node1 | node2 | node1 accession | node2 accession | node1 annotation | node2 annotation | score |
Bckdha | Bckdhb | ENSDORP00000003373 | ENSDORP00000003628 | 2-oxoisovalerate dehydrogenase subunit alpha; The branched-chain alpha-keto dehydrogenase complex catalyzes the overall conversion of alpha-keto acids to acyl-CoA and CO(2). It contains multiple copies of three enzymatic components: branched-chain alpha-keto acid decarboxylase (E1), lipoamide acyltransferase (E2) and lipoamide dehydrogenase (E3). | 2-oxoisovalerate dehydrogenase subunit beta, mitochondrial. | 0.999 |
Bckdha | Dlat | ENSDORP00000003373 | ENSDORP00000018536 | 2-oxoisovalerate dehydrogenase subunit alpha; The branched-chain alpha-keto dehydrogenase complex catalyzes the overall conversion of alpha-keto acids to acyl-CoA and CO(2). It contains multiple copies of three enzymatic components: branched-chain alpha-keto acid decarboxylase (E1), lipoamide acyltransferase (E2) and lipoamide dehydrogenase (E3). | Acetyltransferase component of pyruvate dehydrogenase complex; The pyruvate dehydrogenase complex catalyzes the overall conversion of pyruvate to acetyl-CoA and CO(2). | 0.993 |
Bckdha | Dld | ENSDORP00000003373 | ENSDORP00000001465 | 2-oxoisovalerate dehydrogenase subunit alpha; The branched-chain alpha-keto dehydrogenase complex catalyzes the overall conversion of alpha-keto acids to acyl-CoA and CO(2). It contains multiple copies of three enzymatic components: branched-chain alpha-keto acid decarboxylase (E1), lipoamide acyltransferase (E2) and lipoamide dehydrogenase (E3). | Dihydrolipoyl dehydrogenase. | 0.986 |
Bckdha | Dlst | ENSDORP00000003373 | ENSDORP00000002019 | 2-oxoisovalerate dehydrogenase subunit alpha; The branched-chain alpha-keto dehydrogenase complex catalyzes the overall conversion of alpha-keto acids to acyl-CoA and CO(2). It contains multiple copies of three enzymatic components: branched-chain alpha-keto acid decarboxylase (E1), lipoamide acyltransferase (E2) and lipoamide dehydrogenase (E3). | Dihydrolipoamide S-succinyltransferase. | 0.994 |
Bckdha | LOC105981059 | ENSDORP00000003373 | ENSDORP00000020615 | 2-oxoisovalerate dehydrogenase subunit alpha; The branched-chain alpha-keto dehydrogenase complex catalyzes the overall conversion of alpha-keto acids to acyl-CoA and CO(2). It contains multiple copies of three enzymatic components: branched-chain alpha-keto acid decarboxylase (E1), lipoamide acyltransferase (E2) and lipoamide dehydrogenase (E3). | Pyruvate dehydrogenase E1 component subunit beta, mitochondrial pseudogene. | 0.999 |
Bckdha | LOC105995863 | ENSDORP00000003373 | ENSDORP00000019592 | 2-oxoisovalerate dehydrogenase subunit alpha; The branched-chain alpha-keto dehydrogenase complex catalyzes the overall conversion of alpha-keto acids to acyl-CoA and CO(2). It contains multiple copies of three enzymatic components: branched-chain alpha-keto acid decarboxylase (E1), lipoamide acyltransferase (E2) and lipoamide dehydrogenase (E3). | Pyruvate dehydrogenase E1 component subunit alpha, somatic form, mitochondrial-like. | 0.729 |
Bckdha | Pdha1 | ENSDORP00000003373 | ENSDORP00000011138 | 2-oxoisovalerate dehydrogenase subunit alpha; The branched-chain alpha-keto dehydrogenase complex catalyzes the overall conversion of alpha-keto acids to acyl-CoA and CO(2). It contains multiple copies of three enzymatic components: branched-chain alpha-keto acid decarboxylase (E1), lipoamide acyltransferase (E2) and lipoamide dehydrogenase (E3). | Pyruvate dehydrogenase E1 component subunit alpha; The pyruvate dehydrogenase complex catalyzes the overall conversion of pyruvate to acetyl-CoA and CO(2). | 0.764 |
Bckdha | Pdhb | ENSDORP00000003373 | ENSDORP00000027299 | 2-oxoisovalerate dehydrogenase subunit alpha; The branched-chain alpha-keto dehydrogenase complex catalyzes the overall conversion of alpha-keto acids to acyl-CoA and CO(2). It contains multiple copies of three enzymatic components: branched-chain alpha-keto acid decarboxylase (E1), lipoamide acyltransferase (E2) and lipoamide dehydrogenase (E3). | Pyruvate dehydrogenase E1 component subunit beta; The pyruvate dehydrogenase complex catalyzes the overall conversion of pyruvate to acetyl-CoA and CO2. | 0.999 |
