrome c1 subunit of cytochrome reductase. Cytochrome c then transfers this electron to the cytochrome oxidase complex, the final protein carrier in the mitochondrial electron-transport chain. (110 aa) |
| | COX6B2 | Cytochrome c oxidase subunit 6B2. (88 aa) |
| | TRAP1 | TNF receptor associated protein 1. (673 aa) |
| | NDUFB8 | NADH dehydrogenase [ubiquinone] 1 beta subcomplex subunit 8, mitochondrial; Accessory subunit of the mitochondrial membrane respiratory chain NADH dehydrogenase (Complex I), that is believed not to be involved in catalysis. Complex I functions in the transfer of electrons from NADH to the respiratory chain. The immediate electron acceptor for the enzyme is believed to be ubiquinone. (186 aa) |
| | YJEFN3 | YjeF N-terminal domain containing 3. (299 aa) |
| | ENSPPAP00000006541 | Uncharacterized protein. (480 aa) |
| | PWWP3A | PWWP domain containing 3A, DNA repair factor. (732 aa) |
| | LOC100967281 | Uncharacterized protein. (84 aa) |
| | NDUFA11 | NADH:ubiquinone oxidoreductase subunit A11. (228 aa) |
| | TRIR | Telomerase RNA component interacting RNase. (172 aa) |
| | DMAC2L | Uncharacterized protein. (266 aa) |
| | ENSPPAP00000005297 | ATP-synt_C domain-containing protein; Belongs to the ATPase C chain family. (127 aa) |
| | ENSPPAP00000005280 | ATP-synt_C domain-containing protein; Belongs to the ATPase C chain family. (184 aa) |
| | LDHAL6A | L-lactate dehydrogenase; Belongs to the LDH/MDH superfamily. (332 aa) |
| | ENSPPAP00000004862 | Uncharacterized protein. (353 aa) |
| | ACO2 | Aconitase 2. (800 aa) |
| | MPC1L | Mitochondrial pyruvate carrier; Mediates the uptake of pyruvate into mitochondria. Belongs to the mitochondrial pyruvate carrier (MPC) (TC 2.A.105) family. (136 aa) |
| | ENSPPAP00000004577 | CIA30 domain-containing protein. (295 aa) |
| | PDHA2 | Pyruvate dehydrogenase E1 alpha 2 subunit. (387 aa) |
| | COX7B2 | Cytochrome c oxidase subunit 7B2. (81 aa) |
| | LDHAL6B | L-lactate dehydrogenase; Belongs to the LDH/MDH superfamily. (381 aa) |
| | ATP5F1E | ATP synthase F1 subunit epsilon. (51 aa) |
| | CYCS | Cytochrome c, somatic; Electron carrier protein. The oxidized form of the cytochrome c heme group can accept an electron from the heme group of the cytochrome c1 subunit of cytochrome reductase. Cytochrome c then transfers this electron to the cytochrome oxidase complex, the final protein carrier in the mitochondrial electron-transport chain. (105 aa) |
| | ENSPPAP00000004015 | Uncharacterized protein. (58 aa) |
| | ENSPPAP00000003907 | Uncharacterized protein. (150 aa) |
| | NDUFV3 | NADH:ubiquinone oxidoreductase subunit V3. (473 aa) |
| | NDUFA12 | NADH dehydrogenase [ubiquinone] 1 alpha subcomplex subunit 12; Accessory subunit of the mitochondrial membrane respiratory chain NADH dehydrogenase (Complex I), that is believed not to be involved in catalysis. Complex I functions in the transfer of electrons from NADH to the respiratory chain. The immediate electron acceptor for the enzyme is believed to be ubiquinone. (145 aa) |
| | UQCRHL | Cytochrome b-c1 complex subunit 6; This is a component of the ubiquinol-cytochrome c reductase complex (complex III or cytochrome b-c1 complex), which is part of the mitochondrial respiratory chain. This protein may mediate formation of the complex between cytochromes c and c1. Belongs to the UQCRH/QCR6 family. (93 aa) |
| | LACTB2 | Lactamase beta 2. (287 aa) |
| | ENSPPAP00000003283 | Cytochrome c oxidase subunit 6A, mitochondrial. (109 aa) |
| | C17orf80 | Chromosome 17 open reading frame 80. (609 aa) |
| | NNT | Nicotinamide nucleotide transhydrogenase. (1086 aa) |
| | ATP5PO | Uncharacterized protein. (83 aa) |
| | ENSPPAP00000002695 | Uncharacterized protein. (87 aa) |
| | ENSPPAP00000002472 | Succinate dehydrogenase [ubiquinone] cytochrome b small subunit; Membrane-anchoring subunit of succinate dehydrogenase (SDH) that is involved in complex II of the mitochondrial electron transport chain and is responsible for transferring electrons from succinate to ubiquinone (coenzyme Q); Belongs to the CybS family. (150 aa) |
| | NPVF | Neuropeptide VF precursor. (196 aa) |
| | COQ10B | Coenzyme Q10B. (238 aa) |
| | ENSPPAP00000001813 | Uncharacterized protein; Belongs to the mitochondrial carrier (TC 2.A.29) family. (289 aa) |
| | ATP5F1C | ATP synthase subunit gamma. (298 aa) |
| | LOC100986838 | Uncharacterized protein. (156 aa) |
| | CYC1 | Cytochrome c1. (325 aa) |