Bckdha | Pdhx | ENSDORP00000003373 | ENSDORP00000005938 | 2-oxoisovalerate dehydrogenase subunit alpha; The branched-chain alpha-keto dehydrogenase complex catalyzes the overall conversion of alpha-keto acids to acyl-CoA and CO(2). It contains multiple copies of three enzymatic components: branched-chain alpha-keto acid decarboxylase (E1), lipoamide acyltransferase (E2) and lipoamide dehydrogenase (E3). | Dihydrolipoamide acetyltransferase component of pyruvate dehydrogenase complex. | 0.993 |
Bckdha | Suclg1 | ENSDORP00000003373 | ENSDORP00000010333 | 2-oxoisovalerate dehydrogenase subunit alpha; The branched-chain alpha-keto dehydrogenase complex catalyzes the overall conversion of alpha-keto acids to acyl-CoA and CO(2). It contains multiple copies of three enzymatic components: branched-chain alpha-keto acid decarboxylase (E1), lipoamide acyltransferase (E2) and lipoamide dehydrogenase (E3). | Succinate--CoA ligase [ADP/GDP-forming] subunit alpha, mitochondrial; Succinyl-CoA synthetase functions in the citric acid cycle (TCA), coupling the hydrolysis of succinyl-CoA to the synthesis of either ATP or GTP and thus represents the only step of substrate-level phosphorylation in the TCA. The alpha subunit of the enzyme binds the substrates coenzyme A and phosphate, while succinate binding and specificity for either ATP or GTP is provided by different beta subunits. | 0.744 |
Bckdhb | Bckdha | ENSDORP00000003628 | ENSDORP00000003373 | 2-oxoisovalerate dehydrogenase subunit beta, mitochondrial. | 2-oxoisovalerate dehydrogenase subunit alpha; The branched-chain alpha-keto dehydrogenase complex catalyzes the overall conversion of alpha-keto acids to acyl-CoA and CO(2). It contains multiple copies of three enzymatic components: branched-chain alpha-keto acid decarboxylase (E1), lipoamide acyltransferase (E2) and lipoamide dehydrogenase (E3). | 0.999 |
Bckdhb | Dlat | ENSDORP00000003628 | ENSDORP00000018536 | 2-oxoisovalerate dehydrogenase subunit beta, mitochondrial. | Acetyltransferase component of pyruvate dehydrogenase complex; The pyruvate dehydrogenase complex catalyzes the overall conversion of pyruvate to acetyl-CoA and CO(2). | 0.980 |
Bckdhb | Dld | ENSDORP00000003628 | ENSDORP00000001465 | 2-oxoisovalerate dehydrogenase subunit beta, mitochondrial. | Dihydrolipoyl dehydrogenase. | 0.988 |
Bckdhb | Dlst | ENSDORP00000003628 | ENSDORP00000002019 | 2-oxoisovalerate dehydrogenase subunit beta, mitochondrial. | Dihydrolipoamide S-succinyltransferase. | 0.987 |
Bckdhb | LOC105981059 | ENSDORP00000003628 | ENSDORP00000020615 | 2-oxoisovalerate dehydrogenase subunit beta, mitochondrial. | Pyruvate dehydrogenase E1 component subunit beta, mitochondrial pseudogene. | 0.695 |
Bckdhb | LOC105995863 | ENSDORP00000003628 | ENSDORP00000019592 | 2-oxoisovalerate dehydrogenase subunit beta, mitochondrial. | Pyruvate dehydrogenase E1 component subunit alpha, somatic form, mitochondrial-like. | 0.907 |
Bckdhb | Pdha1 | ENSDORP00000003628 | ENSDORP00000011138 | 2-oxoisovalerate dehydrogenase subunit beta, mitochondrial. | Pyruvate dehydrogenase E1 component subunit alpha; The pyruvate dehydrogenase complex catalyzes the overall conversion of pyruvate to acetyl-CoA and CO(2). | 0.994 |
Bckdhb | Pdhb | ENSDORP00000003628 | ENSDORP00000027299 | 2-oxoisovalerate dehydrogenase subunit beta, mitochondrial. | Pyruvate dehydrogenase E1 component subunit beta; The pyruvate dehydrogenase complex catalyzes the overall conversion of pyruvate to acetyl-CoA and CO2. | 0.677 |
Bckdhb | Pdhx | ENSDORP00000003628 | ENSDORP00000005938 | 2-oxoisovalerate dehydrogenase subunit beta, mitochondrial. | Dihydrolipoamide acetyltransferase component of pyruvate dehydrogenase complex. | 0.983 |
Bckdhb | Suclg1 | ENSDORP00000003628 | ENSDORP00000010333 | 2-oxoisovalerate dehydrogenase subunit beta, mitochondrial. | Succinate--CoA ligase [ADP/GDP-forming] subunit alpha, mitochondrial; Succinyl-CoA synthetase functions in the citric acid cycle (TCA), coupling the hydrolysis of succinyl-CoA to the synthesis of either ATP or GTP and thus represents the only step of substrate-level phosphorylation in the TCA. The alpha subunit of the enzyme binds the substrates coenzyme A and phosphate, while succinate binding and specificity for either ATP or GTP is provided by different beta subunits. | 0.756 |