| | SCO2 | SCO cytochrome c oxidase assembly protein 2. (266 aa) |
| | NDUFAB1 | Acyl carrier protein; Carrier of the growing fatty acid chain in fatty acid biosynthesis. (156 aa) |
| | UCP2 | Uncoupling protein 2; Belongs to the mitochondrial carrier (TC 2.A.29) family. (309 aa) |
| | NDUFS7 | NADH:ubiquinone oxidoreductase core subunit S7; Belongs to the complex I 20 kDa subunit family. (213 aa) |
| | COX7A2 | Cytochrome c oxidase subunit 7A2. (115 aa) |
| | ATP5MG | ATP synthase subunit; Mitochondrial membrane ATP synthase (F1F0 ATP synthase or Complex V) produces ATP from ADP in the presence of a proton gradient across the membrane which is generated by electron transport complexes of the respiratory chain. F-type ATPases consist of two structural domains, F1 - containing the extramembraneous catalytic core, and F0 - containing the membrane proton channel, linked together by a central stalk and a peripheral stalk. During catalysis, ATP synthesis in the catalytic domain of F1 is coupled via a rotary mechanism of the central stalk subunits to proto [...] (103 aa) |
| | SLC25A30 | Solute carrier family 25 member 30; Belongs to the mitochondrial carrier (TC 2.A.29) family. (291 aa) |
| | WBP2 | WW domain binding protein 2. (261 aa) |
| | ENSPPAP00000000738 | Cytochrome c domain-containing protein; Electron carrier protein. The oxidized form of the cytochrome c heme group can accept an electron from the heme group of the cytochrome c1 subunit of cytochrome reductase. Cytochrome c then transfers this electron to the cytochrome oxidase complex, the final protein carrier in the mitochondrial electron-transport chain. (105 aa) |
| | LOC100987437 | Dihydrolipoamide acetyltransferase component of pyruvate dehydrogenase complex. (419 aa) |
| | ENSPPAP00000000554 | Uncharacterized protein. (93 aa) |
| | PDP2 | Pyruvate dehyrogenase phosphatase catalytic subunit 2. (529 aa) |
| | LOC106634335 | Cytochrome c domain-containing protein; Electron carrier protein. The oxidized form of the cytochrome c heme group can accept an electron from the heme group of the cytochrome c1 subunit of cytochrome reductase. Cytochrome c then transfers this electron to the cytochrome oxidase complex, the final protein carrier in the mitochondrial electron-transport chain. (105 aa) |
| | NDUFAF6 | NADH:ubiquinone oxidoreductase complex assembly factor 6. (333 aa) |
| | D2HGDH | D-2-hydroxyglutarate dehydrogenase. (521 aa) |
| | CYTB | Cytochrome b; Component of the ubiquinol-cytochrome c reductase complex (complex III or cytochrome b-c1 complex) that is part of the mitochondrial respiratory chain. The b-c1 complex mediates electron transfer from ubiquinol to cytochrome c. Contributes to the generation of a proton gradient across the mitochondrial membrane that is then used for ATP synthesis. (380 aa) |
| | ND6 | NADH-ubiquinone oxidoreductase chain 6; Core subunit of the mitochondrial membrane respiratory chain NADH dehydrogenase (Complex I) that is believed to belong to the minimal assembly required for catalysis. Complex I functions in the transfer of electrons from NADH to the respiratory chain. The immediate electron acceptor for the enzyme is believed to be ubiquinone (By similarity). (174 aa) |
| | ND5 | NADH-ubiquinone oxidoreductase chain 5; Core subunit of the mitochondrial membrane respiratory chain NADH dehydrogenase (Complex I) that is believed to belong to the minimal assembly required for catalysis. Complex I functions in the transfer of electrons from NADH to the respiratory chain. The immediate electron acceptor for the enzyme is believed to be ubiquinone (By similarity). (603 aa) |
| | ND4 | NADH-ubiquinone oxidoreductase chain 4; Core subunit of the mitochondrial membrane respiratory chain NADH dehydrogenase (Complex I) that is believed to belong to the minimal assembly required for catalysis. Complex I functions in the transfer of electrons from NADH to the respiratory chain. The immediate electron acceptor for the enzyme is believed to be ubiquinone (By similarity). (459 aa) |
| | ND3 | NADH-ubiquinone oxidoreductase chain 3; Core subunit of the mitochondrial membrane respiratory chain NADH dehydrogenase (Complex I) that is believed to belong to the minimal assembly required for catalysis. Complex I functions in the transfer of electrons from NADH to the respiratory chain. The immediate electron acceptor for the enzyme is believed to be ubiquinone (By similarity). (115 aa) |
